Coenzyme Q and the respiratory Chain: Coenzyme Q pool and mitochondrial supercomplexes

Molecular Syndromology

Volumn 5, Issue 3-4, 2014, Pages 119-140

  Enriquez, José Antonio ^a   Lenaz, Giorgio ^b  

^a CENTRO NACIONAL DE INVESTIGACIONES CARDIOVASCULARES CNIC   (Spain)

^b UNIVERSITY OF BOLOGNA   (Italy)

Author keywords

Coenzyme Q; Mitochondria; Respirasome; Respiratory chain; Respiratory complexes; Supercomplexes; Ubiquinone

Indexed keywords

CYTOCHROME C OXIDASE; PHOSPHOLIPID DERIVATIVE; REACTIVE OXYGEN METABOLITE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); SUCCINATE DEHYDROGENASE (UBIQUINONE); UBIDECARENONE; UBIQUINOL CYTOCHROME C REDUCTASE; UBIQUINONE; MITOCHONDRIAL SUPERCOMPLEX; MULTIENZYME COMPLEX; PHOSPHOLIPID; UNCLASSIFIED DRUG;

ANTIOXIDANT ACTIVITY; ARTICLE; BIOENERGY; BIOGENESIS; CHEMICAL STRUCTURE; COENZYME Q DEFICIENCY; COMPLEX I DEFICIENCY; COMPLEX II DEFICIENCY; COMPLEX III DEFICIENCY; CYTOCHROME C OXIDASE DEFICIENCY; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVITY; ENZYME DEFICIENCY; ENZYME KINETICS; ENZYME MECHANISM; ENZYME PHOSPHORYLATION; ENZYME PURIFICATION; ENZYME STABILITY; ENZYME SYNTHESIS; ENZYME THERAPY; HUMAN; MITOCHONDRIAL MEMBRANE; MITOCHONDRIAL MEMBRANE POTENTIAL; MITOCHONDRIAL RESPIRATION; NONHUMAN; OXIDATIVE PHOSPHORYLATION; PLASTICITY; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN FUNCTION; PROTEIN PROCESSING; STEADY STATE; ENZYME STRUCTURE; MEMBRANE POTENTIAL; SUPPLEMENTATION;

EID: 84904003668     PISSN: 16618769     EISSN: 16618777     Source Type: Journal    
DOI: 10.1159/000363364     Document Type: Article

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