-
2
-
-
0020974404
-
An X-linked mitochondrial disease affecting cardiac muscle, skeletal muscle and neutrophil leucocytes
-
Barth, P. G., Scholte, H. R., Berden, J. A., Van der Klei-Van Moorsel, J. M., Luyt-Houwen, I. E., Van't Veer-Korthof, E. T., Van der Harten, J. J., and Sobotka-Plojhar, M. A. (1983). An X-linked mitochondrial disease affecting cardiac muscle, skeletal muscle and neutrophil leucocytes. J. Neurol. Sci. 62, 327-355.
-
(1983)
J. Neurol. Sci.
, vol.62
, pp. 327-355
-
-
Barth, P.G.1
Scholte, H.R.2
Berden, J.A.3
Van Der Klei-Van Moorsel, J.M.4
Luyt-Houwen, I.E.5
Van't Veer-Korthof, E.T.6
Van Der Harten, J.J.7
Sobotka-Plojhar, M.A.8
-
3
-
-
2142765298
-
X-linked cardioskeletal myopathy and neutropenia (Barth syndrome): An update
-
Barth, P. G., Valianpour, F., Bowen, V. M., Lam, J., Duran, M., Vaz, F. M., and Wanders, R. J. (2004). X-linked cardioskeletal myopathy and neutropenia (Barth syndrome): an update. Am. J. Med. Genet. 126, 349-354.
-
(2004)
Am. J. Med. Genet.
, vol.126
, pp. 349-354
-
-
Barth, P.G.1
Valianpour, F.2
Bowen, V.M.3
Lam, J.4
Duran, M.5
Vaz, F.M.6
Wanders, R.J.7
-
4
-
-
0029869035
-
X-linked cardioskeletal myopathy and neutropenia (Barth syndrome): Respiratory-chain abnormalities in cultured fibroblasts
-
Barth, P. G., Van den Bogert, C., Bolhuis, P. A., Scholte, H. R., van Gennip, A. H., Schutgens, R. B., and Ketel, A. G. (1996). X-linked cardioskeletal myopathy and neutropenia (Barth syndrome): respiratory-chain abnormalities in cultured fibroblasts. J. Inherit. Metab. Dis. 19, 157-160.
-
(1996)
J. Inherit. Metab. Dis.
, vol.19
, pp. 157-160
-
-
Barth, P.G.1
Van Den Bogert, C.2
Bolhuis, P.A.3
Scholte, H.R.4
Van Gennip, A.H.5
Schutgens, R.B.6
Ketel, A.G.7
-
5
-
-
0033505467
-
X-linked cardioskeletal myopathy and neutropenia (Barth syndrome)-MIM 302060
-
Barth, P. G., Wanders, R. J., and Vreken, P. (1999). X-linked cardioskeletal myopathy and neutropenia (Barth syndrome)-MIM 302060. J. Pediatr. 135, 273-276.
-
(1999)
J. Pediatr.
, vol.135
, pp. 273-276
-
-
Barth, P.G.1
Wanders, R.J.2
Vreken, P.3
-
6
-
-
0029963145
-
A novel X-linked gene, G4.5. is responsible for Barth syndrome
-
Bione, S., D'Adamo, P., Maestrini, E., Gedeon, A. K., Bolhuis, P. A., and Toniolo, D. (1996). A novel X-linked gene, G4.5. is responsible for Barth syndrome. Nat. Genet. 12, 385-389.
-
(1996)
Nat. Genet.
, vol.12
, pp. 385-389
-
-
Bione, S.1
D'Adamo, P.2
Maestrini, E.3
Gedeon, A.K.4
Bolhuis, P.A.5
Toniolo, D.6
-
7
-
-
0032570865
-
The respiratory chain in yeast behaves as a single functional unit
-
Boumans, H., Grivell, L. A., and Berden, J. A. (1998). The respiratory chain in yeast behaves as a single functional unit. J. Biol. Chem. 273, 4872-4877.
