The bile salt export pump: Clinical and experimental aspects of genetic and acquired cholestatic liver disease

Seminars in Liver Disease

Volumn 30, Issue 2, 2010, Pages 125-133

  Lam, Ping ^a   Soroka, Carol J ^a   Boyer, James L ^a  

^a YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

ATP binding cassette (ABC) transporters; Bile salt export pump (BSEP) mutations; Cholestasis; Polymorphisms; Progressive familial intrahepatic cholestasis; Recycling; Trafficking; Ubiquitination

Indexed keywords

BILE SALT; CARRIER PROTEIN; PROTEIN ABCB11; PROTEIN BSEP; UNCLASSIFIED DRUG;

CHOLESTASIS; GENE MUTATION; HUMAN; INTRAHEPATIC CHOLESTASIS; NONHUMAN; PREGNANCY DISORDER; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FAMILY; PROTEIN FUNCTION; REVIEW;

ANIMALS; ATP-BINDING CASSETTE TRANSPORTERS; BILE ACIDS AND SALTS; BILE CANALICULI; CHOLESTASIS, INTRAHEPATIC; ENDOPLASMIC RETICULUM; GLYCOSYLATION; HUMANS; MICE; MICE, KNOCKOUT; MODELS, ANIMAL; MUTATION; PHOSPHORYLATION; UBIQUITINATION;

EID: 77951613087     PISSN: 02728087     EISSN: 10988971     Source Type: Journal    
DOI: 10.1055/s-0030-1253222     Document Type: Review

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