-
1
-
-
0027740178
-
Scrapie strain variation and mutation
-
Bruce M (1993) Scrapie strain variation and mutation. Br Med Bull 49: 822-838.
-
(1993)
Br Med Bull
, vol.49
, pp. 822-838
-
-
Bruce, M.1
-
2
-
-
12644272790
-
Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity
-
Telling GC, Parchi P, DeArmond SJ, Cortelli P, Montagna P, et al. (1996) Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity. Science 274: 2079-2082.
-
(1996)
Science
, vol.274
, pp. 2079-2082
-
-
Telling, G.C.1
Parchi, P.2
DeArmond, S.J.3
Cortelli, P.4
Montagna, P.5
-
3
-
-
8944259890
-
Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease
-
Parchi P, Castellani R, Capellari S, Ghetti B, Young K, et al. (1996) Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease. Ann Neurol 39: 669-680.
-
(1996)
Ann Neurol
, vol.39
, pp. 669-680
-
-
Parchi, P.1
Castellani, R.2
Capellari, S.3
Ghetti, B.4
Young, K.5
-
4
-
-
0029831213
-
Molecular analysis of prion strain variation and the etiology of "new variant" CJD
-
Collinge J, Sidle KCL, Meads J, Ironside J, Hill AF (1996) Molecular analysis of prion strain variation and the etiology of "new variant" CJD. Nature 383: 685-690.
-
(1996)
Nature
, vol.383
, pp. 685-690
-
-
Collinge, J.1
Sidle, K.C.L.2
Meads, J.3
Ironside, J.4
Hill, A.F.5
-
5
-
-
0032561178
-
Molecular screening of sheep for bovine spongiform encephalopathy
-
Hill AF, Sidle KCL, Joiner S, Keyes P, Martin TC, et al. (1998) Molecular screening of sheep for bovine spongiform encephalopathy. Neurosci Lett 255: 159-162.
-
(1998)
Neurosci Lett
, vol.255
, pp. 159-162
-
-
Hill, A.F.1
Sidle, K.C.L.2
Joiner, S.3
Keyes, P.4
Martin, T.C.5
-
7
-
-
0028069116
-
Prions and related neurological diseases
-
Pocchiari M (1994) Prions and related neurological diseases. Mol Aspects Med 15: 195-291.
-
(1994)
Mol Aspects Med
, vol.15
, pp. 195-291
-
-
Pocchiari, M.1
-
8
-
-
20944445878
-
Mortality from Creutzfeldt-Jakob disease and related disorders in Europe, Australia, and Canada
-
Ladogana A, Puopolo M, Croes EA, Budka H, Jarius C, et al. (2005) Mortality from Creutzfeldt-Jakob disease and related disorders in Europe, Australia, and Canada. Neurology 64: 1586-1591.
-
(2005)
Neurology
, vol.64
, pp. 1586-1591
-
-
Ladogana, A.1
Puopolo, M.2
Croes, E.A.3
Budka, H.4
Jarius, C.5
-
9
-
-
27944483780
-
Genetic prion disease: The EUROCJD experience
-
Kovacs GG, Puopolo M, Ladogana A, Pocchiari M, Budka H, et al. (2005) Genetic prion disease: The EUROCJD experience. Hum Genet 118: 166-174.
-
(2005)
Hum Genet
, vol.118
, pp. 166-174
-
-
Kovacs, G.G.1
Puopolo, M.2
Ladogana, A.3
Pocchiari, M.4
Budka, H.5
-
10
-
-
0342951746
-
A new variant of Creutzfeldt-Jakob disease in the UK
-
Will RG, Ironside JW, Zeidler M, Cousens SN, Estibereiro K, et al. (1996) A new variant of Creutzfeldt-Jakob disease in the UK. Lancet 347: 921-925.