-
(1998)
J. Biol. Chem.
, vol.273
, pp. 4872-4877
-
-
Boumans, H.1
Grivell, L.A.2
Berden, J.A.3
-
9
-
-
16944366521
-
The X-linked gene G4.5 is responsible for different infantile dilated cardiomyopathies
-
D'Adamo, P. et al. (1997). The X-linked gene G4.5 is responsible for different infantile dilated cardiomyopathies. Am. J. Hum. Genet. 61, 862-867.
-
(1997)
Am. J. Hum. Genet.
, vol.61
, pp. 862-867
-
-
D'Adamo, P.1
-
10
-
-
0030845840
-
The Tim core complex defines the number of mitochondrial translocation contact sites and can hold arrested preproteins in the absence of matrix Hsp70-Tim44
-
Dekker, P.J.T., Martin, F., Maarse, A. C., Bömer, U., Müller, H., Guiard, B., Meijer, M., Rassow, J., and Pfanner, N. (1997). The Tim core complex defines the number of mitochondrial translocation contact sites and can hold arrested preproteins in the absence of matrix Hsp70-Tim44. EMBO J. 16, 5408-5419.
-
(1997)
EMBO J.
, vol.16
, pp. 5408-5419
-
-
Dekker, P.J.T.1
Martin, F.2
Maarse, A.C.3
Bömer, U.4
Müller, H.5
Guiard, B.6
Meijer, M.7
Rassow, J.8
Pfanner, N.9
-
11
-
-
1842329159
-
Tom5 functionally links mitochondrial preprotein receptors to the general import pore
-
Dietmeier, K., Hönlinger, A., Bömer, U., Dekker, P.J.T., Eckershkorn, C., Lottspeich, F., Lúbrich, M., and Pfanner, N. (1997). Tom5 functionally links mitochondrial preprotein receptors to the general import pore. Nature 388, 195-200.
-
(1997)
Nature
, vol.388
, pp. 195-200
-
-
Dietmeier, K.1
Hönlinger, A.2
Bömer, U.3
Dekker, P.J.T.4
Eckershkorn, C.5
Lottspeich, F.6
Lúbrich, M.7
Pfanner, N.8
-
12
-
-
0037972522
-
Mitochondrial respiratory-chain diseases
-
DiMauro, S., and Schon, E. A. (2003). Mitochondrial respiratory-chain diseases. N. Engl. J. Med. 348, 2656-2668.
-
(2003)
N. Engl. J. Med.
, vol.348
, pp. 2656-2668
-
-
Dimauro, S.1
Schon, E.A.2
-
13
-
-
14744270722
-
Structure of a mitochondrial supercomplex formed by respiratory-chain complexes I and III
-
Dudkina, N. V., Eubel, H., Keegstra, W., Boekema, E. J., and Braun, H. P. (2005). Structure of a mitochondrial supercomplex formed by respiratory-chain complexes I and III. Proc. Natl. Acad. Sci. USA 102, 3225-3229.
-
(2005)
Proc. Natl. Acad. Sci. USA
, vol.102
, pp. 3225-3229
-
-
Dudkina, N.V.1
Eubel, H.2
Keegstra, W.3
Boekema, E.J.4
Braun, H.P.5
-
14
-
-
10744229056
-
Pam16 has an essential role in the mitochondrial protein import motor
-
Frazier, A. E. et al. (2004). Pam16 has an essential role in the mitochondrial protein import motor. Nat. Struct. Mol. Biol. 11, 226-233.
-
(2004)
Nat. Struct. Mol. Biol.
, vol.11
, pp. 226-233
-
-
Frazier, A.E.1
-
16
-
-
0347595327
-
Aberrant cardiolipin metabolism in the yeast taz1 mutant: A model for Barth syndrome
-
Gu, Z., Valianpour, F., Chen, S., Vaz, F. M., Hakkaart, G. A., Wanders, R. J., and Greenberg, M. L. (2004). Aberrant cardiolipin metabolism in the yeast taz1 mutant: a model for Barth syndrome. Mol. Microbiol. 51, 149-158.
-
(2004)
Mol. Microbiol.
