Respiratory chain supercomplexes set the threshold for respiration defects in human mtDNA mutant cybrids

Human Molecular Genetics

Volumn 15, Issue 13, 2006, Pages 2157-2169

  D'Aurelio, Marilena ^a   Gajewski, Carl D ^a   Lenaz, Giorgio ^b   Manfredi, Giovanni ^a  

^a WEILL CORNELL MEDICAL COLLEGE   (United States)

^b UNIVERSITY OF BOLOGNA   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

CYTOCHROME C OXIDASE; MITOCHONDRIAL DNA; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE; UBIQUINOL CYTOCHROME C REDUCTASE;

ARTICLE; CELL FUSION; CELL MUTANT; COMPLEX FORMATION; CONTROLLED STUDY; CORRELATION FUNCTION; GEL ELECTROPHORESIS; GENE MUTATION; GENETIC COMPLEMENTATION; HUMAN; HUMAN CELL; HYBRID CELL; MITOCHONDRIAL RESPIRATION; PRIORITY JOURNAL; RESPIRATORY CHAIN;

CELL LINE; CELL RESPIRATION; CODON, NONSENSE; CYCLOOXYGENASE 1; CYTOCHROMES B; DNA, MITOCHONDRIAL; ELECTRON TRANSPORT CHAIN COMPLEX PROTEINS; FRAMESHIFT MUTATION; HUMANS; HYBRID CELLS; MEMBRANE PROTEINS; MODELS, BIOLOGICAL; MUTATION;

EID: 33745242989     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddl141     Document Type: Article

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