-
1
-
-
73249123043
-
Persistence of essential fatty acid deficiency in cystic fi-brosis despite nutritional therapy
-
Aldámiz-Echevarría L, Prieto JA, Andrade F, Elorz J, Sojo A, Lage S, Sanjurjo P, Vázquez C, Rodríguez-Soriano J. 2009. Persistence of essential fatty acid deficiency in cystic fi-brosis despite nutritional therapy. Pediatr Res 66: 585-589.
-
(2009)
Pediatr Res
, vol.66
, pp. 585-589
-
-
Aldámiz-Echevarría, L.1
Prieto, J.A.2
Andrade, F.3
Elorz, J.4
Sojo, A.5
Lage, S.6
Sanjurjo, P.7
Vázquez, C.8
Rodríguez-Soriano, J.9
-
2
-
-
0029010510
-
Lower respiratory infection and inflammation in infants with newly diagnosed cystic fi-brosis
-
Armstrong DS, Grimwood K, Carzino R, Carlin JB, Olin-sky A, Phelan PD. 1995. Lower respiratory infection and inflammation in infants with newly diagnosed cystic fi-brosis. BMJ 310: 1571-1572.
-
(1995)
BMJ
, vol.310
, pp. 1571-1572
-
-
Armstrong, D.S.1
Grimwood, K.2
Carzino, R.3
Carlin, J.B.4
Olin-Sky, A.5
Phelan, P.D.6
-
3
-
-
0030768159
-
Lower airway inflammation in infants and young children with cystic fibrosis
-
Armstrong DS, Grimwood K, Carlin JB, Armstrong DS, Grimwood K, Carlin JB, Carzino R, Gutièrrez JP, Hull J, Olinsky A, et al. 1997. Lower airway inflammation in infants and young children with cystic fibrosis. Am J Respir Crit Care Med 156: 1197-1204.
-
(1997)
Am J Respir Crit Care Med
, vol.156
, pp. 1197-1204
-
-
Armstrong, D.S.1
Grimwood, K.2
Carlin, J.B.3
Armstrong, D.S.4
Grimwood, K.5
Carlin, J.B.6
Carzino, R.7
Gutièrrez, J.P.8
Hull, J.9
Olinsky, A.10
-
4
-
-
0021970474
-
Alternate-day prednisone reduces morbidity and improves pulmonary function in cystic fibrosis
-
Auerbach HS, Williams M, Kirkpatrick JA, Colten HR. 1985. Alternate-day prednisone reduces morbidity and improves pulmonary function in cystic fibrosis. Lancet 2: 686-688.
-
(1985)
Lancet
, vol.2
, pp. 686-688
-
-
Auerbach, H.S.1
Williams, M.2
Kirkpatrick, J.A.3
Colten, H.R.4
-
6
-
-
33745130682
-
Multicenter randomized controlled trial of withdrawal of inhaled cor-ticosteroids in cystic fibrosis
-
CF WISE (Withdrawal of Inhaled Steroids Evaluation) Investigators
-
Balfour-Lynn IM, Lees B, Hall P, Phillips G, Khan M, Fla-ther M, Elborn JS, CF WISE (Withdrawal of Inhaled Steroids Evaluation) Investigators. 2006. Multicenter randomized controlled trial of withdrawal of inhaled cor-ticosteroids in cystic fibrosis. Am J Respir Crit Care Med 173: 1356-1362.
-
(2006)
Am J Respir Crit Care Med
, vol.173
, pp. 1356-1362
-
-
Balfour-Lynn, I.M.1
Lees, B.2
Hall, P.3
Phillips, G.4
Khan, M.5
Fla-Ther, M.6
Elborn, J.S.7
-
7
-
-
0037406477
-
Low-dose methotrexate for advanced pulmonarydiseasein patients with cystic fibrosis
-
Ballmann M, Junge S, von der Hardt H. 2003. Low-dose methotrexate for advanced pulmonarydiseasein patients with cystic fibrosis. Respir Med 97: 498-500.
-
(2003)
Respir Med
, vol.97
, pp. 498-500
-
-
Ballmann, M.1
Junge, S.2
von der Hardt, H.3
-
8
-
-
0029346937
-
The relationship between infection and inflammation in the early stages of lung disease from cystic fibrosis
-
Balough K, McCubbin M, Weinberger M, Smits W, Ahrens R, Fick R. 1995. The relationship between infection and inflammation in the early stages of lung disease from cystic fibrosis. Pediatr Pulmonol 20: 63-70.
-
(1995)
Pediatr Pulmonol
, vol.20
, pp. 63-70
-
-
Balough, K.1
McCubbin, M.2
Weinberger, M.3
Smits, W.4
Ahrens, R.5
Fick, R.6
-
9
-
-
33947301605
-
Long-term docosahexaenoic acid therapy in a con- genic murine model of cystic fibrosis
-
Beharry S, Ackerley C, Corey M, Kent G, Heng YM, Chris-tensen H, Luk C, Yantiss RK, Nasser IA, Zaman M, et al. 2007. Long-term docosahexaenoic acid therapy in a con- genic murine model of cystic fibrosis. Am J Physiol Gastrointest Liver Physiol 292: G839-G848.
-
(2007)
Am J Physiol Gastrointest Liver Physiol
, vol.292
-
-
Beharry, S.1
Ackerley, C.2
Corey, M.3
Kent, G.4
Heng, Y.M.5
Chris-Tensen, H.6
Luk, C.7
Yantiss, R.K.8
Nasser, I.A.9
Zaman, M.10
-
11
-
-
0035168113
-
Use of cyclosporin A as a steroid sparing agent in cystic fibrosis
-
Bhal GK, Maguire SA, Bowler IM. 2001. Use of cyclosporin A as a steroid sparing agent in cystic fibrosis. Arch Dis Child 84: 89.
-
(2001)
Arch Dis Child
, vol.84
, pp. 89
-
-
Bhal, G.K.1
Maguire, S.A.2
Bowler, I.M.3
-
12
-
-
13644282540
-
Phase II trial to assess the clinical efficacy of transgenic a-1-antitrypsin (tg-hAAT) as an effective treatment of cystic fibrosis
-
Bilton D, Elborn S, Conway S, Edgar J, Redmond A. 1999. Phase II trial to assess the clinical efficacy of transgenic a-1-antitrypsin (tg-hAAT) as an effective treatment of cystic fibrosis. Pediatr Pulmonol 28 (Suppl 19): 246.
-
(1999)
Pediatr Pulmonol
, vol.28
, Issue.SUPPL. 19
, pp. 246
-
-
Bilton, D.1
Elborn, S.2
Conway, S.3
Edgar, J.4
Redmond, A.5
-
13
-
-
0028240276
-
Pro-tease-antiprotease imbalance in the lungs of children with cystic fibrosis
-
Birrer P, McElvaney NG, Rüdeberg A, Sommer CW, Liechti-Gallati S, Kraemer R, Hubbard R, Crystal RG. 1994. Pro-tease-antiprotease imbalance in the lungs of children with cystic fibrosis. Am J Respir Crit Care Med 150: 207-213.
-
(1994)
Am J Respir Crit Care Med
, vol.150
, pp. 207-213
-
-
Birrer, P.1
McElvaney, N.G.2
Rüdeberg, A.3
Sommer, C.W.4
Liechti-Gallati, S.5
Kraemer, R.6
Hubbard, R.7
Crystal, R.G.8
-
14
-
-
13844322148
-
A pilot study of the effects of inhaled buffered reduced glutathi-one on the clinical status of patients with cystic fibrosis
-
Bishop C, Hudson VM, Hilton SC, Wilde C. 2005. A pilot study of the effects of inhaled buffered reduced glutathi-one on the clinical status of patients with cystic fibrosis. Chest 127: 308-317.
