Protein quality control: The who's who, the where's and therapeutic escapes

Histochemistry and Cell Biology

Volumn 129, Issue 2, 2008, Pages 163-177

  Roth, Jürgen ^a   Yam, Gary Hin Fai ^a,b   Fan, Jingyu ^a,c   Hirano, Kiyoko ^a,d   Gaplovska Kysela, Katarina ^a   Le Fourn, Valerie ^a   Guhl, Bruno ^a   Santimaria, Roger ^a   Torossi, Tania ^a   Ziak, Martin ^a   Zuber, Christian ^a  

^a UNIVERSITY OF ZURICH   (Switzerland)

^b CHINESE UNIVERSITY OF HONG KONG   (Hong Kong)

^c PEKING UNIVERSITY HEALTH SCIENCE CENTER   (China)

^d NOGUCHI INSTITUTE   (Japan)

Author keywords

Chemical chaperones; EDEM1; Endomannosidase; ERAD; Glucosidase II; Glucosyltransferase; Protein folding disease

Indexed keywords

1 DEOXYGALACTONORIJIMYCIN; 4 PHENYLBUTYRIC ACID; CELL PROTEIN; CHAPERONE; DIMETHYL SULFOXIDE; EDEM1 PROTEIN; ENDOMANNOSIDASE; ENZYME INHIBITOR; GLUCOSE; GLYCEROL; MANNOSIDASE; POLYOL; PROTEIN; UNCLASSIFIED DRUG;

ANTIBODY LABELING; CELL ORGANELLE; CELLULAR DISTRIBUTION; ELECTRON MICROSCOPY; ENDOPLASMIC RETICULUM; GOLGI COMPLEX; HUMAN; IMMUNOCYTOCHEMISTRY; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEFICIENCY; PROTEIN FOLDING; PROTEIN FUNCTION; PROTEIN QUALITY; PROTEIN TRANSPORT; REVIEW; ROUGH ENDOPLASMIC RETICULUM;

DRUG DESIGN; ENDOPLASMIC RETICULUM; HUMANS; MEMBRANE PROTEINS; METABOLISM, INBORN ERRORS; MOLECULAR CHAPERONES; PROTEIN FOLDING; PROTEINS;

EID: 39149084378     PISSN: 09486143     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00418-007-0366-7     Document Type: Review

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