Degradation of the Bile salt export pump at endoplasmic reticulum in progressive familial Intrahepatic cholestasis type II

Hepatology

Volumn 48, Issue 5, 2008, Pages 1558-1569

  Wang, Lin ^a   Dong, Huiping ^a   Soroka, Carol J ^a   Wei, Ning Wei ^a   Boyer, James L ^a   Hochstrasser, Mark ^a  

^a YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BILE SALT EXPORT PUMP; CARRIER PROTEIN; CELL PROTEIN; GLYCEROL; MUTANT PROTEIN; PROTEASOME; PROTEASOME INHIBITOR; PROTEIN HRD1; PROTEIN RMA1; PROTEIN TEB4; UBIQUITIN PROTEIN LIGASE E3; UNCLASSIFIED DRUG; ABC TRANSPORTER; ABCB11 PROTEIN, HUMAN; GLYCOPROTEIN P; MARCH6 PROTEIN, HUMAN; MEMBRANE PROTEIN; SYVN1 PROTEIN, HUMAN; UBIQUITIN PROTEIN LIGASE;

ARTICLE; CELL STRAIN HEK293; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; GENE MUTATION; HUMAN; HUMAN CELL; INTRAHEPATIC CHOLESTASIS; LOW TEMPERATURE; LYSOSOME; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROGRESSIVE FAMILIAL INTRAHEPATIC CHOLESTASIS TYPE 2; PROTEIN DEGRADATION; PROTEIN DOMAIN; PROTEIN EXPRESSION; PROTEIN FOLDING; PROTEIN PROCESSING; PROTEIN STABILITY; QUALITY CONTROL; SIGNAL TRANSDUCTION; UBIQUITINATION; WILD TYPE; BILE; CELL LINE; DISEASE COURSE; GENETIC TRANSFECTION; GENETICS; KIDNEY; METABOLISM; PATHOLOGY; PLASMID; SECRETION;

ATP-BINDING CASSETTE TRANSPORTERS; BILE; CELL LINE; CHOLESTASIS, INTRAHEPATIC; DISEASE PROGRESSION; ENDOPLASMIC RETICULUM; HUMANS; KIDNEY; MEMBRANE PROTEINS; P-GLYCOPROTEIN; PLASMIDS; TRANSFECTION; UBIQUITIN-PROTEIN LIGASES;

EID: 56149102929     PISSN: 02709139     EISSN: None     Source Type: Journal    
DOI: 10.1002/hep.22499     Document Type: Article

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