Genetic studies provide clues on the pathogenesis of idiopathic pulmonary fibrosis

DMM Disease Models and Mechanisms

Volumn 6, Issue 1, 2013, Pages 9-17

  Kropski, Jonathan A ^a   Lawson, William E ^a,b   Young, Lisa R ^a,c   Blackwell, Timothy S ^a,b,c  

^a Division of Allergy   (United States)

^b VETERANS AFFAIRS MEDICAL CENTER   (United States)

^c VANDERBILT UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ACTIVATING TRANSCRIPTION FACTOR 6; MUCIN 5B; SURFACTANT PROTEIN A; SURFACTANT PROTEIN B; SURFACTANT PROTEIN C; TELOMERASE REVERSE TRANSCRIPTASE;

ADULT; ARTICLE; CARBOXY TERMINAL SEQUENCE; CASE REPORT; CELL AGING; CELL DAMAGE; COMPUTER ASSISTED TOMOGRAPHY; COUGHING; DISEASE COURSE; DNA DAMAGE; DNA REPAIR; DYSPNEA; ENDOPLASMIC RETICULUM STRESS; FAMILY HISTORY; FIBROSING ALVEOLITIS; GENE MUTATION; GENE SEQUENCE; GENETIC VARIABILITY; GENETICS; HUMAN; LUNG DIFFUSION CAPACITY; LUNG FUNCTION TEST; MALE; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN UNFOLDING; SEROLOGY; TELOMERE;

CELL AGING; DNA DAMAGE; DNA REPAIR; ENDOPLASMIC RETICULUM STRESS; GENETIC VARIATION; HERMANSKI-PUDLAK SYNDROME; HUMANS; IDIOPATHIC PULMONARY FIBROSIS; MALE; MIDDLE AGED; MODELS, GENETIC; MUCIN-5B; MUTATION; PULMONARY SURFACTANT-ASSOCIATED PROTEIN A; PULMONARY SURFACTANT-ASSOCIATED PROTEIN C; RNA; TELOMERASE; TELOMERE SHORTENING; UNFOLDED PROTEIN RESPONSE;

EID: 84872054447     PISSN: 17548403     EISSN: 17548411     Source Type: Journal    
DOI: 10.1242/dmm.010736     Document Type: Article

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