-
(2005)
Chest
, vol.127
, pp. 308-317
-
-
Bishop, C.1
Hudson, V.M.2
Hilton, S.C.3
Wilde, C.4
-
15
-
-
0028784322
-
Inflammatory cy-tokines in cystic fibrosis lungs
-
Bonfield TL, Panuska JR, Konstan MW, Hilliard KA, Hil-liard JB, Ghnaim H, Berger M. 1995a. Inflammatory cy-tokines in cystic fibrosis lungs. Am J Respir Crit Care Med 152: 2111-2118.
-
(1995)
Am J Respir Crit Care Med
, vol.152
, pp. 2111-2118
-
-
Bonfield, T.L.1
Panuska, J.R.2
Konstan, M.W.3
Hilliard, K.A.4
Hil-Liard, J.B.5
Ghnaim, H.6
Berger, M.7
-
16
-
-
0029372481
-
Normal bronchial epithelial cells constitutively produce the anti-inflammatory cytokine interleukin-10, which is downregulated in cystic fibrosis
-
Bonfield TL, Konstan MW, Burfeind P, Panuska JR, Hilli-ard JB, Berger M. 1995b. Normal bronchial epithelial cells constitutively produce the anti-inflammatory cytokine interleukin-10, which is downregulated in cystic fibrosis. Am J Respir Cell Mol Biol 13: 257-261.
-
(1995)
Am J Respir Cell Mol Biol
, vol.13
, pp. 257-261
-
-
Bonfield, T.L.1
Konstan, M.W.2
Burfeind, P.3
Panuska, J.R.4
Hilli-Ard, J.B.5
Berger, M.6
-
17
-
-
0032817772
-
Altered respiratory epithelial cell cytokine production in cystic fibrosis
-
Bonfield TL, Konstan MW, Berger M. 1999. Altered respiratory epithelial cell cytokine production in cystic fibrosis. J Allergy Clin Immunol 104: 72-78.
-
(1999)
J Allergy Clin Immunol
, vol.104
, pp. 72-78
-
-
Bonfield, T.L.1
Konstan, M.W.2
Berger, M.3
-
18
-
-
54449093079
-
2 and inflammatory cytokine produc tion
-
Chen J, Kinter M, Shank S, Cotton C, Kelley TJ, Ziady AG. 2008. Dysfunction of Nrf-2 in CFepithelia leads to excess intracellular H2O2 and inflammatory cytokine produc tion. PLoS ONE 3: e3367.
-
(2008)
PLoS ONE
, vol.3
-
-
Chen, J.1
Kinter, M.2
Shank, S.3
Cotton, C.4
Kelley, T.J.5
Ziady, A.G.6
-
19
-
-
1542267080
-
State of the art: Why do the lungs of patients with cystic fibrosis become infected and why can't they clear the infection?
-
Chmiel JF, Davis PB. 2003. State of the art: Why do the lungs of patients with cystic fibrosis become infected and why can't they clear the infection? Respir Res 4: 8-21.
-
(2003)
Respir Res
, vol.4
, pp. 8-21
-
-
Chmiel, J.F.1
Davis, P.B.2
-
20
-
-
0033456217
-
IL-10 attenuates excessive inflammation in chronic Pseudomonas infection in mice
-
Chmiel JF, Konstan MW, Knesebeck JE, Hilliard JB, Bon-field TL, Dawson DV, Berger M. 1999. IL-10 attenuates excessive inflammation in chronic Pseudomonas infection in mice. Am J Respir Crit Care Med 160: 2040-2047.
-
(1999)
Am J Respir Crit Care Med
, vol.160
, pp. 2040-2047
-
-
Chmiel, J.F.1
Konstan, M.W.2
Knesebeck, J.E.3
Hilliard, J.B.4
Bon-Field, T.L.5
Dawson, D.V.6
Berger, M.7
-
22
-
-
0037090469
-
Prolonged inflammatory response to acute Pseudomonas challenge in interleukin-10 knockout mice
-
Chmiel JF, Konstan MW, Saadane A, Krenicky JE, Lester Kirchner H, Berger M. 2002b. Prolonged inflammatory response to acute Pseudomonas challenge in interleukin-10 knockout mice. Am J Respir Crit Care Med 165: 1176-1181.
-
(2002)
Am J Respir Crit Care Med
, vol.165
, pp. 1176-1181
-
-
Chmiel, J.F.1
Konstan, M.W.2
Saadane, A.3
Krenicky, J.E.4
Lester Kirchner, H.5
Berger, M.6
-
23
-
-
54049139978
-
Persistent methicillin-resistant Staphylococcus aureus and rate of FEV1 decline in cystic fibrosis
-
Dasenbrook EC, Merlo CA, Diener-West M, Lechtzin N, Boyle MP. 2008. Persistent methicillin-resistant Staphylococcus aureus and rate of FEV1 decline in cystic fibrosis. Am J Respir Crit Care Med 178: 814-821.
-
(2008)
Am J Respir Crit Care Med
, vol.178
, pp. 814-821
-
-
Dasenbrook, E.C.1
Merlo, C.A.2
Diener-West, M.3
Lechtzin, N.4
Boyle, M.P.5
-
24
-
-
77953635880
-
Association between respiratory tract methicillin-resistant Staphylococcus aureus and survival in cystic fibrosis
-
Dasenbrook EC, Checkley W, Merlo CA, Konstan MW, Lechtzin N, Boyle MP. 2010. Association between respiratory tract methicillin-resistant Staphylococcus aureus and survival in cystic fibrosis. JAMA 303: 2386-2392.
-
(2010)
JAMA
, vol.303
, pp. 2386-2392
-
-
Dasenbrook, E.C.1
Checkley, W.2
Merlo, C.A.3
Konstan, M.W.4
Lechtzin, N.5
Boyle, M.P.6
-
26
-
-
62949129940
-
Inhibition of proinflammatory cytokine production by PPARg agonists in airway epithelial cells
-
Davis PB, Gupta S, Eastman J, Konstan MW. 2003. Inhibition of proinflammatory cytokine production by PPARg agonists in airway epithelial cells. Pediatr Pulmonol 36 (Suppl 25): 268-269.
-
(2003)
Pediatr Pulmonol
, vol.36
, Issue.SUPPL. 25
, pp. 268-269
-
-
Davis, P.B.1
Gupta, S.2
Eastman, J.3
Konstan, M.W.4
-
27
-
-
79955667134
-
Inhaled corticoste-roids and lower lung function decline in young children with cystic fibrosis
-
Members of the Belgian CF Registry
-
De Boeck K, Vermeulen F, Wanyama S, Thomas M, Members of the Belgian CF Registry. 2011. Inhaled corticoste-roids and lower lung function decline in young children with cystic fibrosis. Eur Respir J 37: 1091-1095.
-
(2011)
Eur Respir J
, vol.37
, pp. 1091-1095
-
-
de Boeck, K.1
Vermeulen, F.2
Wanyama, S.3
Thomas, M.4
-
28
-
-
84869120178
-
Treatment of lung infection in patients with cystic fibrosis: Current and future strategies
-
Consensus Study Group
-
Döring G, Flume P, Heijerman H, Elborn JS, Consensus Study Group. 2012. Treatment of lung infection in patients with cystic fibrosis: Current and future strategies. J Cyst Fibros 2012 11: 461-479.
-
(2012)
J Cyst Fibros
, vol.2012
, Issue.11
, pp. 461-479
-
-
Döring, G.1
Flume, P.2
Heijerman, H.3
Elborn, J.S.4
-
29
-
-
33847043963
-
IL-23 mediates inflammatory responses to mucoid Pseudomonas aeruginosa lung infection in mice
-
Dubin PJ, Kolls JK. 2007. IL-23 mediates inflammatory responses to mucoid Pseudomonas aeruginosa lung infection in mice. Am J Physiol Lung Cell Mol Physiol 292: L519-L528.
