A closer look at prion strains: Characterization and important implications

Prion

Volumn 7, Issue 2, 2013, Pages 99-108

  Solforosi, Laura ^a   Milani, Michela ^a   Mancini, Nicasio ^a   Clementi, Massimo ^a   Burioni, Roberto ^a  

^a VITA SALUTE SAN RAFFAELE UNIVERSITY   (Italy)

Author keywords

Cellular prion protein (PrPC); Prion strains; Scrapie prion protein (PrP Sc); Sporadic Creutzfeldt Jakob disease; Strain mutation; Transmissible spongiform encephalopathies (TSEs); Variant Creutzfeldt Jakob disease

Indexed keywords

PRION PROTEIN;

BINDING AFFINITY; BRAIN HOMOGENATE; BRAIN REGION; CONFORMATION; CREUTZFELDT JAKOB DISEASE; ERYTHROCYTE SEDIMENTATION RATE; GENOTYPE; HUMAN; INCUBATION TIME; INFRARED SPECTROSCOPY; INOCULATION; MUTATION; NONHUMAN; PHENOTYPE; PRION DISEASE; PROTEIN FOLDING; REVIEW;

CELLULAR PRION PROTEIN (PRPC); PRION STRAINS; SCRAPIE PRION PROTEIN (PRPSC); SPORADIC CREUTZFELDT-JAKOB DISEASE; STRAIN MUTATION; TRANSMISSIBLE SPONGIFORM ENCEPHALOPATHIES (TSES); VARIANT CREUTZFELDT-JAKOB DISEASE;

ANIMALS; HUMANS; MUTATION; PRION DISEASES; PRIONS; PROTEIN STABILITY;

ANIMALIA; SCRAPIE PRION;

EID: 84875444996     PISSN: 19336896     EISSN: 1933690X     Source Type: Journal    
DOI: 10.4161/pri.23490     Document Type: Review

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