Modulation of ΔF508 cystic fibrosis transmembrane regulator trafficking and function with 4-phenylbutyrate and flavonoids

American Journal of Respiratory Cell and Molecular Biology

Volumn 31, Issue 3, 2004, Pages 351-357

  Lim, Meerana ^a   McKenzie, Karen ^a   Floyd, Alexandra D ^a   Kwon, Edwin ^a   Zeitlin, Pamela L ^a  

^a JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

4 PHENYLBUTYRIC ACID; APIGENIN; CHLORIDE ION; FLAVANOID; GENISTEIN; KAEMPFEROL; QUERCETIN; TRANSMEMBRANE CONDUCTANCE REGULATOR; 4-PHENYLBUTYRIC ACID; ARYLBUTYRIC ACID DERIVATIVE; CFTR PROTEIN, HUMAN; CHAPERONE; CHLORIDE; FLAVONOID;

ARTICLE; CHLORIDE CONDUCTANCE; CONTROLLED STUDY; DRUG EFFECT; DRUG POTENTIATION; HUMAN; HUMAN CELL; IMMUNOBLOTTING; IMMUNOFLUORESCENCE; ION TRANSPORT; PROTEIN LOCALIZATION; PROTEIN PROCESSING; CYSTIC FIBROSIS; DOSE RESPONSE; DRUG COMBINATION; GENETICS; METABOLISM; PATHOPHYSIOLOGY; PHYSIOLOGY; PROTEIN FOLDING; PROTEIN TRANSPORT; RESPIRATORY TRACT MUCOSA; UPREGULATION;

CHLORIDES; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; DOSE-RESPONSE RELATIONSHIP, DRUG; DRUG THERAPY, COMBINATION; FLAVONOIDS; HUMANS; MOLECULAR CHAPERONES; PHENYLBUTYRATES; PROTEIN FOLDING; PROTEIN TRANSPORT; RESPIRATORY MUCOSA; UP-REGULATION;

EID: 4444371518     PISSN: 10441549     EISSN: None     Source Type: Journal    
DOI: 10.1165/rcmb.2002-0086OC     Document Type: Article

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