-
(2007)
Am J Physiol Lung Cell Mol Physiol
, vol.292
-
-
Dubin, P.J.1
Kolls, J.K.2
-
31
-
-
0030814892
-
Mevalonate-de-pendent inhibition of transendothelial migration and chemotaxis of human peripheral blood neutrophils by pravastatin
-
Dunzendorfer S, Rothbucher D, Schratzberger P, Reinisch N, Kahler CM, Wiedermann CJ. 1997. Mevalonate-de-pendent inhibition of transendothelial migration and chemotaxis of human peripheral blood neutrophils by pravastatin. Circ Res 81: 963-969.
-
(1997)
Circ Res
, vol.81
, pp. 963-969
-
-
Dunzendorfer, S.1
Rothbucher, D.2
Schratzberger, P.3
Reinisch, N.4
Kahler, C.M.5
Wiedermann, C.J.6
-
32
-
-
0028969594
-
A multicenter study of alternate-day prednisone therapy in patientswith cysticfibrosis
-
Cystic Fibrosis Foundation Prednisone Trial Group
-
Eigen H, Rosenstein BJ, FitzSimmons S, Schidlow DV. 1995. A multicenter study of alternate-day prednisone therapy in patientswith cysticfibrosis. Cystic Fibrosis Foundation Prednisone Trial Group. J Pediatr 126: 515-523.
-
(1995)
J Pediatr
, vol.126
, pp. 515-523
-
-
Eigen, H.1
Rosenstein, B.J.2
Fitzsimmons, S.3
Schidlow, D.V.4
-
33
-
-
0037442137
-
IL-17, produced by lymphocytes and neutrophils, is necessary for lipopolysaccharide-induced airway neu-trophilia: IL-15 as a possible trigger
-
Ferretti S, Bonneau O, Dubois GR, Jones CE, Trifilieff A. 2003. IL-17, produced by lymphocytes and neutrophils, is necessary for lipopolysaccharide-induced airway neu-trophilia: IL-15 as a possible trigger. J Immunol 170: 2106-2112.
-
(2003)
J Immunol
, vol.170
, pp. 2106-2112
-
-
Ferretti, S.1
Bonneau, O.2
Dubois, G.R.3
Jones, C.E.4
Trifilieff, A.5
-
34
-
-
36248953255
-
Cystic fibrosis pulmonary guidelines
-
Flume PA, O'Sullivan BP, Robinson KA, Goss CH, Mogay-zel PJ Jr, Willey-Courand DB, Bujan J, Finder J, Lester M, Quittell L, et al. 2007. Cystic fibrosis pulmonary guidelines. Am J Respir Crit Care Med 176: 957-969.
-
(2007)
Am J Respir Crit Care Med
, vol.176
, pp. 957-969
-
-
Flume, P.A.1
O'Sullivan, B.P.2
Robinson, K.A.3
Goss, C.H.4
Mogay-Zel Jr., P.J.5
Willey-Courand, D.B.6
Bujan, J.7
Finder, J.8
Lester, M.9
Quittell, L.10
-
36
-
-
0036085182
-
2/2 mice and the effect of docosahexaenoic acid
-
2/2 mice and the effect of docosahexaenoic acid. J Appl Physiol 92: 2169-2176.
-
(2002)
J Appl Physiol
, vol.92
, pp. 2169-2176
-
-
Freedman, S.D.1
Weinstein, D.2
Blanco, P.G.3
Martinez-Clark, P.4
Urman, S.5
Zaman, M.6
Morrow, J.D.7
Alvarez, J.G.8
-
37
-
-
0030961127
-
Decreased concentration of exhaled nitric oxide (NO) in patients with cystic fibrosis
-
Grasemann H, Michler E, Wallot M, Ratjen F. 1997. Decreased concentration of exhaled nitric oxide (NO) in patients with cystic fibrosis. Pediatr Pulmonol 24: 173-177.
-
(1997)
Pediatr Pulmonol
, vol.24
, pp. 173-177
-
-
Grasemann, H.1
Michler, E.2
Wallot, M.3
Ratjen, F.4
-
38
-
-
30444439420
-
Increased arginase activity in cystic fibrosis airways
-
Grasemann H, Schwiertz R, Matthiesen S, Racke K, Ratjen F. 2005a. Increased arginase activity in cystic fibrosis airways. Am J Respir Crit Care Med 172: 1523-1528.
-
(2005)
Am J Respir Crit Care Med
, vol.172
, pp. 1523-1528
-
-
Grasemann, H.1
Schwiertz, R.2
Matthiesen, S.3
Racke, K.4
Ratjen, F.5
-
39
-
-
13444292529
-
Oral L-arginine supplementation in cystic fibrosis patients: A placebo-controlled study
-
Grasemann H, Grasemann C, Kurtz F, Tietze-Schillings G, Vester U, Ratjen F. 2005b. Oral L-arginine supplementation in cystic fibrosis patients: A placebo-controlled study. Eur Respir J 25: 62-68.
-
(2005)
Eur Respir J
, vol.25
, pp. 62-68
-
-
Grasemann, H.1
Grasemann, C.2
Kurtz, F.3
Tietze-Schillings, G.4
Vester, U.5
Ratjen, F.6
-
40
-
-
33846907545
-
A1-Antitrypsin inhalation reduces airway inflammation in cystic fibrosis patients
-
Griese M, Latzin P, Kappler M, Weckerle K, Heinzlmaier T, Bernhardt T, Hartl D. 2007. a1-Antitrypsin inhalation reduces airway inflammation in cystic fibrosis patients. Eur Respir J 29: 240-250.
-
(2007)
Eur Respir J
, vol.29
, pp. 240-250
-
-
Griese, M.1
Latzin, P.2
Kappler, M.3
Weckerle, K.4
Heinzlmaier, T.5
Bernhardt, T.6
Hartl, D.7
-
41
-
-
0037794398
-
Characteristics of EPI-hNE4 aerosol: A new elastase inhibitor for treatment of cystic fibrosis
-
Grimbert D, Vecellio L, Delépine P, Attucci S, Boissinot E, Poncin A, Gauthier F, Valat C, Saudubray F, Antonioz P, et al. 2003. Characteristics of EPI-hNE4 aerosol: A new elastase inhibitor for treatment of cystic fibrosis. J Aerosol Med 16: 121-129.
-
(2003)
J Aerosol Med
, vol.16
, pp. 121-129
-
-
Grimbert, D.1
Vecellio, L.2
Delépine, P.3
Attucci, S.4
Boissinot, E.5
Poncin, A.6
Gauthier, F.7
Valat, C.8
Saudubray, F.9
Antonioz, P.10
-
42
-
-
22544453909
-
Inhaled glutathione decreases PGE2 and increases lymphocytes in cystic fibrosis lungs
-
Hartl D, Starosta V, Maier K, Beck-Speier I, Rebhan C, Becker BF, Latzin P, Fischer R, Ratjen F, Huber RM, et al. 2005. Inhaled glutathione decreases PGE2 and increases lymphocytes in cystic fibrosis lungs. Free Radic Biol Med 39: 463-472.
-
(2005)
Free Radic Biol Med
, vol.39
, pp. 463-472
-
-
Hartl, D.1
Starosta, V.2
Maier, K.3
Beck-Speier, I.4
Rebhan, C.5
Becker, B.F.6
Latzin, P.7
Fischer, R.8
Ratjen, F.9
Huber, R.M.10
-
43
-
-
33744461829
-
Anti-inflammatory effect of augmented nitric oxide production in chronic lung infection
-
Hopkins N, Gunning Y, O'Croinin DF, Laffey JG, Mc-Loughlin P. 2006. Anti-inflammatory effect of augmented nitric oxide production in chronic lung infection. J Pathol 209: 198-205.