, vol.51
, pp. 149-158
-
-
Gu, Z.1
Valianpour, F.2
Chen, S.3
Vaz, F.M.4
Hakkaart, G.A.5
Wanders, R.J.6
Greenberg, M.L.7
-
17
-
-
0022895277
-
Transport into mitochondria and intramitochondrial sorting of the Fe/S protein of ubiquinol-cytochrome c reductase
-
Hartl, F. U., Schmidt, B., Wachter, E., Weiss, H., and Neupert, W. (1986). Transport into mitochondria and intramitochondrial sorting of the Fe/S protein of ubiquinol-cytochrome c reductase. Cell 47, 939-951.
-
(1986)
Cell
, vol.47
, pp. 939-951
-
-
Hartl, F.U.1
Schmidt, B.2
Wachter, E.3
Weiss, H.4
Neupert, W.5
-
18
-
-
2342542370
-
Cell biology of cardiac mitochondrial phospholipids
-
Hatch, G. M. (2004). Cell biology of cardiac mitochondrial phospholipids. Biochem. Cell Biol. 82, 99-112.
-
(2004)
Biochem. Cell Biol.
, vol.82
, pp. 99-112
-
-
Hatch, G.M.1
-
19
-
-
23644456143
-
Biogenesis of cytochrome oxidase-sophisticated assembly lines in the mitochondrial inner membrane
-
Herrmann, J. M., and Funes, S. (2005). Biogenesis of cytochrome oxidase-sophisticated assembly lines in the mitochondrial inner membrane. Gene 354, 43-52.
-
(2005)
Gene
, vol.354
, pp. 43-52
-
-
Herrmann, J.M.1
Funes, S.2
-
20
-
-
0026603840
-
Cardiolipins and biomembrane function
-
Hoch, F. L. (1992). Cardiolipins and biomembrane function. Biochim. Biophys. Acta 1113, 71-133.
-
(1992)
Biochim. Biophys. Acta
, vol.1113
, pp. 71-133
-
-
Hoch, F.L.1
-
21
-
-
1842478040
-
The Tim8-Tim13 complex in Neurospora crassa functions in the assembly of proteins into both mitochondrial membranes
-
Hoppins, S. C., and Nargang, F. E. (2004). The Tim8-Tim13 complex in Neurospora crassa functions in the assembly of proteins into both mitochondrial membranes. J. Biol. Chem. 279, 12396-12405.
-
(2004)
J. Biol. Chem.
, vol.279
, pp. 12396-12405
-
-
Hoppins, S.C.1
Nargang, F.E.2
-
22
-
-
0015020471
-
Cardiolipin content of wild type and mutant yeasts in relation to mitochondrial function and development
-
Jakovcic, S., Getz, G. S., Rabinowitz, M., Jakob, H., and Swift, H. (1971). Cardiolipin content of wild type and mutant yeasts in relation to mitochondrial function and development. J. Cell Biol. 48, 490-502.
-
(1971)
J. Cell Biol.
, vol.48
, pp. 490-502
-
-
Jakovcic, S.1
Getz, G.S.2
Rabinowitz, M.3
Jakob, H.4
Swift, H.5
-
23
-
-
0037009105
-
Protein import into and across the mitochondrial inner membrane: Role of the TIM23 and TIM22 translocons
-
Jensen, R. E., and Dunn, C. D. (2002). Protein import into and across the mitochondrial inner membrane: role of the TIM23 and TIM22 translocons. Biochim. Biophys. Acta 1592, 25-34.
-
(2002)
Biochim. Biophys. Acta
, vol.1592
, pp. 25-34
-
-
Jensen, R.E.1
Dunn, C.D.2
-
24
-
-
0034698098
-
Absence of cardiolipin in the crd1 null mutant results in decreased mitochondrial membrane potential and reduced mitochondrial function
-
Jiang, F., Ryan, M. T., Schlame, M., Zhao, M., Gu, Z., Klingenberg, M., Pfanner, N., and Greenberg, M. L. (2000). Absence of cardiolipin in the crd1 null mutant results in decreased mitochondrial membrane potential and reduced mitochondrial function. J. Biol. Chem. 275, 22387-22394.
