Intrinsic mitochondrial DNA repair defects in ataxia telangiectasia

DNA Repair

Volumn 13, Issue 1, 2014, Pages 22-31

  Sharma, Nilesh K ^a,d   Lebedeva, Maria ^b   Thomas, Terace ^a   Kovalenko, Olga A ^a   Stumpf, Jeffrey D ^c   Shadel, Gerald S ^b   Santos, Janine H ^a,c  

^a RUTGERS NEW JERSEY MEDICAL SCHOOL   (United States)

^b YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^c NATIONAL INSTITUTE OF ENVIRONMENTAL HEALTH SCIENCES   (United States)

^d DR D Y PATIL BIOTECHNOLOGY AND BIOINFORMATICS INSTITUTE   (India)

Author keywords

Ataxia Telangiectasia; ATM; DNA ligase 3; Mitochondria; Mitochondrial DNA repair

Indexed keywords

ATM PROTEIN; HYDROGEN PEROXIDE; MITOCHONDRIAL DNA; POLYDEOXYRIBONUCLEOTIDE SYNTHASE; PROTEASOME; SUPEROXIDE;

ANIMAL TISSUE; ARTICLE; ATAXIA TELANGIECTASIA; DNA REPAIR; FIBROBLAST; HUMAN; HUMAN CELL; HUMAN CELL CULTURE; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN PHOSPHORYLATION; PROTEIN STABILITY;

ATAXIA TELANGIECTASIA; MUS;

ATAXIA TELANGIECTASIA; ATM; DNA LIGASE 3; MITOCHONDRIA; MITOCHONDRIAL DNA REPAIR;

ANIMALS; ATAXIA TELANGIECTASIA; ATAXIA TELANGIECTASIA MUTATED PROTEINS; CELL LINE; DNA LIGASES; DNA REPAIR; DNA, MITOCHONDRIAL; GENE EXPRESSION REGULATION; GENE KNOCKDOWN TECHNIQUES; HUMANS; LEUPEPTINS; MICE; MICE, KNOCKOUT; MITOCHONDRIA; NERVOUS SYSTEM; TUMOR MARKERS, BIOLOGICAL;

EID: 84891142463     PISSN: 15687864     EISSN: 15687856     Source Type: Journal    
DOI: 10.1016/j.dnarep.2013.11.002     Document Type: Article

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