-
(2006)
J Pathol
, vol.209
, pp. 198-205
-
-
Hopkins, N.1
Gunning, Y.2
O'Croinin, D.F.3
Laffey, J.G.4
Mc-Loughlin, P.5
-
44
-
-
0030802906
-
Pulmonary oxidative stress response in young children with cystic fibrosis
-
Hull J, Vervaart P, Grimwood K, Phelan P. 1997. Pulmonary oxidative stress response in young children with cystic fibrosis. Thorax 52: 557-560.
-
(1997)
Thorax
, vol.52
, pp. 557-560
-
-
Hull, J.1
Vervaart, P.2
Grimwood, K.3
Phelan, P.4
-
45
-
-
0035894284
-
2 synthases by ibuprofen, naproxen, and indomethacin
-
Jaradat MS, Wongsud B, Phornchirasilp S, Rangwala SM, Shams G, Sutton M, Romstedt KJ, Noonan DJ, Feller DR. 2001. Activation of peroxisome proliferators-activated receptor isoforms and inhibition of prostaglandin H2 synthases by ibuprofen, naproxen, and indomethacin. Biochem Pharmacol 62: 1587-1595.
-
(2001)
Biochem Pharmacol
, vol.62
, pp. 1587-1595
-
-
Jaradat, M.S.1
Wongsud, B.2
Phornchirasilp, S.3
Rangwala, S.M.4
Shams, G.5
Sutton, M.6
Romstedt, K.J.7
Noonan, D.J.8
Feller, D.R.9
-
46
-
-
0032531160
-
Inducible nitric oxide synthase expression is reduced in cystic fibrosis murine and human airway epithelial cells
-
Kelley TJ, Drumm ML. 1998. Inducible nitric oxide synthase expression is reduced in cystic fibrosis murine and human airway epithelial cells. J Clin Invest 102: 1200-1207.
-
(1998)
J Clin Invest
, vol.102
, pp. 1200-1207
-
-
Kelley, T.J.1
Drumm, M.L.2
-
47
-
-
0028914085
-
Early pulmonary inflammation in infants with cystic fibrosis
-
Khan TZ, Wagener JS, Bost T, Martinez J, Accurso FJ, Riches DW. 1995. Early pulmonary inflammation in infants with cystic fibrosis. Am J Respir Crit Care Med 151: 1075-1082.
-
(1995)
Am J Respir Crit Care Med
, vol.151
, pp. 1075-1082
-
-
Khan, T.Z.1
Wagener, J.S.2
Bost, T.3
Martinez, J.4
Accurso, F.J.5
Riches, D.W.6
-
48
-
-
0029799340
-
Increased DNA levels in bronchoalveo-lar lavage fluid obtained from infants with cystic fibrosis
-
Kirchner KK, Wagener JS, Khan TZ, Copenhaver SC, Accurso FJ. 1996. Increased DNA levels in bronchoalveo-lar lavage fluid obtained from infants with cystic fibrosis. Am J Respir Crit Care Med 154: 1426-1429.
-
(1996)
Am J Respir Crit Care Med
, vol.154
, pp. 1426-1429
-
-
Kirchner, K.K.1
Wagener, J.S.2
Khan, T.Z.3
Copenhaver, S.C.4
Accurso, F.J.5
-
49
-
-
55149093388
-
Ibuprofen therapy for cystic fibrosis lung disease: Revisited
-
Konstan MW. 2008. Ibuprofen therapy for cystic fibrosis lung disease: Revisited. Curr Opin Pulm Med 14: 567-573.
-
(2008)
Curr Opin Pulm Med
, vol.14
, pp. 567-573
-
-
Konstan, M.W.1
-
50
-
-
0030881846
-
Current understanding of the inflammatory process in cystic fibrosis-Onset and etiology
-
Konstan MW, Berger M. 1997. Current understanding of the inflammatory process in cystic fibrosis-Onset and etiology. Pediatr Pulmonol 24: 137-142.
-
(1997)
Pediatr Pulmonol
, vol.24
, pp. 137-142
-
-
Konstan, M.W.1
Berger, M.2
-
51
-
-
0027682586
-
Leukotriene B4 is markedly elevated in the epithelial lining fluidof patients with cystic fibrosis
-
Konstan MW, Walenga RW, Hilliard KA, Hilliard JB. 1993. Leukotriene B4 is markedly elevated in the epithelial lining fluidof patients with cystic fibrosis. Am Rev Respir Dis 148: 896-901.
-
(1993)
Am Rev Respir Dis
, vol.148
, pp. 896-901
-
-
Konstan, M.W.1
Walenga, R.W.2
Hilliard, K.A.3
Hilliard, J.B.4
-
52
-
-
0028015883
-
Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation
-
Konstan MW, Hilliard KA, Norvell TM, Berger M. 1994. Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation. Am J Respir Crit Care Med 150: 448-454.
-
(1994)
Am J Respir Crit Care Med
, vol.150
, pp. 448-454
-
-
Konstan, M.W.1
Hilliard, K.A.2
Norvell, T.M.3
Berger, M.4
-
54
-
-
0042934009
-
Effect of ibuprofen on neutrophil migration in vivo in cystic fibrosis
-
Konstan MW, Krenicky JE, Finney MR, Kirchner HL, Hilliard KA, Hilliard JB, Davis PB, Hoppel CL. 2003. Effect of ibuprofen on neutrophil migration in vivo in cystic fibrosis. J Pharmacol Exp Ther 306: 1086-1091.
-
(2003)
J Pharmacol Exp Ther
, vol.306
, pp. 1086-1091
-
-
Konstan, M.W.1
Krenicky, J.E.2
Finney, M.R.3
Kirchner, H.L.4
Hilliard, K.A.5
Hilliard, J.B.6
Davis, P.B.7
Hoppel, C.L.8
-
55
-
-
29144528654
-
4 receptor antagonist) for the treatment of CF lung disease
-
Konstan MW, Doring G, Lands LC, Hilliard KA, Koker P, Bhattacharya S, Staab A, Hamilton AL. 2005. Results of a phase II clinical trial of BIIL 284 BS (a LTB4 receptor antagonist) for the treatment of CF lung disease. Pediatr Pulmonol 40 (Suppl 28): 125-127.
-
(2005)
Pediatr Pulmonol
, vol.40
, Issue.SUPPL. 28
, pp. 125-127
-
-
Konstan, M.W.1
Doring, G.2
Lands, L.C.3
Hilliard, K.A.4
Koker, P.5
Bhattacharya, S.6
Staab, A.7
Hamilton, A.L.8
-
56
-
-
36848999782
-
Clinical use of ibuprofen is associated with slower FEV1 decline in children with cystic fibrosis
-
Konstan MW, Schluchter MD, Xue W, Davis PB. 2007. Clinical use of ibuprofen is associated with slower FEV1 decline in children with cystic fibrosis. Am J Respir Crit Care Med 176: 1084-1089.
-
(2007)
Am J Respir Crit Care Med
, vol.176
, pp. 1084-1089
-
-
Konstan, M.W.1
Schluchter, M.D.2
Xue, W.3
Davis, P.B.4
-
57
-
-
84886091119
-
A pilot study evaluating the effect of pioglitazone, simvastatin, and ibuprofen on neutrophil migration in vivo in healthy subjects
-
Konstan M, Krenicky J, Hilliard K, Hilliard J. 2009. A pilot study evaluating the effect of pioglitazone, simvastatin, and ibuprofen on neutrophil migration in vivo in healthy subjects. Pediatr Pulmonol 44 (Suppl 32): 289-290.