-
(1996)
Lancet
, vol.347
, pp. 921-925
-
-
Will, R.G.1
Ironside, J.W.2
Zeidler, M.3
Cousens, S.N.4
Estibereiro, K.5
-
11
-
-
0030775632
-
Transmissions to mice indicate that "new variant" CJD is caused by the BSE agent
-
Bruce M, Will RG, Ironside JW, McConnell I, Drummond D, et al. (1997) Transmissions to mice indicate that "new variant" CJD is caused by the BSE agent. Nature 389: 498-501.
-
(1997)
Nature
, vol.389
, pp. 498-501
-
-
Bruce, M.1
Will, R.G.2
Ironside, J.W.3
McConnell, I.4
Drummond, D.5
-
12
-
-
0030820354
-
The same prion strain causes vCJD and BSE
-
Hill AF, Desbruslais M, Joiner S, Sidle KCL, Gowland I, et al. (1997) The same prion strain causes vCJD and BSE. Nature 389: 448-450.
-
(1997)
Nature
, vol.389
, pp. 448-450
-
-
Hill, A.F.1
Desbruslais, M.2
Joiner, S.3
Sidle, K.C.L.4
Gowland, I.5
-
13
-
-
0028235176
-
Human spongiform encephalopathy: The National Institutes of Health series of 300 cases of experimentally transmitted disease
-
Brown P, Gibbs CJ, Rodgers-Johnson P, Asher DM, Sulima MP, et al. (1994) Human spongiform encephalopathy: The National Institutes of Health series of 300 cases of experimentally transmitted disease. Ann Neurol 35: 513-529.
-
(1994)
Ann Neurol
, vol.35
, pp. 513-529
-
-
Brown, P.1
Gibbs, C.J.2
Rodgers-Johnson, P.3
Asher, D.M.4
Sulima, M.P.5
-
14
-
-
0025244011
-
Transgenetic studies implicate interactions between homologous PrP isoforms in scrapie prion replication
-
Prusiner SB, Scott M, Foster D, Pan KM, Groth D, et al. (1990) Transgenetic studies implicate interactions between homologous PrP isoforms in scrapie prion replication. Cell 63: 673-686.
-
(1990)
Cell
, vol.63
, pp. 673-686
-
-
Prusiner, S.B.1
Scott, M.2
Foster, D.3
Pan, K.M.4
Groth, D.5
-
15
-
-
0028782015
-
Transmission of bovine spongiform encephalopathy and scrapie to mice: Strain variation and the species barrier
-
Bruce M, Chree A, McConnell I, Foster J, Pearson G, et al. (1994) Transmission of bovine spongiform encephalopathy and scrapie to mice: Strain variation and the species barrier. Philos Trans R Soc Lond B Biol Sci 343: 405-411.
-
(1994)
Philos Trans R Soc Lond B Biol Sci
, vol.343
, pp. 405-411
-
-
Bruce, M.1
Chree, A.2
McConnell, I.3
Foster, J.4
Pearson, G.5
-
16
-
-
0037071874
-
A change in the conformation of prions accompanies the emergence of a new prion strain
-
Peretz D, Williamson RA, Legname G, Matsunaga Y, Vergara J, et al. (2002) A change in the conformation of prions accompanies the emergence of a new prion strain. Neuron 34: 921-932.
-
(2002)
Neuron
, vol.34
, pp. 921-932
-
-
Peretz, D.1
Williamson, R.A.2
Legname, G.3
Matsunaga, Y.4
Vergara, J.5
-
17
-
-
0028102794
-
Transmission of Creutzfeldt-Jakob disease from humans to transgenic mice expressing chimeric human-mouse prion protein
-
U S A
-
Telling GC, Scott M, Hsiao KK, Foster D, Yang SL, et al. (1994) Transmission of Creutzfeldt-Jakob disease from humans to transgenic mice expressing chimeric human-mouse prion protein. Proc Natl Acad Sci U S A 91: 9936-9940.
