Idiopathic pulmonary fibrosis: A genetic disease that involves mucociliary dysfunction of the peripheral airways

Physiological Reviews

Volumn 96, Issue 4, 2016, Pages 1567-1591

  Evans, Christopher M ^a,b   Fingerlin, Tasha E ^a,b   Schwarz, Marvin I ^a,b   Lynch, David ^a,b   Kurche, Jonathan ^a,b   Warg, Laura ^a,b   Yang, Ivana V ^a,b   Schwartz, David A ^a,b  

^a UNIVERSITY OF COLORADO SCHOOL OF MEDICINE   (United States)

^b DEPARTMENT OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

MUCIN 5B; MUC5B PROTEIN, HUMAN;

AIRWAY; ALLELE; ARTICLE; FIBROSING ALVEOLITIS; GAIN OF FUNCTION MUTATION; GENE; GENE EXPRESSION; GENE LOCUS; GENETIC RISK; GENETIC VARIABILITY; HUMAN; LUNG ALVEOLUS EPITHELIUM; MUC5B GENE; MUCOCILIARY CLEARANCE; NONHUMAN; PARN GENE; PATHOGENESIS; PRIORITY JOURNAL; PROMOTER REGION; PROTEIN EXPRESSION; RTEL1 GENE; SFTPA2 GENE; SFTPC GENE; TERC GENE; TERT GENE; ANIMAL; BRONCHIOLE; GENETIC PREDISPOSITION; GENETICS; LUNG ALVEOLUS; PATHOPHYSIOLOGY; RESPIRATORY MUCOSA;

ANIMALS; BRONCHIOLES; GENETIC PREDISPOSITION TO DISEASE; HUMANS; IDIOPATHIC PULMONARY FIBROSIS; MUCIN-5B; MUCOCILIARY CLEARANCE; PULMONARY ALVEOLI; RESPIRATORY MUCOSA;

EID: 84988664684     PISSN: 00319333     EISSN: 15221210     Source Type: Journal    
DOI: 10.1152/physrev.00004.2016     Document Type: Article

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