-
(2009)
Pediatr Pulmonol
, vol.44
, Issue.SUPPL. 32
, pp. 289-290
-
-
Konstan, M.1
Krenicky, J.2
Hilliard, K.3
Hilliard, J.4
-
58
-
-
79951840468
-
Tobramycin inhalation powder for P. aeruginosa infection in cystic fibrosis: The EVOLVE trial
-
Konstan MW, Geller DE, Minić P, Brockhaus F, Zhang J, Angyalosi G. 2011. Tobramycin inhalation powder for P. aeruginosa infection in cystic fibrosis: The EVOLVE trial. Pediatr Pulmonol 46: 230-238.
-
(2011)
Pediatr Pulmonol
, vol.46
, pp. 230-238
-
-
Konstan, M.W.1
Geller, D.E.2
Minić, P.3
Brockhaus, F.4
Zhang, J.5
Angyalosi, G.6
-
60
-
-
70350506537
-
Effect of simvastatin on exhaled nitric oxide and inflammatory markers in sputum in patients with cystic fibrosis
-
Kraynack NC, Chmiel JF, Xue W, Schluchter MD, Gibson RL, Kelley TJ, Hilliard JB, Konstan MW. 2008. Effect of simvastatin on exhaled nitric oxide and inflammatory markers in sputum in patients with cystic fibrosis. Pediatr Pulmonol 43 (Suppl 31): 300.
-
(2008)
Pediatr Pulmonol
, vol.43
, Issue.SUPPL. 31
, pp. 300
-
-
Kraynack, N.C.1
Chmiel, J.F.2
Xue, W.3
Schluchter, M.D.4
Gibson, R.L.5
Kelley, T.J.6
Hilliard, J.B.7
Konstan, M.W.8
-
61
-
-
0034704799
-
Risk of persistent growth impairment after alternate-day prednisone treatment in children with cystic fibrosis
-
Lai H-C, FitzSimmons SC, Allen DB, Kosorok MR, Ro-senstein BJ, Campbell PW, Farrell PM. 2000. Risk of persistent growth impairment after alternate-day prednisone treatment in children with cystic fibrosis. N Engl J Med 342: 851-859.
-
(2000)
N Engl J Med
, vol.342
, pp. 851-859
-
-
Lai, H.-C.1
Fitzsimmons, S.C.2
Allen, D.B.3
Kosorok, M.R.4
Ro-Senstein, B.J.5
Campbell, P.W.6
Farrell, P.M.7
-
62
-
-
44949151079
-
Oral non-steroidal anti-inflammatory drug therapy for cystic fibrosis
-
Lands L, Stanojevic S. 2007. Oral non-steroidal anti-inflammatory drug therapy for cystic fibrosis. Cochrane Database Syst Rev 17: CD001505.
-
(2007)
Cochrane Database Syst Rev
, vol.17
-
-
Lands, L.1
Stanojevic, S.2
-
63
-
-
34548038663
-
High-dose ibuprofen in cystic fibrosis: Canadian safety and effectiveness trial
-
Lands LC, Milner R, Cantin AM, Manson D, Corey M. 2007. High-dose ibuprofen in cystic fibrosis: Canadian safety and effectiveness trial. J Pediatr 151: 228-230.
-
(2007)
J Pediatr
, vol.151
, pp. 228-230
-
-
Lands, L.C.1
Milner, R.2
Cantin, A.M.3
Manson, D.4
Corey, M.5
-
64
-
-
79959340752
-
SB-656933, a novel CXCR2 selective antagonist, inhibits ex vivo neutrophil activation and ozone-induced airway inflammation in humans
-
Lazaar AL, Sweeney LE, MacDonald AJ, Alexis NE, Chen C, Tal-Singer R. 2011. SB-656933, a novel CXCR2 selective antagonist, inhibits ex vivo neutrophil activation and ozone-induced airway inflammation in humans. Br J Clin Pharmacol 72: 282-293.
-
(2011)
Br J Clin Pharmacol
, vol.72
, pp. 282-293
-
-
Lazaar, A.L.1
Sweeney, L.E.2
Macdonald, A.J.3
Alexis, N.E.4
Chen, C.5
Tal-Singer, R.6
-
65
-
-
0031851457
-
Glutathione permeability of CFTR
-
Linsdell P, Hanrahan JW. 1998. Glutathione permeability of CFTR. Am J Physiol 275 (Pt 1): C323-C326.
-
(1998)
Am J Physiol
, vol.275
, Issue.PART 1
-
-
Linsdell, P.1
Hanrahan, J.W.2
-
66
-
-
77950682572
-
The changing microbial epidemiology in CF
-
LiPuma J. 2010. The changing microbial epidemiology in CF. Clin Microbiol Rev 23: 299-323.
-
(2010)
Clin Microbiol Rev
, vol.23
, pp. 299-323
-
-
Lipuma, J.1
-
67
-
-
84866063949
-
The new microbiology of cystic fibrosis: It takes a community
-
LiPuma J. 2012. The new microbiology of cystic fibrosis: It takes a community. Thorax 67: 851-852.
-
(2012)
Thorax
, vol.67
, pp. 851-852
-
-
Lipuma, J.1
-
68
-
-
21244455537
-
Role of IL-17A, IL-17F, and the IL-17 receptor in regulating growth related oncogene-a and granulocyte colony-stimulating factor in bronchial epithelium: Implications for airway inflammation in cystic fibrosis
-
McAllister F, Henry A, Kreindler JL, Dubin PJ, Ulrich L, Steele C, Finder JD, Pilewski JM, Carreno BM, Goldman SJ, et al. 2005. Role of IL-17A, IL-17F, and the IL-17 receptor in regulating growth related oncogene-a and granulocyte colony-stimulating factor in bronchial epithelium: Implications for airway inflammation in cystic fibrosis. J Immunol 175: 404-412.
-
(2005)
J Immunol
, vol.175
, pp. 404-412
-
-
McAllister, F.1
Henry, A.2
Kreindler, J.L.3
Dubin, P.J.4
Ulrich, L.5
Steele, C.6
Finder, J.D.7
Pilewski, J.M.8
Carreno, B.M.9
Goldman, S.J.10
-
69
-
-
0025966879
-
Aerosol a1-antitrypsin treatment for cystic fibrosis
-
McElvaney NG, Hubbard RC, Birrer P, Chernick MS, Caplan DB, Frank MM, Crystal RG. 1991. Aerosol a1-antitrypsin treatment for cystic fibrosis. Lancet 337: 392-394.
-
(1991)
Lancet
, vol.337
, pp. 392-394
-
-
McElvaney, N.G.1
Hubbard, R.C.2
Birrer, P.3
Chernick, M.S.4
Caplan, D.B.5
Frank, M.M.6
Crystal, R.G.7
-
70
-
-
0027495712
-
Pharmacokinetics of recombinant secretory leukoprotease inhibitor aerosolized to normals and individuals with cystic fibrosis
-
McElvaney NG, Doujaiji B, Moan MJ, Burnham MR, Wu MC, Crystal RG. 1993. Pharmacokinetics of recombinant secretory leukoprotease inhibitor aerosolized to normals and individuals with cystic fibrosis. Am Rev Respir Dis 148 (Pt 1): 1056-1060.
-
(1993)
Am Rev Respir Dis
, vol.148
, Issue.PART 1
, pp. 1056-1060
-
-
McElvaney, N.G.1
Doujaiji, B.2
Moan, M.J.3
Burnham, M.R.4
Wu, M.C.5
Crystal, R.G.6
-
71
-
-
0031913858
-
Lack of inducible nitric oxide syn-thase in bronchial epithelium: A possible mechanism of susceptibility to infection in cystic fibrosis
-
Meng QH, Springall DR, Bishop AE, Morgan K, Evans TJ, Habib S, Gruenert DC, Gyi KM, Hodson ME, Ya-coub MH, et al. 1998. Lack of inducible nitric oxide syn-thase in bronchial epithelium: A possible mechanism of susceptibility to infection in cystic fibrosis. J Pathol 184: 323-331.