-
(1994)
Proc Natl Acad Sci
, vol.91
, pp. 9936-9940
-
-
Telling, G.C.1
Scott, M.2
Hsiao, K.K.3
Foster, D.4
Yang, S.L.5
-
18
-
-
13344293718
-
Unaltered susceptibility to BSE in transgenic mice expressing human prion protein
-
Collinge J, Sidle KCL, Meads J, Ironside J, Hill AF (1995) Unaltered susceptibility to BSE in transgenic mice expressing human prion protein. Nature 378: 779-783.
-
(1995)
Nature
, vol.378
, pp. 779-783
-
-
Collinge, J.1
Sidle, K.C.L.2
Meads, J.3
Ironside, J.4
Hill, A.F.5
-
19
-
-
18744362997
-
BSE prions propagate as either variant CJD-like or sporadic CJD-like prion strains in transgenic mice expressing human prion protein
-
Asante EA, Linehan JM, Desbruslais M, Joiner S, Gowland I, et al. (2002) BSE prions propagate as either variant CJD-like or sporadic CJD-like prion strains in transgenic mice expressing human prion protein. EMBO J 21: 6358-6366.
-
(2002)
EMBO J
, vol.21
, pp. 6358-6366
-
-
Asante, E.A.1
Linehan, J.M.2
Desbruslais, M.3
Joiner, S.4
Gowland, I.5
-
20
-
-
0037447071
-
Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene
-
U S A
-
Korth C, Kaneko K, Groth D, Heye N, Telling G, et al. (2003) Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene. Proc Natl Acad Sci U S A 100: 4784-4789.
-
(2003)
Proc Natl Acad Sci
, vol.100
, pp. 4784-4789
-
-
Korth, C.1
Kaneko, K.2
Groth, D.3
Heye, N.4
Telling, G.5
-
21
-
-
0344844524
-
Humanized knock-in mice expressing chimeric prion protein showed varied susceptibility to different human prions
-
Taguchi Y, Mohri S, Ironside JW, Muramoto T, Kitamoto T (2003) Humanized knock-in mice expressing chimeric prion protein showed varied susceptibility to different human prions. Am J Pathol 163: 2585-2593.
-
(2003)
Am J Pathol
, vol.163
, pp. 2585-2593
-
-
Taguchi, Y.1
Mohri, S.2
Ironside, J.W.3
Muramoto, T.4
Kitamoto, T.5
-
22
-
-
10044224475
-
Human prion protein with valine 129 prevents expression of variant CJD phenotype
-
Wadsworth JD, Asante EA, Desbruslais M, Linehan JM, Joiner S, et al. (2004) Human prion protein with valine 129 prevents expression of variant CJD phenotype. Science 306: 1793-1796.
-
(2004)
Science
, vol.306
, pp. 1793-1796
-
-
Wadsworth, J.D.1
Asante, E.A.2
Desbruslais, M.3
Linehan, J.M.4
Joiner, S.5
-
24
-
-
20444417775
-
Identification of the pathological prion protein allotypes in scrapie-infected heterozygous bank voles (Clethrionomys glareolus) by high-performance liquid chromatography-mass spectrometry
-
Cartoni C, Schininà ME, Maras B, Nonno R, Vaccari G, et al. (2005) Identification of the pathological prion protein allotypes in scrapie-infected heterozygous bank voles (Clethrionomys glareolus) by high-performance liquid chromatography-mass spectrometry. J Chromatogr A 1081: 122-126.
-
(2005)
J Chromatogr A
, vol.1081
, pp. 122-126
-
-
Cartoni, C.1
Schininà, M.E.2
Maras, B.3
Nonno, R.4
Vaccari, G.5
-
25
-
-
0032816292
-
Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects
-
Parchi P, Giese A, Capellari S, Brown P, Schulz-Schaeffer W, et al. (1999) Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects. Ann Neurol 46: 224-233.
