Defective aquaporin-2 trafficking in nephrogenic diabetes insipidus and correction by chemical chaperones

Journal of Clinical Investigation

Volumn 101, Issue 10, 1998, Pages 2257-2267

  Tamarappoo, B K ^a   Verkman, A S ^a,b  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

Glycerol; Kidney; Protein folding; Urinary concentrating; Water transport

Indexed keywords

AQUAPORIN; AQUAPORIN 2; CHAPERONE; DIMETHYL SULFOXIDE; GLYCEROL; TRANSMEMBRANE CONDUCTANCE REGULATOR; TRIMETHYLAMINE OXIDE; UNCLASSIFIED DRUG;

ANIMAL CELL; ARTICLE; CELLULAR DISTRIBUTION; ENDOPLASMIC RETICULUM; GENE MUTATION; KIDNEY CONCENTRATING CAPACITY; NEPHROGENIC DIABETES INSIPIDUS; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN FOLDING; PROTEIN PROCESSING; PROTEIN STABILITY; WATER PERMEABILITY; WATER TRANSPORT; XENOPUS LAEVIS;

EID: 0032524048     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI2303     Document Type: Article

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