A membrane lipid imbalance plays a role in the phenotypic expression of cystic fibrosis in cftr-/- mice

Proceedings of the National Academy of Sciences of the United States of America

Volumn 96, Issue 24, 1999, Pages 13995-14000

  Freedman, Steven D ^a,c   Katz, Mark H ^a   Parker, Eliza M ^a   Laposata, Michael ^a,b   Urman, Mark Y ^a   Alvarez, Juan G ^a,c  

^a HARVARD MEDICAL SCHOOL   (United States)

^b MASSACHUSETTS GENERAL HOSPITAL   (United States)

^c BETH ISRAEL DEACONESS MEDICAL CENTER   (United States)

Author keywords

Arachidonic acid; Docosahexaenoic acid; Fish oil; Lung; Pancreas

Indexed keywords

DOCOSAHEXAENOIC ACID; ESSENTIAL FATTY ACID; FISH OIL; MEMBRANE LIPID; PHOSPHOLIPID; TRANSMEMBRANE CONDUCTANCE REGULATOR;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARACHIDONIC ACID METABOLISM; ARTICLE; CYSTIC FIBROSIS; FATTY ACID DESATURATION; FATTY ACID METABOLISM; GENE EXPRESSION; GENE MUTATION; INTESTINE ABSORPTION; LIPID ANALYSIS; LUNG LAVAGE; MOUSE; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL;

ADMINISTRATION, ORAL; ANIMALS; ARACHIDONIC ACID; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; DOCOSAHEXAENOIC ACIDS; ILEUM; INTESTINAL ABSORPTION; LIPOPOLYSACCHARIDES; LIVER; LUNG; MEMBRANE LIPIDS; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; PANCREAS; PHENOTYPE; PHOSPHOLIPIDS; PNEUMONIA; PSEUDOMONAS;

ANIMALIA;

EID: 0033598714     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.96.24.13995     Document Type: Article

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