Deferiprone targets aconitase: Implication for Friedreich's ataxia treatment

BMC Neurology

Volumn 8, Issue , 2008, Pages

  Goncalves, Sergio ^a,b   Paupe, Vincent ^a,b   Dassa, Emmanuel P ^a,b   Rustin, Pierre ^a,b  

^a HÔPITAL ROBERT DEBRÉ   (France)

^b UNIVERSITÉ PARIS DESCARTES   (France)

Author keywords

[No Author keywords available]

Indexed keywords

ACONITATE HYDRATASE; DEFERIPRONE; FRATAXIN; IRON SULFUR PROTEIN; IRON; IRON CHELATING AGENT; PYRIDONE DERIVATIVE;

ARTICLE; CELL PROLIFERATION; CONCENTRATION RESPONSE; CONTROLLED STUDY; DISEASE COURSE; DRUG TARGETING; ENZYME ACTIVITY; ENZYME DEFICIENCY; FIBROBLAST CULTURE; FRIEDREICH ATAXIA; HUMAN; HUMAN CELL; IRON CHELATION; MITOCHONDRION; NEUROBLASTOMA; NEUROLOGIC DISEASE; SKIN FIBROBLAST; CELL CULTURE; CYTOSOL; DRUG EFFECT; ENZYMOLOGY; FIBROBLAST; METABOLISM; PATHOLOGY;

ACONITATE HYDRATASE; CELL PROLIFERATION; CELLS, CULTURED; CYTOSOL; FIBROBLASTS; FRIEDREICH ATAXIA; HUMANS; IRON; IRON CHELATING AGENTS; MITOCHONDRIA; PYRIDONES;

EID: 46749101742     PISSN: None     EISSN: 14712377     Source Type: Journal    
DOI: 10.1186/1471-2377-8-20     Document Type: Article

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