Dynactin deficiency in the CNS of humans with sporadic ALS and mice with genetically determined motor neuron degeneration

Neurochemical Research

Volumn 38, Issue 12, 2013, Pages 2463-2473

  Kuåma Kozakiewicz, Magdalena ^a   Chudy, Agnieszka ^a   Kaåmierczak, Beata ^a   Dziewulska, Dorota ^a,b   Usarek, Ewa ^a   Barańczyk Kuåma, Anna ^a  

^a MEDICAL UNIVERSITY OF WARSAW   (Poland)

^b MOSSAKOWSKI MEDICAL RESEARCH CENTRE   (Poland)

Author keywords

Amyotrophic lateral sclerosis; Dynactin; Dync1h1 mutation; hSOD1G93A mutation; Motor neuron degeneration; Retrograde axonal transport; Transgenic mice

Indexed keywords

DCTN1 PROTEIN; DCTN3 PROTEIN; DYNACTIN; MESSENGER RNA; UNCLASSIFIED DRUG;

ADULT; AGED; AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUTOPSY; AXONAL RETROGRADE TRANSPORT; CENTRAL NERVOUS SYSTEM; CLINICAL ARTICLE; CONTROLLED STUDY; DCTN1 GENE; DCTN3 GENE; FEMALE; FRONTAL CORTEX; GENE EXPRESSION; GENE MUTATION; HEAVY CHAIN; HIPPOCAMPUS; HUMAN; HUMAN TISSUE; LIGHT CHAIN; MALE; MIDDLE AGED; MOTONEURON; MOTOR CORTEX; MOUSE; NERVE CELL; NERVE DEGENERATION; NONHUMAN; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROTEIN SUBUNIT; SENSORY CORTEX; SPINAL CORD; VERY ELDERLY;

EID: 84890259049     PISSN: 03643190     EISSN: 15736903     Source Type: Journal    
DOI: 10.1007/s11064-013-1160-7     Document Type: Article

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