-
(2000)
J. Biol. Chem.
, vol.275
, pp. 22387-22394
-
-
Jiang, F.1
Ryan, M.T.2
Schlame, M.3
Zhao, M.4
Gu, Z.5
Klingenberg, M.6
Pfanner, N.7
Greenberg, M.L.8
-
25
-
-
0025951140
-
X-linked dilated cardiomyopathy with neutropenia, growth retardation, and 3-methylglutaconic aciduria
-
Kelley, R. I., Cheatham, J. P., Clark, B. J., Nigro, M. A., Powell, B. R., Sherwood, G. W., Sladky, J. T., and Swisher, W. P. (1991). X-linked dilated cardiomyopathy with neutropenia, growth retardation, and 3-methylglutaconic aciduria. J. Pediatr. 119, 738-747.
-
(1991)
J. Pediatr.
, vol.119
, pp. 738-747
-
-
Kelley, R.I.1
Cheatham, J.P.2
Clark, B.J.3
Nigro, M.A.4
Powell, B.R.5
Sherwood, G.W.6
Sladky, J.T.7
Swisher, W.P.8
-
26
-
-
0032775010
-
Epitope tagging of yeast genes using a PCR-based strategy: More tags and improved practical routines
-
Knop, M., Siegers, K., Pereira, G., Zachariae, W., Winsor, B., Nasmyth, K., and Schiebel, E. (1999). Epitope tagging of yeast genes using a PCR-based strategy: more tags and improved practical routines. Yeast 15, 963-972.
-
(1999)
Yeast
, vol.15
, pp. 963-972
-
-
Knop, M.1
Siegers, K.2
Pereira, G.3
Zachariae, W.4
Winsor, B.5
Nasmyth, K.6
Schiebel, E.7
-
27
-
-
7544219638
-
New developments in mitochondrial assembly
-
Koehler, C. M. (2004). New developments in mitochondrial assembly. Annu. Rev. Cell. Dev. Biol. 20, 309-335.
-
(2004)
Annu. Rev. Cell. Dev. Biol.
, vol.20
, pp. 309-335
-
-
Koehler, C.M.1
-
28
-
-
0037093493
-
Cardiolipin prevents rate-dependent uncoupling and provides osmotic stability in yeast mitochondria
-
Koshkin, V., and Greenberg, M. L. (2002). Cardiolipin prevents rate-dependent uncoupling and provides osmotic stability in yeast mitochondria. Biochem. J. 364, 317-322.
-
(2002)
Biochem. J.
, vol.364
, pp. 317-322
-
-
Koshkin, V.1
Greenberg, M.L.2
-
29
-
-
0348093762
-
An essential role of Sam50 in the protein sorting and assembly machinery of the mitochondrial outer membrane
-
Kozjak, V., Wiedemann, N., Milenkovic, D., Lohaus, C., Meyer, H. E., Guiard, B., Meisinger, C., and Pfanner, N. (2003). An essential role of Sam50 in the protein sorting and assembly machinery of the mitochondrial outer membrane. J. Biol. Chem. 278, 48520-48523.
-
(2003)
J. Biol. Chem.
, vol.278
, pp. 48520-48523
-
-
Kozjak, V.1
Wiedemann, N.2
Milenkovic, D.3
Lohaus, C.4
Meyer, H.E.5
Guiard, B.6
Meisinger, C.7
Pfanner, N.8
-
30
-
-
0035931764
-
Biogenesis of porin of the outer mitochondrial membrane involved an import pathway via receptors and the general import pore of the Tom complex
-
Krimmer, T. et al. (2001). Biogenesis of porin of the outer mitochondrial membrane involved an import pathway via receptors and the general import pore of the Tom complex. J. Cell Biol. 152, 289-300.
-
(2001)
J. Cell Biol.
, vol.152
, pp. 289-300
-
-
Krimmer, T.1
-
31
-
-
0032854652
-
Biogenesis of Tim proteins of the mitochondrial carrier import pathway: Differential targeting mechanisms and crossing over with the main import pathway
-
Kurz, M., Martin, H., Rassow, J., Pfanner, N., and Ryan, M. T. (1999). Biogenesis of Tim proteins of the mitochondrial carrier import pathway: differential targeting mechanisms and crossing over with the main import pathway. Mol. Biol. Cell 10, 2461-2474.
