Differential DNA damage signaling accounts for distinct neural apoptotic responses in ATLD and NBS

Genes and Development

Volumn 23, Issue 2, 2009, Pages 171-180

  Shull, Erin R P ^a,b   Lee, Youngsoo ^a   Nakane, Hironobu ^a,c   Stracker, Travis H ^d,e   Zhao, Jingfeng ^a   Russell, Helen R ^a   Petrini, John H J ^d,e   McKinnon, Peter J ^a,b  

^a ST JUDE CHILDREN S RESEARCH HOSPITAL   (United States)

^b UNIVERSITY OF TENNESSEE HEALTH SCIENCE CENTER   (United States)

^c TOTTORI UNIVERSITY   (Japan)

^d MEMORIAL SLOAN KETTERING CANCER CENTER   (United States)

^e Weill Cornell Graduate School of Biomedical Sciences   (United States)

Author keywords

A T; ATLD; DNA damage; NBS; Neurodegeneration

Indexed keywords

ATM PROTEIN; CRE RECOMBINASE; LIG4 PROTEIN; MRE11 PROTEIN; NIBRIN; POLYDEOXYRIBONUCLEOTIDE SYNTHASE; PROTEIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; ATAXIA TELANGIECTASIA; CONTROLLED STUDY; DNA DAMAGE; EMBRYO; GENE MUTATION; GENOTOXICITY; IONIZING RADIATION; MICROCEPHALY; MOUSE; NERVOUS SYSTEM; NEUROPATHOLOGY; NIJMEGEN BREAKAGE SYNDROME; NONHUMAN; PRIORITY JOURNAL; PROTEIN PHOSPHORYLATION;

ANIMALS; APOPTOSIS; ATAXIA TELANGIECTASIA; BRAIN; CELL CYCLE PROTEINS; DNA DAMAGE; DNA LIGASES; DNA REPAIR ENZYMES; DNA-BINDING PROTEINS; ENZYME ACTIVATION; FEMALE; MALE; MICE; MICE, TRANSGENIC; MICROCEPHALY; MUTATION; NEURONS; NIJMEGEN BREAKAGE SYNDROME; NUCLEAR PROTEINS; PROTEIN-SERINE-THREONINE KINASES; RADIATION, IONIZING; SIGNAL TRANSDUCTION; TUMOR SUPPRESSOR PROTEINS;

ATAXIA TELANGIECTASIA; MUS; NES;

EID: 58849135489     PISSN: 08909369     EISSN: 15495477     Source Type: Journal    
DOI: 10.1101/gad.1746609     Document Type: Article

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