-
(1998)
J Pathol
, vol.184
, pp. 323-331
-
-
Meng, Q.H.1
Springall, D.R.2
Bishop, A.E.3
Morgan, K.4
Evans, T.J.5
Habib, S.6
Gruenert, D.C.7
Gyi, K.M.8
Hodson, M.E.9
Ya-Coub, M.H.10
-
72
-
-
20144387174
-
Randomized, double-blind, placebo-controlled, dose-escalating studyof aerosolized inter-feron g-1b in patients with mild to moderate cystic fibro-sis lung disease
-
Moss RB, Mayer-Hamblett N, Wagener J, Daines C, Hale K, Ahrens R, Gibson RL, Anderson P, Retsch-Bogart G, Nasr SZ, et al. 2005. Randomized, double-blind, placebo-controlled, dose-escalating studyof aerosolized inter-feron g-1b in patients with mild to moderate cystic fibro-sis lung disease. Pediatr Pulmonol 39: 209-218.
-
(2005)
Pediatr Pulmonol
, vol.39
, pp. 209-218
-
-
Moss, R.B.1
Mayer-Hamblett, N.2
Wagener, J.3
Daines, C.4
Hale, K.5
Ahrens, R.6
Gibson, R.L.7
Anderson, P.8
Retsch-Bogart, G.9
Nasr, S.Z.10
-
73
-
-
84885086048
-
Safety and early treatment effects of the CXCR2 antagonist SB-656933 in patients with cystic fibrosis
-
for the CF2110399 Investigators, pii: S1569-1993(12)00155-5
-
Moss RB, Mistry SJ, Konstan MW, Pilewski JM, Kerem E, Tal-Singer R, Lazaar AL, for the CF2110399 Investigators. 2012. Safety and early treatment effects of the CXCR2 antagonist SB-656933 in patients with cystic fibrosis. J Cyst Fibros pii: S1569-1993(12)00155-5
-
(2012)
J Cyst Fibros
-
-
Moss, R.B.1
Mistry, S.J.2
Konstan, M.W.3
Pilewski, J.M.4
Kerem, E.5
Tal-Singer, R.6
Lazaar, A.L.7
-
74
-
-
0032770489
-
Quantitation of inflammatory response to bacteria in young cystic fibrosis and control patients
-
Muhlebach MS, PW Stewart, Leigh MW, Noah TL. 1999. Quantitation of inflammatory response to bacteria in young cystic fibrosis and control patients. Am J Respir Crit Care Med 160: 186-191.
-
(1999)
Am J Respir Crit Care Med
, vol.160
, pp. 186-191
-
-
Muhlebach, M.S.1
Stewart, P.W.2
Leigh, M.W.3
Noah, T.L.4
-
75
-
-
72449174784
-
The triterpenoid CDDO limits inflammation in preclinical models of cystic fibrosis lung disease
-
Nichols DP, Ziady AG, Shank SL, Eastman JF, Davis PB. 2009. The triterpenoid CDDO limits inflammation in preclinical models of cystic fibrosis lung disease. Am J Physiol Lung Cell Mol Physiol 297: L828-L836.
-
(2009)
Am J Physiol Lung Cell Mol Physiol
, vol.297
-
-
Nichols, D.P.1
Ziady, A.G.2
Shank, S.L.3
Eastman, J.F.4
Davis, P.B.5
-
76
-
-
0031035884
-
Nasal and bronchoalveolar lavage fluid cytokines in early cystic fibrosis
-
Noah TL, Black HR, Cheng PW, Wood RE, Leigh MW. 1997. Nasal and bronchoalveolar lavage fluid cytokines in early cystic fibrosis. J Infect Dis 175: 638-647.
-
(1997)
J Infect Dis
, vol.175
, pp. 638-647
-
-
Noah, T.L.1
Black, H.R.2
Cheng, P.W.3
Wood, R.E.4
Leigh, M.W.5
-
77
-
-
84886086446
-
A pilot studyevaluating the potential useoflow-dose meth-otrexate as an anti-inflammatory therapy for cystic fibro-sis lung disease
-
Oermann CM, Katz M, Wheeler C, Cumming S. 2007. A pilot studyevaluating the potential useoflow-dose meth-otrexate as an anti-inflammatory therapy for cystic fibro-sis lung disease. Pediatr Pulmonol 42 (Suppl 30): 292-293.
-
(2007)
Pediatr Pulmonol
, vol.42
, Issue.SUPPL. 30
, pp. 292-293
-
-
Oermann, C.M.1
Katz, M.2
Wheeler, C.3
Cumming, S.4
-
78
-
-
3042856185
-
2/2 mice
-
2/2 mice. J Cell Physiol 200: 235-244.
-
(2004)
J Cell Physiol
, vol.200
, pp. 235-244
-
-
Ollero, M.1
Junaidi, O.2
Zaman, M.M.3
Tzameli, I.4
Ferrando, A.A.5
Andersson, C.6
Blanco, P.G.7
Bialecki, E.8
Freedman, S.D.9
-
79
-
-
84856731944
-
Incidence and risk factors for pulmonary exacerbation treatment failures in cystic fibrosis patients chronically infected with Pseudo-monas aeruginosa
-
Parkins MD, Rendall JC, Elborn JS. 2012. Incidence and risk factors for pulmonary exacerbation treatment failures in cystic fibrosis patients chronically infected with Pseudo-monas aeruginosa. Chest 141: 485-493.
-
(2012)
Chest
, vol.141
, pp. 485-493
-
-
Parkins, M.D.1
Rendall, J.C.2
Elborn, J.S.3
-
80
-
-
52149111858
-
Peroxisome proliferator-activated re-ceptor-g in cystic fibrosis lung epithelium
-
Perez A, van Heeckeren AM, Nichols D, Gupta S, Eastman JF, Davis PB. 2008. Peroxisome proliferator-activated re-ceptor-g in cystic fibrosis lung epithelium. Am J Physiol Lung Cell Mol Physiol 295: L303-L313.
-
(2008)
Am J Physiol Lung Cell Mol Physiol
, vol.295
-
-
Perez, A.1
van Heeckeren, A.M.2
Nichols, D.3
Gupta, S.4
Eastman, J.F.5
Davis, P.B.6
-
81
-
-
84870742117
-
Comparisonof two treatment regimens for eradication of P. aeruginosa infection in children with cystic fibrosis
-
Proesmans M. 2013. Comparisonof two treatment regimens for eradication of P. aeruginosa infection in children with cystic fibrosis. J Cyst Fibros 12: 29-34.
-
(2013)
J Cyst Fibros
, vol.12
, pp. 29-34
-
-
Proesmans, M.1
-
82
-
-
77950914953
-
Treatment of early Pseudomonas aeruginosa infec tion in patients with cystic fibrosis: The ELITE trial
-
ELITE Study Group
-
Ratjen F, Munck A, Kho P, Angyalosi G, ELITE Study Group. 2010. Treatment of early Pseudomonas aeruginosa infec tion in patients with cystic fibrosis: The ELITE trial. Tho rax 65: 286-291.
-
(2010)
Tho Rax
, vol.65
, pp. 286-291
-
-
Ratjen, F.1
Munck, A.2
Kho, P.3
Angyalosi, G.4
-
83
-
-
56049085357
-
Relationship between inhaled corticoste-roid therapy and rate of lung function decline in children with cystic fibrosis
-
Scientific Advisory Group the Investigators and Coordinators of the Epidemiologic Study of Cystic Fibrosis
-
Ren CL, Pasta DJ, Rasouliyan L, Wagener JS, Konstan MW, Morgan WJ, Scientific Advisory Group the Investigators and Coordinators of the Epidemiologic Study of Cystic Fibrosis. 2008. Relationship between inhaled corticoste-roid therapy and rate of lung function decline in children with cystic fibrosis. J Pediatr 153: 746-751.