-
(1999)
Mol. Biol. Cell
, vol.10
, pp. 2461-2474
-
-
Kurz, M.1
Martin, H.2
Rassow, J.3
Pfanner, N.4
Ryan, M.T.5
-
32
-
-
0037022594
-
1 complex with its bound substrate cytochrome c
-
1 complex with its bound substrate cytochrome c. Proc. Natl. Acad. Sci. USA 99, 2800-2805.
-
(2002)
Proc. Natl. Acad. Sci. USA
, vol.99
, pp. 2800-2805
-
-
Lange, C.1
Hunte, C.2
-
33
-
-
7244224978
-
The human TAZ gene complements mitochondrial dysfunction in the yeast taz1Δ mutant
-
Ma, L., Vaz, F. M., Gu, Z., Wanders, R. J., and Greenberg, M. L. (2004). The human TAZ gene complements mitochondrial dysfunction in the yeast taz1Δ mutant. J. Biol. Chem. 279, 44394-44399.
-
(2004)
J. Biol. Chem.
, vol.279
, pp. 44394-44399
-
-
Ma, L.1
Vaz, F.M.2
Gu, Z.3
Wanders, R.J.4
Greenberg, M.L.5
-
34
-
-
0035066635
-
Multistep assembly of the protein import channel of the mitochondrial outer membrane
-
Model, K., Meisinger, C., Prinz, T., Wiedemann, N., Truscott, K. N., Pfanner, N., and Ryan, M. T. (2001). Multistep assembly of the protein import channel of the mitochondrial outer membrane. Nature Struct. Biol. 8, 361-370.
-
(2001)
Nature Struct. Biol.
, vol.8
, pp. 361-370
-
-
Model, K.1
Meisinger, C.2
Prinz, T.3
Wiedemann, N.4
Truscott, K.N.5
Pfanner, N.6
Ryan, M.T.7
-
35
-
-
0030969942
-
Protein import into mitochondria
-
Neupert, W. (1997). Protein import into mitochondria. Annu. Rev. Biochem. 66, 863-917.
-
(1997)
Annu. Rev. Biochem.
, vol.66
, pp. 863-917
-
-
Neupert, W.1
-
36
-
-
0031204998
-
Barth syndrome may be due to an acyltransferase deficiency
-
Neuwald, A. F. (1997). Barth syndrome may be due to an acyltransferase deficiency. Curr. Biol. 7, R465-R456.
-
(1997)
Curr. Biol.
, vol.7
-
-
Neuwald, A.F.1
-
37
-
-
7044274626
-
Lipids in membrane protein structures
-
Palsdottir, H., and Hunte, C. (2004). Lipids in membrane protein structures. Biochim. Biophys. Acta 1666, 2-18.
-
(2004)
Biochim. Biophys. Acta
, vol.1666
, pp. 2-18
-
-
Palsdottir, H.1
Hunte, C.2
-
38
-
-
0346727130
-
Evolutionary conservation of biogenesis of beta-barrel membrane proteins
-
Paschen, S. A., Waizenegger, T., Stan, T., Preuss, M., Cyrklaff, M., Hell, K., Rapaport, D., and Neupert, W. (2003). Evolutionary conservation of biogenesis of beta-barrel membrane proteins. Nature 426, 862-866.
-
(2003)
Nature
, vol.426
, pp. 862-866
-
-
Paschen, S.A.1
Waizenegger, T.2
Stan, T.3
Preuss, M.4
Cyrklaff, M.5
Hell, K.6
Rapaport, D.7
Neupert, W.8
-
39
-
-
7544235254
-
Assembling the mitochondrial outer membrane
-
Pfanner, N., Wiedemann, N., Meisinger, C., and Lithgow, T. (2004). Assembling the mitochondrial outer membrane. Nat. Struct. Mol. Biol. 11, 1044-1048.
-
(2004)
Nat. Struct. Mol. Biol.
, vol.11
, pp. 1044-1048
-
-
Pfanner, N.1
Wiedemann, N.2
Meisinger, C.3
Lithgow, T.4
-
40
-
-
0347362791
-
Cardiolipin stabilizes respiratory chain supercomplexes
-
Pfeiffer, K., Gohil, V., Stuart, R. A., Hunte, C., Brandt, U., Greenberg, M. L., and Schägger, H. (2003). Cardiolipin stabilizes respiratory chain supercomplexes. J. Biol. Chem. 278, 52873-52880.
