A Drosophila model of the neurodegenerative disease SCA17 reveals a role of RBJ-J/Su(H) in modulating the pathological outcome

Human Molecular Genetics

Volumn 20, Issue 17, 2011, Pages 3424-3436

  Ren, Jie ^a,b   Jegga, Anil G ^b   Zhang, Minlu ^b,c   Deng, Jingyuan ^b,c   Liu, Junbo ^b   Gordon, Christopher B ^b   Aronow, Bruce J ^b   Lu, Long J ^b,c   Zhang, Bo ^a   Ma, Jun ^b  

^a Peking University   (China)

^b CINCINNATI CHILDREN S HOSPITAL RESEARCH FOUNDATION   (United States)

^c University of Cincinnati   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COMPLEMENTARY DNA; DROSOPHILA PROTEIN; IMMUNOGLOBULIN J RECOMBINATION SIGNAL SEQUENCE BINDING PROTEIN; MESSENGER RNA; NOTCH RECEPTOR; POLYGLUTAMINE; SUPPRESSOR OF HAIRLESS PROTEIN; TATA BINDING PROTEIN; TRANSCRIPTION FACTOR; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BINDING SITE; CLIMBING; CONTROLLED STUDY; CORRELATION ANALYSIS; DROSOPHILA; GENE CONSTRUCT; GENE OVEREXPRESSION; HISTOLOGY; HUMAN; IMMUNOPRECIPITATION; MICROARRAY ANALYSIS; NONHUMAN; PATHOPHYSIOLOGY; PHENOTYPE; PLASMID; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN PROTEIN INTERACTION; RETINA DEGENERATION; RNA INTERFERENCE; SCANNING ELECTROCHEMICAL MICROSCOPY; SIGNAL TRANSDUCTION; SPINOCEREBELLAR ATAXIA 17; SPINOCEREBELLAR DEGENERATION; SURVIVAL RATE; TRANSCRIPTION REGULATION; WESTERN BLOTTING;

ANIMALS; ANIMALS, GENETICALLY MODIFIED; BLOTTING, WESTERN; DROSOPHILA; DROSOPHILA PROTEINS; HUMANS; IMMUNOPRECIPITATION; MICROARRAY ANALYSIS; NEURODEGENERATIVE DISEASES; REPRESSOR PROTEINS; SPINOCEREBELLAR ATAXIAS; TATA-BOX BINDING PROTEIN;

EID: 80051704854     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddr251     Document Type: Article

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