Review: The history and role of naturally occurring mouse models with Pde6b mutations

Molecular Vision

Volumn 19, Issue , 2013, Pages 2579-2589

  Han, Juanjuan ^a   Dinculescu, Astra ^b   Dai, Xufeng ^a   Du, Wei ^b   Clay Smith, W ^b   Pang, Jijing ^a,b  

^a WENZHOU MEDICAL UNIVERSITY   (China)

^b UNIVERSITY OF FLORIDA COLLEGE OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AGENTS ACTING ON THE EYE; ALPHA TOCOPHEROL; ASCORBIC ACID; BETA PHOSPHODIESTERASE; BRAIN DERIVED NEUROTROPHIC FACTOR; CASPASE 3; CHANNEL RHODOPSIN 2; CILIARY NEUROTROPHIC FACTOR; COMPLEMENTARY DNA; CYCLIC GMP PHOSPHODIESTERASE BETA SUBUNIT; DILTIAZEM; GLIAL CELL LINE DERIVED NEUROTROPHIC FACTOR; GRANULOCYTE COLONY STIMULATING FACTOR; LENTIVIRUS VECTOR; MELANOPSIN; PARVOVIRUS VECTOR; PHENYLALANINE; PHOSPHODIESTERASE 6B; PHOSPHODIESTERASE VI; RECOMBINANT ERYTHROPOIETIN; SMCBA BETA PHOSPHODIESTERASE; SMCBA PHOSPHODIESTERASE 6B; TAUROURSODEOXYCHOLIC ACID; THIOCTIC ACID; TYROSINE; UNCLASSIFIED DRUG; XANTHOPHYLL; ZEAXANTHIN;

ANTIOXIDANT ACTIVITY; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; BETA PDE6B GENE; CELL ACTIVATION; CELL FUNCTION; CELL LINEAGE; CELL PROTECTION; CELL SURVIVAL; CELL TRANSPLANTATION; CHR2 GENE; CHROMOSOME 5; DISEASE COURSE; DISEASE MODEL; DRUG ADMINISTRATION ROUTE; DRUG EFFICACY; DRUG PENETRATION; ENDOTHELIAL PROGENITOR CELL; ENZYME ACTIVATION; ENZYME ACTIVITY; GENE; GENE INSERTION; GENE MUTATION; GENE REPLACEMENT THERAPY; GENETIC SIMILARITY; GENETIC TRANSCRIPTION; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HUMAN; INTRON; LEBER CONGENITAL AMAUROSIS; LIN CELL; MEDICAL DEVICE COMPLICATION; MICROGLIA; MINICHROMOSOME; MISSENSE MUTATION; MOUSE; MOUSE STRAIN; MURINE LEUKEMIA PROVIRUS; MURINE LEUKEMIA VIRUS; NEUROPROTECTION; NONHUMAN; NONSENSE MUTATION; OPTOGENETICS; PATHOPHYSIOLOGY; PHENOTYPE; PHOTORECEPTOR TRANSPLANTATION; POINT MUTATION; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROVIRUS; RETINA BIPOLAR GANGLION CELL; RETINA DEGENERATION; RETINA ROD; RETINITIS PIGMENTOSA; SOMATIC GENE THERAPY; SPONTANEOUS MUTATION; STOP CODON; SUBRETINAL DRUG ADMINISTRATION; TRANSCORNEA SUBRETINAL INJECTION; TRANSSCLERA SUBRETINAL INJECTION; VIRAL GENE DELIVERY SYSTEM; VIRAL GENE THERAPY; VIRUS CAPSID; VISION;

ADENOVIRIDAE; ANIMALS; CELL- AND TISSUE-BASED THERAPY; CYCLIC NUCLEOTIDE PHOSPHODIESTERASES, TYPE 6; DISEASE MODELS, ANIMAL; GENE EXPRESSION; GENETIC THERAPY; GENETIC VECTORS; HUMANS; MICE; MUTATION; RETINA; RETINITIS PIGMENTOSA;

EID: 84890862365     PISSN: None     EISSN: 10900535     Source Type: Journal    
DOI: None     Document Type: Article

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