Phenotypic heterogeneity of monogenic frontotemporal dementia

Frontiers in Aging Neuroscience

Volumn 7, Issue SEP, 2015, Pages

  Benussi, Alberto ^a   Padovani, Alessandro ^a   Borroni, Barbara ^a  

^a UNIVERSITY OF BRESCIA   (Italy)

Author keywords

Frontotemporal dementia; Frontotemporal lobar degeneration; Genetics; Mutation; Neuroimaging

Indexed keywords

CHARGED MULTIVESICULAR BODY PROTEIN 2B; FUSED IN SARCOMA PROTEIN; HEXANUCLEOTIDE REPEAT EXPANSION IN INTRON 1 OF THE CHROMOSOME 9 OPEN READING FRAME 72 PROTEIN; MICROTUBULE ASSOCIATED PROTEIN; NUCLEIC ACID BINDING PROTEIN; PROGRANULIN; TAR DNA BINDING PROTEIN; UNCLASSIFIED DRUG; VALOSIN CONTAINING PROTEIN;

AUTOSOMAL DOMINANT INHERITANCE; C9ORF72 GENE; CHMP2B GENE; DCTN1 GENE; DEMENTIA; FAMILY HISTORY; FRONTOTEMPORAL DEMENTIA; FUS GENE; GENE; GENE MUTATION; GENETIC HETEROGENEITY; GRN GENE; HUMAN; MAPT GENE; MOTOR DYSFUNCTION; MOTOR NEURON DISEASE; PARKINSONISM; PHENOTYPE; PRIMARY PROGRESSIVE APHASIA; PROGRESSIVE SUPRANUCLEAR PALSY; REVIEW; TARDBP GENE; TREM2 GENE; VCP GENE;

EID: 84946548438     PISSN: None     EISSN: 16634365     Source Type: Journal    
DOI: 10.3389/fnagi.2015.00171     Document Type: Review

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