-
(1999)
Ann Neurol
, vol.46
, pp. 224-233
-
-
Parchi, P.1
Giese, A.2
Capellari, S.3
Brown, P.4
Schulz-Schaeffer, W.5
-
26
-
-
4944246589
-
Predictors of survival in sporadic Creutzfeldt-Jakob disease and other human transmissible spongiform encephalopathies
-
Pocchiari M, Puopolo M, Croes EA, Budka H, Gelpi E, et al. (2004) Predictors of survival in sporadic Creutzfeldt-Jakob disease and other human transmissible spongiform encephalopathies. Brain 127: 2348-2359.
-
(2004)
Brain
, vol.127
, pp. 2348-2359
-
-
Pocchiari, M.1
Puopolo, M.2
Croes, E.A.3
Budka, H.4
Gelpi, E.5
-
27
-
-
0033180143
-
Prion protein glycotype analysis in familial and sporadic Creutzfeldt-Jakob disease patients
-
Cardone F, Liu QG, Petraroli R, Ladogana A, D'Alessandro M, et al. (1999) Prion protein glycotype analysis in familial and sporadic Creutzfeldt-Jakob disease patients. Brain Res Bull 49: 429-433.
-
(1999)
Brain Res Bull
, vol.49
, pp. 429-433
-
-
Cardone, F.1
Liu, Q.G.2
Petraroli, R.3
Ladogana, A.4
D'Alessandro, M.5
-
28
-
-
0015550206
-
Scrapie in mice: Agent-strain differences in the distribution and intensity of grey matter vacuolation
-
Fraser H, Dickinson AG (1973) Scrapie in mice: Agent-strain differences in the distribution and intensity of grey matter vacuolation. J Comp Pathol 83: 29-40.
-
(1973)
J Comp Pathol
, vol.83
, pp. 29-40
-
-
Fraser, H.1
Dickinson, A.G.2
-
29
-
-
0035957401
-
Adaptation of the bovine spongiform encephalopathy agent to primates and comparison with Creutzfeldt-Jakob disease: Implications for human health
-
U S A
-
Lasmezàs CI, Fournier JG, Nouvel V, Boe H, Marcé D, et al. (2001) Adaptation of the bovine spongiform encephalopathy agent to primates and comparison with Creutzfeldt-Jakob disease: Implications for human health. Proc Natl Acad Sci U S A 98: 4142-4147.
-
(2001)
Proc Natl Acad Sci
, vol.98
, pp. 4142-4147
-
-
Lasmezàs, C.I.1
Fournier, J.G.2
Nouvel, V.3
Boe, H.4
Marcé, D.5
-
30
-
-
0023265523
-
Temporary and permanent modifications to a single strain of mouse scrapie on transmission to rats and hamsters
-
Kimberlin RH, Cole S, Walker CA (1987) Temporary and permanent modifications to a single strain of mouse scrapie on transmission to rats and hamsters. J Gen Virol 68: 1875-1881.
-
(1987)
J Gen Virol
, vol.68
, pp. 1875-1881
-
-
Kimberlin, R.H.1
Cole, S.2
Walker, C.A.3
-
31
-
-
0032560124
-
Scrapie infectivity found in resistant species
-
Race R, Chesebro B (1998) Scrapie infectivity found in resistant species. Nature 392: 770.
-
(1998)
Nature
, vol.392
, pp. 770
-
-
Race, R.1
Chesebro, B.2
-
32
-
-
0034730170
-
Species barrier-independent prion replication in apparently resistant species
-
U S A
-
Hill AF, Joiner S, Linehan J, Desbruslais M, Lantos PL, et al. (2000) Species barrier-independent prion replication in apparently resistant species. Proc Natl Acad Sci U S A 97: 10248-10253.
-
(2000)
Proc Natl Acad Sci
, vol.97
, pp. 10248-10253
-
-
Hill, A.F.1
Joiner, S.2
Linehan, J.3
Desbruslais, M.4
Lantos, P.L.5
-
33
-
-
0032829127
-
Scrapie pathogenesis in subclinically infected B-cell-deficient mice
-
Frigg R, Klein MA, Hegyi I, Zinkernagel RM, Aguzzi A (1999) Scrapie pathogenesis in subclinically infected B-cell-deficient mice. J Virol 73: 9584-9588.
