Mice with a mutation in the dynein heavy chain 1 gene display sensory neuropathy but lack motor neuron disease

Experimental Neurology

Volumn 215, Issue 1, 2009, Pages 146-152

  Dupuis, Luc ^a,b   Fergani, Anissa ^a,b   Braunstein, Kerstin E ^c   Eschbach, Judith ^a,b   Holl, Nathalie ^a,b   Rene, Frédérique ^a,b   Gonzalez De Aguilar, Jose Luis ^a,b   Zoerner, Björn ^d   Schwalenstocker, Birgit ^c   Ludolph, Albert C ^c   Loeffler, Jean Philippe ^a,b  

^a INSERM   (France)

^b UNIVERSITÉ DE STRASBOURG   (France)

^c UNIVERSITY OF ULM   (Germany)

^d UNIVERSITY OF ZURICH   (Switzerland)

Author keywords

Amyotrophic lateral sclerosis; Axonal transport; Dynein; Motor neuron

Indexed keywords

DYNEIN ADENOSINE TRIPHOSPHATASE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; EXPERIMENTAL MODEL; GENE MUTATION; HEAVY CHAIN; HETEROZYGOTE; MISSENSE MUTATION; MOTOR NEURON DISEASE; MOUSE; MOUSE STRAIN; MUSCLE DENERVATION; MUSCLE SPINDLE; NERVE CELL DEGENERATION; NERVE FIBER DEGENERATION; NONHUMAN; PHENOTYPE; POINT MUTATION; PRIORITY JOURNAL; PROTEIN FUNCTION; RETROGRADE NERVE FIBER TRANSPORT; SENSORY NERVE CELL; SENSORY NEUROPATHY;

AGE FACTORS; ANALYSIS OF VARIANCE; ANIMALS; BENZOFURANS; CHOLINE O-ACETYLTRANSFERASE; DISEASE MODELS, ANIMAL; DYNEIN ATPASE; ELECTROMYOGRAPHY; MICE; MICE, INBRED C3H; MICE, MUTANT STRAINS; MOTOR NEURON DISEASE; MOTOR NEURONS; MUSCLE DENERVATION; MUSCLE, SKELETAL; MUTATION; NEUROMUSCULAR JUNCTION; SENSATION DISORDERS; SPINAL NERVE ROOTS; SUPEROXIDE DISMUTASE;

EID: 57649107154     PISSN: 00144886     EISSN: 10902430     Source Type: Journal    
DOI: 10.1016/j.expneurol.2008.09.019     Document Type: Article

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