-
(2003)
J. Biol. Chem.
, vol.278
, pp. 52873-52880
-
-
Pfeiffer, K.1
Gohil, V.2
Stuart, R.A.3
Hunte, C.4
Brandt, U.5
Greenberg, M.L.6
Schägger, H.7
-
41
-
-
3042778732
-
Mitochondrial import and the twin-pore translocase
-
Rehling, P., Brandner, K., and Pfanner, N. (2004). Mitochondrial import and the twin-pore translocase. Nat. Rev. Mol. Cell. Biol. 5, 519-530.
-
(2004)
Nat. Rev. Mol. Cell. Biol.
, vol.5
, pp. 519-530
-
-
Rehling, P.1
Brandner, K.2
Pfanner, N.3
-
42
-
-
0242669353
-
Protein insertion into the mitochondria inner membrane by a twin-pore translocase
-
Rehling, P., Model, K., Brandner, K., Kovermann, P., Sickmann, A., Meyer, H. E., W., K., Wagner, R., Truscott, K. N., and Pfanner, N. (2003). Protein insertion into the mitochondria inner membrane by a twin-pore translocase. Science 299, 1747-1751.
-
(2003)
Science
, vol.299
, pp. 1747-1751
-
-
Rehling, P.1
Model, K.2
Brandner, K.3
Kovermann, P.4
Sickmann, A.5
Meyer, H.E.6
Wagner, R.7
Truscott, K.N.8
Pfanner, N.9
-
43
-
-
0035229003
-
Assaying protein import into mitochondria
-
Ryan, M. T., Voos, W., and Pfanner, N. (2001). Assaying protein import into mitochondria. Methods Cell Biol. 65, 189-215.
-
(2001)
Methods Cell Biol.
, vol.65
, pp. 189-215
-
-
Ryan, M.T.1
Voos, W.2
Pfanner, N.3
-
44
-
-
0034193996
-
The biosynthesis and functional role of cardiolipin
-
Schlame, M., Rua, D., and Greenberg, M. L. (2000). The biosynthesis and functional role of cardiolipin. Prog. Lipid Res. 39, 257-288.
-
(2000)
Prog. Lipid Res.
, vol.39
, pp. 257-288
-
-
Schlame, M.1
Rua, D.2
Greenberg, M.L.3
-
45
-
-
4344630010
-
Significance of respirasomes for the assembly/stability of human respiratory chain complex I
-
Schägger, H., de Coo, R., Bauer, M. F., Hofmann, S., Godinot, C., and Brandt, U. (2004). Significance of respirasomes for the assembly/stability of human respiratory chain complex I. J. Biol. Chem. 279, 36349-36353.
-
(2004)
J. Biol. Chem.
, vol.279
, pp. 36349-36353
-
-
Schägger, H.1
De Coo, R.2
Bauer, M.F.3
Hofmann, S.4
Godinot, C.5
Brandt, U.6
-
46
-
-
0038230469
-
Supercomplexes in the respiratory chains of yeast and mammalian mitochondria
-
Schägger, H., and Pfeiffer, K. (2000). Supercomplexes in the respiratory chains of yeast and mammalian mitochondria. EMBO J. 19, 1777-1783.
-
(2000)
EMBO J.
, vol.19
, pp. 1777-1783
-
-
Schägger, H.1
Pfeiffer, K.2
-
47
-
-
0345687191
-
The proteome of Saccharomyces cerevisiae mitochondria
-
Sickmann, A. et al. (2003). The proteome of Saccharomyces cerevisiae mitochondria. Proc. Natl. Acad. Sci. USA 100, 13207-13212.
-
(2003)
Proc. Natl. Acad. Sci. USA
, vol.100
, pp. 13207-13212
-
-
Sickmann, A.1
-
48
-
-
0024669291
-
A system of shuttle vectors and yeast host strains designed for efficient manipulation of DNA in Saccharomyces cerevisiae
-
Sikorski, R. S., and Hieter, P. (1989). A system of shuttle vectors and yeast host strains designed for efficient manipulation of DNA in Saccharomyces cerevisiae. Genetics 122, 19-27.