-
(1999)
J Virol
, vol.73
, pp. 9584-9588
-
-
Frigg, R.1
Klein, M.A.2
Hegyi, I.3
Zinkernagel, R.M.4
Aguzzi, A.5
-
34
-
-
0036168776
-
Chronic subclinical prion disease induced by low-dose inoculum
-
Thackray AM, Klein MA, Aguzzi A, Bujdoso R (2002) Chronic subclinical prion disease induced by low-dose inoculum. J Virol 76: 2510-2517.
-
(2002)
J Virol
, vol.76
, pp. 2510-2517
-
-
Thackray, A.M.1
Klein, M.A.2
Aguzzi, A.3
Bujdoso, R.4
-
35
-
-
0032559911
-
The prion's perplexing persistence
-
Aguzzi A, Weissmann C (1998) The prion's perplexing persistence. Nature 392: 763-764.
-
(1998)
Nature
, vol.392
, pp. 763-764
-
-
Aguzzi, A.1
Weissmann, C.2
-
36
-
-
0031942579
-
Mice with gene targeted prion protein alterations show that Prnp, Sinc and Prni are congruent
-
Moore RC, Hope J, McBride PA, McConnell I, Selfridge J, et al. (1998) Mice with gene targeted prion protein alterations show that Prnp, Sinc and Prni are congruent. Nat Genet 18: 118-125.
-
(1998)
Nat Genet
, vol.18
, pp. 118-125
-
-
Moore, R.C.1
Hope, J.2
McBride, P.A.3
McConnell, I.4
Selfridge, J.5
-
37
-
-
14744302246
-
Polymorphisms at codons 108 and 189 in murine PrP play distinct roles in the control of scrapie incubation time
-
Barron RM, Baybutt H, Tuzi NL, McCormack J, King D, et al. (2005) Polymorphisms at codons 108 and 189 in murine PrP play distinct roles in the control of scrapie incubation time. J Gen Virol 86: 859-868.
-
(2005)
J Gen Virol
, vol.86
, pp. 859-868
-
-
Barron, R.M.1
Baybutt, H.2
Tuzi, N.L.3
McCormack, J.4
King, D.5
-
38
-
-
0141514771
-
Sporadic and familial CJD: Classification and characterisation
-
Gambetti P, Kong Q, Zou W, Parchi P, Chen SG (2003) Sporadic and familial CJD: Classification and characterisation. Br Med Bull 66: 213-239.
-
(2003)
Br Med Bull
, vol.66
, pp. 213-239
-
-
Gambetti, P.1
Kong, Q.2
Zou, W.3
Parchi, P.4
Chen, S.G.5
-
39
-
-
17444393595
-
Transmission barriers for bovine, ovine, and human prions in transgenic mice
-
Scott MR, Peretz D, Nguyen HO, Dearmond SJ, Prusiner SB (2005) Transmission barriers for bovine, ovine, and human prions in transgenic mice. J Virol 79: 5259-5271.
-
(2005)
J Virol
, vol.79
, pp. 5259-5271
-
-
Scott, M.R.1
Peretz, D.2
Nguyen, H.O.3
Dearmond, S.J.4
Prusiner, S.B.5
-
40
-
-
0035903461
-
Changing a single amino acid in the N-terminus of murine PrP alters TSE incubation time across three species barriers
-
Barron RM, Thomson V, Jamieson E, Melton DW, Ironside J, et al. (2001) Changing a single amino acid in the N-terminus of murine PrP alters TSE incubation time across three species barriers. EMBO J 20: 5070-5078.
