Friedreich ataxia: A paradigm for mitochondrial diseases

Current Opinion in Genetics and Development

Volumn 12, Issue 3, 2002, Pages 272-277

  Puccio, Hélène ^a   Kœnig, Michel ^a  

^a INSTITUT DE GÉNÉTIQUE ET DE BIOLOGIE MOLÉCULAIRE ET CELLULAIRE   (France)

Author keywords

[No Author keywords available]

Indexed keywords

FRATAXIN; FREE RADICAL; IRON SULFUR PROTEIN; MITOCHONDRIAL DNA; IRON; IRON BINDING PROTEIN;

ANTIOXIDANT ACTIVITY; BIOGENESIS; FRIEDREICH ATAXIA; HOMEOSTASIS; HUMAN; IN VITRO STUDY; MITOCHONDRION; NONHUMAN; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN FUNCTION; REVIEW; ANIMAL; BIOSYNTHESIS; GENETICS; METABOLISM; MOUSE; PHYSIOLOGY;

ATAXIA;

ANIMALS; FRIEDREICH ATAXIA; HOMEOSTASIS; HUMANS; IRON; IRON-BINDING PROTEINS; IRON-SULFUR PROTEINS; MICE; MITOCHONDRIA; OXIDATIVE STRESS;

EID: 0036603021     PISSN: 0959437X     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0959-437X(02)00298-8     Document Type: Review

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