Protein stability, folding and misfolding in human PGK1 deficiency

Biomolecules

Volumn 3, Issue 4, 2013, Pages 1030-1052

  Valentini, Giovanna ^a   Maggi, Maristella ^a   Pey, Angel L ^b  

^a UNIVERSITY OF PAVIA   (Italy)

^b UNIVERSITY OF GRANADA   (Spain)

Author keywords

Conformational disease; Kinetic stability; Molecular chaperones; Pharmacological therapies; Protein aggregation; Protein misfolding; Proteolysis; Thermodynamic stability

Indexed keywords

CHAPERONE; MUTANT PROTEIN;

ENZYME ACTIVITY; ENZYME DEFICIENCY; ENZYME KINETICS; ENZYME STRUCTURE; ESCHERICHIA COLI; GENE; GENE MUTATION; GENETIC DISORDER; HEMOLYTIC ANEMIA; HUMAN; LIGAND BINDING; MYOPATHY; NEUROLOGIC DISEASE; NONHUMAN; PGK 1 GENE; PROTEIN AGGREGATION; PROTEIN DEGRADATION; PROTEIN DENATURATION; PROTEIN EXPRESSION; PROTEIN FOLDING; PROTEIN MISFOLDING; PROTEIN STABILITY; RETICULOCYTE; REVIEW; THERMODYNAMICS; X CHROMOSOME RECESSIVE DISORDER;

EID: 85016346854     PISSN: None     EISSN: 2218273X     Source Type: Journal    
DOI: 10.3390/biom3041030     Document Type: Review

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