-
(2008)
J Pediatr
, vol.153
, pp. 746-751
-
-
Ren, C.L.1
Pasta, D.J.2
Rasouliyan, L.3
Wagener, J.S.4
Konstan, M.W.5
Morgan, W.J.6
-
84
-
-
0036066345
-
Simvastatin reduces expression of cytokines inter-leukin-6, interleukin-8, and monocyte chemoattractant protein-1 in circulating monocytes from hypercholester-olemic patients
-
Rezaie-Majd A, Maca T, Bucek RA, Valent P, Müller MR, Husslein P, Kashanipour A, Minar E, Baghestanian M. 2002. Simvastatin reduces expression of cytokines inter-leukin-6, interleukin-8, and monocyte chemoattractant protein-1 in circulating monocytes from hypercholester-olemic patients. Arterioscler Thromb Vasc Biol 22: 1194-1199.
-
(2002)
Arterioscler Thromb Vasc Biol
, vol.22
, pp. 1194-1199
-
-
Rezaie-Majd, A.1
Maca, T.2
Bucek, R.A.3
Valent, P.4
Müller, M.R.5
Husslein, P.6
Kashanipour, A.7
Minar, E.8
Baghestanian, M.9
-
85
-
-
62949240359
-
The role of inhaled corticosteroids in the management of cystic fibrosis
-
Ross KR, Chmiel JF, Konstan MW. 2009. The role of inhaled corticosteroids in the management of cystic fibrosis. Paediatr Drugs 11: 101-113.
-
(2009)
Paediatr Drugs
, vol.11
, pp. 101-113
-
-
Ross, K.R.1
Chmiel, J.F.2
Konstan, M.W.3
-
86
-
-
0027742895
-
Systemic deficiencyof glutathione in cystic fibrosis
-
Roum JH, Buhl R, McElvaney NG, Borok Z, Crystal RG. 1993. Systemic deficiencyof glutathione in cystic fibrosis. J Appl Physiol 75: 2419-2424.
-
(1993)
J Appl Physiol
, vol.75
, pp. 2419-2424
-
-
Roum, J.H.1
Buhl, R.2
McElvaney, N.G.3
Borok, Z.4
Crystal, R.G.5
-
87
-
-
0042867242
-
Troglitazone antagonizes tumor necrosis factor-a-induced reprogramming of adipocyte gene expression by inhibiting the transcrip-tional regulatory functions of NF-kB
-
Ruan H, Pownall HJ, Lodish HF. 2003. Troglitazone antagonizes tumor necrosis factor-a-induced reprogramming of adipocyte gene expression by inhibiting the transcrip-tional regulatory functions of NF-kB. J Biol Chem 278: 28181-28192.
-
(2003)
J Biol Chem
, vol.278
, pp. 28181-28192
-
-
Ruan, H.1
Pownall, H.J.2
Lodish, H.F.3
-
88
-
-
77957694293
-
Failure to recover to baseline pulmonary function after cystic fibrosis pulmonaryexac-erbation
-
Sanders DB, Bittner RC, Rosenfeld M, Hoffman LR, Redding GJ, Goss CH. 2010. Failure to recover to baseline pulmonary function after cystic fibrosis pulmonaryexac-erbation. Am J Respir Crit Care Med 182: 627-632.
-
(2010)
Am J Respir Crit Care Med
, vol.182
, pp. 627-632
-
-
Sanders, D.B.1
Bittner, R.C.2
Rosenfeld, M.3
Hoffman, L.R.4
Redding, G.J.5
Goss, C.H.6
-
89
-
-
84875215401
-
Safety, efficacy and convenience of colistimethate sodium dry powder for inhalation (Colobreathe DPI) in cystic fibrosis patients: A randomised study
-
for the Freedom Study Group
-
Schuster A, Haliburn C, Döring G, Goldman MH, for the Freedom Study Group. 2012. Safety, efficacy and convenience of colistimethate sodium dry powder for inhalation (Colobreathe DPI) in cystic fibrosis patients: A randomised study. Thorax 68: 344-350.
-
(2012)
Thorax
, vol.68
, pp. 344-350
-
-
Schuster, A.1
Haliburn, C.2
Döring, G.3
Goldman, M.H.4
-
90
-
-
39049142717
-
Exacerbations in cystic fibrosis: 3-Management
-
Smyth A, Elborn JS. 2008. Exacerbations in cystic fibrosis: 3-Management. Thorax 63: 180-184.
-
(2008)
Thorax
, vol.63
, pp. 180-184
-
-
Smyth, A.1
Elborn, J.S.2
-
91
-
-
84874139969
-
Prophylactic anti-staphylococ-cal antibiotics for cystic fibrosis
-
23235585
-
Smyth AR, Walters S. 2012. Prophylactic anti-staphylococ-cal antibiotics for cystic fibrosis. Cochrane Database Syst Rev 12: CD001912. 23235585.
-
(2012)
Cochrane Database Syst Rev
, vol.12
-
-
Smyth, A.R.1
Walters, S.2
-
92
-
-
80053364019
-
Pulmonary exacerbations in cystic fibrosis
-
Stenbit AE, Flume PA. 2011. Pulmonary exacerbations in cystic fibrosis. Curr Opin Pulm Med 17: 442-447.
-
(2011)
Curr Opin Pulm Med
, vol.17
, pp. 442-447
-
-
Stenbit, A.E.1
Flume, P.A.2
-
93
-
-
84866061431
-
Early antibiotic treatment for Pseudo-monas aeruginosa eradication in patients with cystic fi-brosis: A randomised multicentre study comparing two different protocols
-
Taccetti G, Bianchini E, Cariani L, Buzzetti R, Costantini D, Trevisan F. 2012. Early antibiotic treatment for Pseudo-monas aeruginosa eradication in patients with cystic fi-brosis: A randomised multicentre study comparing two different protocols. Thorax 67: 853-859.
-
(2012)
Thorax
, vol.67
, pp. 853-859
-
-
Taccetti, G.1
Bianchini, E.2
Cariani, L.3
Buzzetti, R.4
Costantini, D.5
Trevisan, F.6
-
94
-
-
33645229803
-
High-dose oral N-ace-tylcysteine, a glutathione prodrug, modulates inflammation in cystic fibrosis
-
Tirouvanziam R, Conrad CK, Bottiglieri T, Herzenberg LA, Moss RB, Herzenberg LA. 2006. High-dose oral N-ace-tylcysteine, a glutathione prodrug, modulates inflammation in cystic fibrosis. Proc Natl Acad Sci 103: 4628-4633.
-
(2006)
Proc Natl Acad Sci
, vol.103
, pp. 4628-4633
-
-
Tirouvanziam, R.1
Conrad, C.K.2
Bottiglieri, T.3
Herzenberg, L.A.4
Moss, R.B.5
Herzenberg, L.A.6
-
95
-
-
80052511405
-
Comparative efficacy and safetyof 4 randomized regimens to treat early Pseudomonas aerugi-nosa infection inchildren with cystic fibrosis
-
Treggiari MM, Retsch-Bogart G, Mayer-Hamblett N, Khan U, Kulich M, Kronmal R, Williams J, Hiatt P, Gibson RL, Spencer T, et al. 2011. Comparative efficacy and safetyof 4 randomized regimens to treat early Pseudomonas aerugi-nosa infection inchildren with cystic fibrosis. Arch Pediatr Adolesc Med 165: 847-856.
