Polyglutamine expansions: Proteolysis, chaperones, and the dangers of promiscuity

Neuron

Volumn 26, Issue 1, 2000, Pages 9-12

  Ferrigno, Paul ^a   Silver, Pamela A ^a  

^a HARVARD MEDICAL SCHOOL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CHAPERONE; MUTANT PROTEIN; POLYGLUTAMINE;

ATAXIA; CYTOTOXICITY; GENETIC TRANSCRIPTION; HELA CELL; HUMAN; HUMAN CELL; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; SHORT SURVEY; TANDEM REPEAT;

EID: 0033679283     PISSN: 08966273     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0896-6273(00)81132-0     Document Type: Review

References (20)

1. H Blumberg P.A Silver Nature 349 1991 627 630
2. J.M Boutell P Thomas J.W Neal V.J Weston J Duce P.S Harper A.L Jones Hum. Mol. Genet. 8 1999 1647 1655
3. Y Chai S.L Koppenhafer N Bonini H.L Paulson J. Neurosci. 19 1999 10338 10347
4. C.J Cummings E Reinstein Y Sun B Antallfy Y.-H Jiang A Ciechanover H.T Orr A.L Beaudet H.Y Zoghbi Neuron 24 1999 879 892
5. S.W Davies M Turmaine B.A Cozens M DiFiglia A.H Sharp C.A Ross E Scherzinger E.E Wanker L Mangiarini G.P Bates Cell 90 1997 537 548
6. M.I Diamond M.R Robinson K.R Yamamoto Proc. Natl. Acad. Sci. USA 97 2000 657 661
7. A.T Hoogeveen R Willemsen N Meyer K.E de Rooij R.A Roos G.J van Ommen H Galjaard Hum. Mol. Genet. 2 1993 2069 2073
8. P Kazemi-Esfarjani S Benzer Science 287 2000 1837 1840
9. I.A Klement P.J Skinner M.D Kaytor H Yi S.M Hersch H.B Clark H.Y Zoghbi H.T Orr Cell 95 1998 41 53
10. S Krobitsch S Lindquist Proc. Natl. Acad. Sci. USA 97 2000 1589 1594
11. S.-H Li A.L Cheng H Li X.-J Li J. Neurosci. 19 1999 5159 5172
12. X Lin B Antallfy D Kang H.T Orr H.Y Zoghbi Nat. Neurosci. 3 2000 157 163
13. A Lunkes J.-L Mandel Hum. Mol. Genet. 7 1998 1355 1361
14. L Mangiarini K Sathasivam M Seller B Cozens C Hetherington M Lawton Y Trottier H Lehrach S.W Davies G.P Bates Cell 87 1996 493 506
15. V.O Ona M Li J.P Vonstattel L.J Andrews S.Q Khan W.M Chung A.S Frey A.S Menon X.J Li P.E Stieg Nature 399 1999 263 267
16. M.K Perez H.L Paulson S.J Pendse S.J Saionz N.M Bonini R.N Pittman J. Cell Biol. 143 1998 1457 1470
17. M.F Perutz T Johnson M Suzuki J.T Finch Proc. Natl. Acad. Sci. USA 91 1994 5355 5358
18. I Sanchez P Juo A Kazizaka J Blenis J Yuan Neuron 22 1999 623 633
19. F Saudou S Finkbeiner D Devys M.E Greenberg Cell 95 1998 55 66
20. A Yamamoto J.J Lucas R Hen Cell 101 2000 57 66