Therapeutic strategies in Friedreich's Ataxia

Brain Research

Volumn 1514, Issue , 2013, Pages 91-97

  Richardson, Timothy E ^a,b   Kelly, Heather N ^b   Yu, Amanda E ^a,b   Simpkins, James W ^a  

^a UNIVERSITY OF NORTH TEXAS HEALTH SCIENCE CENTER   (United States)

^b University of North Texas Health Science Center   (United States)

Author keywords

17 estradiol; Frataxin; Friedreich's Ataxia; Methylene blue; Therapeutic Strategies

Indexed keywords

BML 210; DEFERIPRONE; DEFEROXAMINE; ERYTHROPOIETIN; ESTRADIOL; FRATAXIN; HISTONE DEACETYLASE INHIBITOR; IDEBENONE; IRON CHELATING AGENT; MESSENGER RNA; METHYLENE BLUE; REACTIVE OXYGEN METABOLITE; TRINUCLEOTIDE; UNCLASSIFIED DRUG;

ALZHEIMER DISEASE; ARTICLE; CELL DEATH; CELL PROTECTION; DEACETYLATION; DOSE RESPONSE; DRUG POTENCY; ESTROGEN THERAPY; FIBROBLAST; FRIEDREICH ATAXIA; GENE SILENCING; GENOTYPE; GLUCOSE INTOLERANCE; HUMAN; INSULIN RESISTANCE; INTRON; IRON CHELATION; LIPID PEROXIDATION; MITOCHONDRIAL MEMBRANE POTENTIAL; MITOCHONDRION; MOLECULAR PATHOLOGY; MOSAICISM; NEUROPROTECTION; ONSET AGE; OPTIC NERVE DISEASE; OXIDATIVE PHOSPHORYLATION; OXIDATIVE STRESS; PHASE 3 CLINICAL TRIAL; PHASE 3 CLINICAL TRIAL (TOPIC); PHYSICAL DISEASE BY BODY FUNCTION; PRIORITY JOURNAL; PROTEIN FUNCTION; RETINA DISEASE; TRINUCLEOTIDE REPEAT;

ANTIOXIDANTS; FRIEDREICH ATAXIA; HISTORY, 19TH CENTURY; HUMANS; IRON CHELATING AGENTS; IRON-BINDING PROTEINS; TRINUCLEOTIDE REPEAT EXPANSION;

EID: 84878488044     PISSN: 00068993     EISSN: 18726240     Source Type: Journal    
DOI: 10.1016/j.brainres.2013.04.005     Document Type: Article

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