-
(1989)
Genetics
, vol.122
, pp. 19-27
-
-
Sikorski, R.S.1
Hieter, P.2
-
49
-
-
0016188814
-
Studies on the mechanism by which cyanine dyes measure membrane potential in red blood cells and phosphatidylcholine vesicles
-
Sims, P. J., Waggoner, A. S., Wang, C. H., and Hoffman, J. F. (1974). Studies on the mechanism by which cyanine dyes measure membrane potential in red blood cells and phosphatidylcholine vesicles. Biochemistry 13, 3315-3330.
-
(1974)
Biochemistry
, vol.13
, pp. 3315-3330
-
-
Sims, P.J.1
Waggoner, A.S.2
Wang, C.H.3
Hoffman, J.F.4
-
50
-
-
0034866945
-
Assembly of cytochrome c oxidase: What can we learn from patients with cytochrome c oxidase deficiency?
-
Taanman, J. W., and Williams, S. L. (2001). Assembly of cytochrome c oxidase: what can we learn from patients with cytochrome c oxidase deficiency? Biochem. Soc. Trans. 29, 446-451.
-
(2001)
Biochem. Soc. Trans.
, vol.29
, pp. 446-451
-
-
Taanman, J.W.1
Williams, S.L.2
-
51
-
-
0027209265
-
Subunit VIa of yeast cytochrome c oxidase is not necessary for assembly of the enzyme complex but modulates the enzyme activity
-
Taanman, J. W., and Capaldi, R. A. (1993). Subunit VIa of yeast cytochrome c oxidase is not necessary for assembly of the enzyme complex but modulates the enzyme activity. J. Biol. Chem. 268, 18754-18761.
-
(1993)
J. Biol. Chem.
, vol.268
, pp. 18754-18761
-
-
Taanman, J.W.1
Capaldi, R.A.2
-
52
-
-
18844391214
-
Ypr140wp, "the yeast tafazzin," displays a mitochondrial lyso-PC acyltransferase activity related to triglyceride and mitochondrial lipid synthesis
-
Testet, E., Laroche-Traineau, J., Noubhani, A., Coulon, D., Bunoust, O., Camougrand, N., Manon, S., Lessire, R., and Bessoule, J. J. (2004). Ypr140wp, "the yeast tafazzin," displays a mitochondrial lyso-PC acyltransferase activity related to triglyceride and mitochondrial lipid synthesis. Biochem. J. 387, 617-626.
-
(2004)
Biochem. J.
, vol.387
, pp. 617-626
-
-
Testet, E.1
Laroche-Traineau, J.2
Noubhani, A.3
Coulon, D.4
Bunoust, O.5
Camougrand, N.6
Manon, S.7
Lessire, R.8
Bessoule, J.J.9
-
53
-
-
10744228445
-
A J-protein is an essential subunit of the presequence translocase-associated protein import motor of mitochondria
-
Truscott, K. N. et al. (2003). A J-protein is an essential subunit of the presequence translocase-associated protein import motor of mitochondria. J. Cell Biol. 163, 707-713.
-
(2003)
J. Cell Biol.
, vol.163
, pp. 707-713
-
-
Truscott, K.N.1
-
54
-
-
0036840342
-
Mitochondrial import of the ADP/ATP carrier: The essential TIM complex of the intermembrane space is required for precursor release from the TOM complex
-
Truscott, K. N., Wiedemann, N., Rehling, P., Müller, H., Meisinger, C., Pfanner, N., and Guiard, B. (2002). Mitochondrial import of the ADP/ATP carrier: the essential TIM complex of the intermembrane space is required for precursor release from the TOM complex. Mol. Cell. Biol. 22, 7780-7789.
-
(2002)
Mol. Cell. Biol.
, vol.22
, pp. 7780-7789
-
-
Truscott, K.N.1
Wiedemann, N.2
Rehling, P.3
Müller, H.4
Meisinger, C.5
Pfanner, N.6
Guiard, B.7
-
55
-
-
0242322008
-
Only one splice variant of the human TAZ gene encodes a functional protein with a role in cardiolipin metabolism
-
Vaz, F. M., Houtkooper, R. H., Valianpour, F., Barth, P. G., and Wanders, R. J. (2003). Only one splice variant of the human TAZ gene encodes a functional protein with a role in cardiolipin metabolism. J. Biol. Chem. 278, 43089-43094.
