Mitochondrial Respiratory Chain Supercomplexes Are Destabilized in Barth Syndrome Patients

Journal of Molecular Biology

Volumn 361, Issue 3, 2006, Pages 462-469

  McKenzie, Matthew ^a   Lazarou, Michael ^a   Thorburn, David R ^b,c   Ryan, Michael T ^a  

^a LA TROBE UNIVERSITY   (Australia)

^b ROYAL CHILDREN'S HOSPITAL   (Australia)

^c UNIVERSITY OF MELBOURNE   (Australia)

Author keywords

blue native PAGE; cardiolipin; membrane protein; mitochondria; supercomplex

Indexed keywords

ACYLTRANSFERASE; CARDIOLIPIN; DIGITONIN; TAFAZZIN; UNCLASSIFIED DRUG;

ARTICLE; BARTH SYNDROME; CONTROLLED STUDY; DISSOCIATION; EXTRACTION; GENE DISRUPTION; HUMAN; HUMAN CELL; LYMPHOBLAST; MITOCHONDRIAL MEMBRANE; MITOCHONDRIAL RESPIRATION; MOLECULAR INTERACTION; POLYACRYLAMIDE GEL ELECTROPHORESIS; PRIORITY JOURNAL; YEAST;

EID: 33746327466     PISSN: 00222836     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jmb.2006.06.057     Document Type: Article

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