-
(2001)
EMBO J
, vol.20
, pp. 5070-5078
-
-
Barron, R.M.1
Thomson, V.2
Jamieson, E.3
Melton, D.W.4
Ironside, J.5
-
41
-
-
0035826236
-
Conformational diversity in a yeast prion dictates its seeding specificity
-
Chien P, Weissman JS (2001) Conformational diversity in a yeast prion dictates its seeding specificity. Nature 410: 223-227.
-
(2001)
Nature
, vol.410
, pp. 223-227
-
-
Chien, P.1
Weissman, J.S.2
-
42
-
-
0042358923
-
Generation of prion transmission barriers by mutational control of amyloid conformations
-
Chien P, DePace AH, Collins SR, Weissman JS (2003) Generation of prion transmission barriers by mutational control of amyloid conformations. Nature 424: 948-951.
-
(2003)
Nature
, vol.424
, pp. 948-951
-
-
Chien, P.1
DePace, A.H.2
Collins, S.R.3
Weissman, J.S.4
-
43
-
-
17044381327
-
Fibril conformation as the basis of species and strain-dependent seeding specificity of mammalian prion amyloids
-
Jones EM, Surewicz WK (2005) Fibril conformation as the basis of species and strain-dependent seeding specificity of mammalian prion amyloids. Cell 121: 63-72.
-
(2005)
Cell
, vol.121
, pp. 63-72
-
-
Jones, E.M.1
Surewicz, W.K.2
-
44
-
-
17044435107
-
Mechanism of cross-species prion transmission: An infectious conformation compatible with two highly divergent yeast prion proteins
-
Tanaka M, Chien P, Yonekura K, Weissman JS (2005) Mechanism of cross-species prion transmission: An infectious conformation compatible with two highly divergent yeast prion proteins. Cell 121: 49-62.
-
(2005)
Cell
, vol.121
, pp. 49-62
-
-
Tanaka, M.1
Chien, P.2
Yonekura, K.3
Weissman, J.S.4
-
45
-
-
0028882424
-
Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein
-
Telling GC, Scott M, Mastrianni J, Gabizon R, Torchia M, et al. (1995) Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein. Cell 83: 79-90.
-
(1995)
Cell
, vol.83
, pp. 79-90
-
-
Telling, G.C.1
Scott, M.2
Mastrianni, J.3
Gabizon, R.4
Torchia, M.5
-
47
-
-
10644241804
-
Protease-resistant human prion protein and ferritin are cotransported across Caco-2 epithelial cells: Implications for species barrier in prion uptake from the intestine
-
Mishra RS, Basu S, Gu Y, Luo X, Zou WQ, et al. (2004) Protease-resistant human prion protein and ferritin are cotransported across Caco-2 epithelial cells: Implications for species barrier in prion uptake from the intestine. J Neurosci 24: 11280-11290.
-
(2004)
J Neurosci
, vol.24
, pp. 11280-11290
-
-
Mishra, R.S.1
Basu, S.2
Gu, Y.3
Luo, X.4
Zou, W.Q.5
-
48
-
-
1542357669
-
Identification of a second bovine amyloidotic spongiform encephalopathy: Molecular similarities with sporadic Creutzfeldt-Jakob disease
-
U S A
-
Casalone C, Zanusso G, Acutis P, Ferrari S, Capucci L, et al. (2004) Identification of a second bovine amyloidotic spongiform encephalopathy: Molecular similarities with sporadic Creutzfeldt-Jakob disease. Proc Natl Acad Sci U S A 101: 3065-3070.
-
(2004)
Proc Natl Acad Sci
, vol.101
, pp. 3065-3070
-
-
Casalone, C.1
Zanusso, G.2
Acutis, P.3
Ferrari, S.4
Capucci, L.5
-
49
-
-
0014308027
-
The sequential development of the brain lesions of scrapie in three strains of mice
-
Fraser H, Dickinson AG (1968) The sequential development of the brain lesions of scrapie in three strains of mice. J Comp Pathol 78: 301-311.
-
(1968)
J Comp Pathol
, vol.78
, pp. 301-311
-
-
Fraser, H.1
Dickinson, A.G.2
|