-
(2003)
J. Biol. Chem.
, vol.278
, pp. 43089-43094
-
-
Vaz, F.M.1
Houtkooper, R.H.2
Valianpour, F.3
Barth, P.G.4
Wanders, R.J.5
-
56
-
-
0034694802
-
Defective remodeling of cardiolipin and phosphatidylglycerol in Barth syndrome
-
Vreken, P., Valianpour, F., Nijtmans, L. G., Grivell, L. A., Plecko, B., Wanders, R. J., and Barth, P. G. (2000). Defective remodeling of cardiolipin and phosphatidylglycerol in Barth syndrome. Biochem. Biophys. Res. Commun. 279, 378-382.
-
(2000)
Biochem. Biophys. Res. Commun.
, vol.279
, pp. 378-382
-
-
Vreken, P.1
Valianpour, F.2
Nijtmans, L.G.3
Grivell, L.A.4
Plecko, B.5
Wanders, R.J.6
Barth, P.G.7
-
57
-
-
0042163218
-
Machinery for protein sorting and assembly in the mitochondrial outer membrane
-
Wiedemann, N., Kozjak, V., Chacinska, A., Schönfisch, B., Rospert, S., Ryan, M. T., Pfanner, N., and Meisinger, C. (2003). Machinery for protein sorting and assembly in the mitochondrial outer membrane. Nature 424, 565-571.
-
(2003)
Nature
, vol.424
, pp. 565-571
-
-
Wiedemann, N.1
Kozjak, V.2
Chacinska, A.3
Schönfisch, B.4
Rospert, S.5
Ryan, M.T.6
Pfanner, N.7
Meisinger, C.8
-
58
-
-
2442421175
-
Biogenesis of the protein import channel Tom40 of the mitochondrial outer membrane: Intermembrane space components are involved in an early stage of the assembly pathway
-
Wiedemann, N., Truscott, K. N., Pfannschmidt, S., Guiard, B., Meisinger, C., and Pfanner, N. (2004). Biogenesis of the protein import channel Tom40 of the mitochondrial outer membrane: intermembrane space components are involved in an early stage of the assembly pathway. J. Biol. Chem. 279, 18188-18194.
-
(2004)
J. Biol. Chem.
, vol.279
, pp. 18188-18194
-
-
Wiedemann, N.1
Truscott, K.N.2
Pfannschmidt, S.3
Guiard, B.4
Meisinger, C.5
Pfanner, N.6
-
59
-
-
0345803935
-
Remodeling of cardiolipin by phospholipid transacylation
-
Xu, Y., Kelley, R. I., Blanck, T. J., and Schlame, M. (2003). Remodeling of cardiolipin by phospholipid transacylation. J. Biol. Chem. 278, 51380-51385.
-
(2003)
J. Biol. Chem.
, vol.278
, pp. 51380-51385
-
-
Xu, Y.1
Kelley, R.I.2
Blanck, T.J.3
Schlame, M.4
-
60
-
-
0037113864
-
Gluing the respiratory chain together
-
Zhang, M., Mileykovskaya, E., and Dowhan, W. (2002). Gluing the respiratory chain together. J. Biol. Chem. 277, 43553-43556.
-
(2002)
J. Biol. Chem.
, vol.277
, pp. 43553-43556
-
-
Zhang, M.1
Mileykovskaya, E.2
Dowhan, W.3
-
61
-
-
23844540312
-
Cardiolipin is essential for organization of complexes III and IV into a supercomplex in intact yeast mitochondria
-
Zhang, M., Mileykovskaya, E., and Dowhan, W. (2005). Cardiolipin is essential for organization of complexes III and IV into a supercomplex in intact yeast mitochondria. J. Biol. Chem. 280, 29403-29408.
-
(2005)
J. Biol. Chem.
, vol.280
, pp. 29403-29408
-
-
Zhang, M.1
Mileykovskaya, E.2
Dowhan, W.3
|