-
(2011)
Arch Pediatr Adolesc Med
, vol.165
, pp. 847-856
-
-
Treggiari, M.M.1
Retsch-Bogart, G.2
Mayer-Hamblett, N.3
Khan, U.4
Kulich, M.5
Kronmal, R.6
Williams, J.7
Hiatt, P.8
Gibson, R.L.9
Spencer, T.10
-
96
-
-
42949105490
-
Detection of anaerobic bacteria in high numbers in sputum from patients with cystic fibrosis
-
Tunney MM, Field TR, Moriarty TF, Patrick S, Doering G, Muhlebach MS, Wolfgang MC, Boucher R, Gilpin DF, McDowell A, et al. 2008. Detection of anaerobic bacteria in high numbers in sputum from patients with cystic fibrosis. Am J Respir Crit Care Med 177: 995-1001.
-
(2008)
Am J Respir Crit Care Med
, vol.177
, pp. 995-1001
-
-
Tunney, M.M.1
Field, T.R.2
Moriarty, T.F.3
Patrick, S.4
Doering, G.5
Muhlebach, M.S.6
Wolfgang, M.C.7
Boucher, R.8
Gilpin, D.F.9
McDowell, A.10
-
97
-
-
79959325084
-
Use of culture and molecular analysis to determine the effect of antibiotic treatment on microbial community diversity and abundance during exacerbation in patients with cystic fibrosis
-
Tunney MM, Klem ER, Fodor AA, Gilpin DF, Moriarty TF, McGrath SJ, Muhlebach MS, Boucher RC, Cardwell C, Doering G, et al. 2011. Use of culture and molecular analysis to determine the effect of antibiotic treatment on microbial community diversity and abundance during exacerbation in patients with cystic fibrosis. Thorax 66: 579-584.
-
(2011)
Thorax
, vol.66
, pp. 579-584
-
-
Tunney, M.M.1
Klem, E.R.2
Fodor, A.A.3
Gilpin, D.F.4
Moriarty, T.F.5
McGrath, S.J.6
Muhlebach, M.S.7
Boucher, R.C.8
Cardwell, C.9
Doering, G.10
-
98
-
-
0025868478
-
Prevention of chronic Pseudomonas aeruginosa colonisation in cystic fibrosis by early treatment
-
Valerius NH, Koch C, Høiby N. 1991. Prevention of chronic Pseudomonas aeruginosa colonisation in cystic fibrosis by early treatment. Lancet 338: 725-726.
-
(1991)
Lancet
, vol.338
, pp. 725-726
-
-
Valerius, N.H.1
Koch, C.2
Høiby, N.3
-
99
-
-
39849100408
-
Oral DHA supplementation in DF508 homozygous cystic fibrosis patients
-
Van Biervliet S, Devos M, Delhaye T, Van Biervliet JP, Robberecht E, Christophe A. 2008. Oral DHA supplementation in DF508 homozygous cystic fibrosis patients. Prostaglandins Leukot Essent Fatty Acids 78: 109-115.
-
(2008)
Prostaglandins Leukot Essent Fatty Acids
, vol.78
, pp. 109-115
-
-
van Biervliet, S.1
Devos, M.2
Delhaye, T.3
van Biervliet, J.P.4
Robberecht, E.5
Christophe, A.6
-
100
-
-
1542373503
-
A paradigm for gene regulation: Inflammation, NF-kB, and PPAR
-
Vanden Berghe W, Vermeulen L, Delerive P, De Bosscher K, Staels B, Haegeman G. 2003. A paradigm for gene regulation: Inflammation, NF-kB, and PPAR. Adv Exp Med Biol 544: 181-196.
-
(2003)
Adv Exp Med Biol
, vol.544
, pp. 181-196
-
-
Vanden Berghe, W.1
Vermeulen, L.2
Delerive, P.3
de Bosscher, K.4
Staels, B.5
Haegeman, G.6
-
101
-
-
77957296044
-
Assessing time to pulmonary function benefit following antibiotic treatment of acute cystic fibrosis exacerbations
-
VanDevanter DR, O'Riordan MA, Blumer JL, Konstan MW. 2010. Assessing time to pulmonary function benefit following antibiotic treatment of acute cystic fibrosis exacerbations. Respir Res 11: 137.
-
(2010)
Respir Res
, vol.11
, pp. 137
-
-
Vandevanter, D.R.1
O'Riordan, M.A.2
Blumer, J.L.3
Konstan, M.W.4
-
102
-
-
0034816784
-
Antioxidant imbalance in the lungs of cystic fibrosis transmembrane conductance regulator protein mutant mice
-
Velsor LW, van Heeckeren A, Day BJ. 2001. Antioxidant imbalance in the lungs of cystic fibrosis transmembrane conductance regulator protein mutant mice. Am J Physiol Lung Cell Mol Physiol 281: L31-L38.
-
(2001)
Am J Physiol Lung Cell Mol Physiol
, vol.281
-
-
Velsor, L.W.1
van Heeckeren, A.2
Day, B.J.3
-
103
-
-
84859839030
-
Basic science for the chest physician: Pseudomonas aeruginosa and the cystic fibrosis airway
-
Williams HD, Davies JC. 2012. Basic science for the chest physician: Pseudomonas aeruginosa and the cystic fibrosis airway. Thorax 67: 465-467.
-
(2012)
Thorax
, vol.67
, pp. 465-467
-
-
Williams, H.D.1
Davies, J.C.2
-
104
-
-
70350512309
-
Hydroxychloroquine-Pilot study of anti-inflammatory effects in cystic fibrosis
-
Williams B, Robinette M, Slovis B, Deretci V, Perkett E.2008. Hydroxychloroquine-Pilot study of anti-inflammatory effects in cystic fibrosis. Pediatr Pulmonol 43 (Suppl 31): 314.
-
(2008)
Pediatr Pulmonol
, vol.43
, Issue.SUPPL. 31
, pp. 314
-
-
Williams, B.1
Robinette, M.2
Slovis, B.3
Deretci, V.4
Perkett, E.5
-
105
-
-
0036445650
-
Modulation of inflammatory mediators and PPARg and NFkB expression by pravastatin in response to lipopro-teins in human monocytes in vitro
-
Zelvyte I, Dominaitiene R, Crisby M, Janciauskiene S. 2002. Modulation of inflammatory mediators and PPARg and NFkB expression by pravastatin in response to lipopro-teins in human monocytes in vitro. Pharmacol Res 45: 147-154.
-
(2002)
Pharmacol Res
, vol.45
, pp. 147-154
-
-
Zelvyte, I.1
Dominaitiene, R.2
Crisby, M.3
Janciauskiene, S.4
-
106
-
-
84859576702
-
Decade-long bacterial community dynamics in cystic fibrosis airways
-
Zhao J, Schloss PD, Kalikin LM, Carmody LA, Foster BK, Petrosino JF, Cavalcoli JD, VanDevanter DR, Murray S, Li JZ, et al. 2012. Decade-long bacterial community dynamics in cystic fibrosis airways. Proc Natl Acad Sci 109: 5809-5814.
-
(2012)
Proc Natl Acad Sci
, vol.109
, pp. 5809-5814
-
-
Zhao, J.1
Schloss, P.D.2
Kalikin, L.M.3
Carmody, L.A.4
Foster, B.K.5
Petrosino, J.F.6
Cavalcoli, J.D.7
Vandevanter, D.R.8
Murray, S.9
Li, J.Z.10
-
107
-
-
0346366979
-
2 and ciglitazone, reduce systemic inflammation in polymicor-bial sepsis by modulation of signal transduction pathways
-
12,14-prostaglandin J2 and ciglitazone, reduce systemic inflammation in polymicor-bial sepsis by modulation of signal transduction pathways. J Immunol 171: 6827-6837.
-
(2003)
J Immunol
, vol.171
, pp. 6827-6837
-
-
Zingarelli, B.1
Sheehan, M.2
Hake, P.W.3
O'Connor, M.4
Denen-Berg, A.5
Cook, J.A.6
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