Mitochondrial Dysfunction in NnaD Mutant Flies and Purkinje Cell Degeneration Mice Reveals a Role for Nna Proteins in Neuronal Bioenergetics

Neuron

Volumn 66, Issue 6, 2010, Pages 835-847

  Chakrabarti, Lisa ^a   Zahra, Rabaab ^b   Jackson, Stephen M ^c   Kazemi Esfarjani, Parsa ^b   Sopher, Bryce L ^c   Mason, Amanda G ^b   Toneff, Thomas ^d   Ryu, Soyoung ^c   Shaffer, Scott ^c   Kansy, Janice W ^b   Eng, Jeremiah ^c   Merrihew, Gennifer ^c   MacCoss, Michael J ^c   Murphy, Anne ^e   Goodlett, David R ^c   Hook, Vivian ^d   Bennett, Craig L ^b   Pallanck, Leo J ^c   La Spada, Albert R ^b,f,g  

^a UNIVERSITY OF NOTTINGHAM   (United Kingdom)

^b RADY CHILDREN'S HOSPITAL   (United States)

^c UNIVERSITY OF WASHINGTON MEDICAL CENTER   (United States)

^d UNIVERSITY OF CALIFORNIA SAN DIEGO   (United States)

^e San Diego   (United States)

^f UNIVERSITY OF CALIFORNIA   (United States)

^g UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Cellbio; Humdisease; Molneuro

Indexed keywords

CARBOXYPEPTIDASE; CYTOSOLIC CARBOXYPEPTIDASE 1; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELLULAR DISTRIBUTION; CONTROLLED STUDY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DROSOPHILA; EMBRYO; ENZYME LOCALIZATION; FEMALE; LOSS OF FUNCTION MUTATION; MALE; MOUSE; MUTANT; NERVE CELL DEGENERATION; NONHUMAN; NUCLEOTIDE SEQUENCE; ORTHOLOGY; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN PROCESSING; PROTEOMICS; PURKINJE CELL;

ANIMALS; ANIMALS, GENETICALLY MODIFIED; CELL LINE, TRANSFORMED; CEREBELLUM; DISEASE MODELS, ANIMAL; DROSOPHILA; DROSOPHILA PROTEINS; ENERGY METABOLISM; GENE EXPRESSION REGULATION; GREEN FLUORESCENT PROTEINS; GTP-BINDING PROTEINS; HUMANS; MALE; MICE; MICROSCOPY, ELECTRON, TRANSMISSION; MITOCHONDRIA; MITOCHONDRIAL DISEASES; MUTATION; NERVE DEGENERATION; PHENOTYPE; PROTEOMICS; PURKINJE CELLS; RETINA; RETINAL DEGENERATION; SERINE-TYPE D-ALA-D-ALA CARBOXYPEPTIDASE; TRANSDUCTION, GENETIC; TRANSFECTION;

EID: 77953933808     PISSN: 08966273     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.neuron.2010.05.024     Document Type: Article

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