메뉴 건너뛰기




Volumn 176, Issue 10, 2007, Pages 957-969

Cystic fibrosis pulmonary guidelines: Chronic medications for maintenance of lung health

(15)  Flume, Patrick A a,h   O'Sullivan, Brian P b   Robinson, Karen A c   Goss, Christopher H d   Mogayzel Jr , Peter J c   Willey Courand, Donna Beth e   Bujan, Janet f   Finder, Jonathan g   Lester, Mary h   Quittell, Lynne i   Rosenblatt, Randall j   Vender, Robert L k   Hazle, Leslie l   Sabadosa, Kathy m   Marshall, Bruce l  


Author keywords

Antibiotics; Antiinflammatory agents; Bronchodilators; Hypertonic; Mucolytics; Saline solution

Indexed keywords

ACETYLCYSTEINE; ANTIBIOTIC AGENT; AZITHROMYCIN; BECLOMETASONE; BETA 2 ADRENERGIC RECEPTOR STIMULATING AGENT; BRONCHODILATING AGENT; BUDESONIDE; CEFALEXIN; CEFTAZIDIME; CHOLINERGIC RECEPTOR BLOCKING AGENT; CLARITHROMYCIN; COLISTIN; CORTICOSTEROID; CROMOGLYCATE DISODIUM; DORNASE ALFA; FLUTICASONE; GENTAMICIN; IBUPROFEN; ICOSAPENTAENOIC ACID; LEUKOTRIENE RECEPTOR BLOCKING AGENT; MACROLIDE; MONTELUKAST; NONSTEROID ANTIINFLAMMATORY AGENT; PIROXICAM; PREDNISONE; SALBUTAMOL; SODIUM CHLORIDE; TOBRAMYCIN; UNINDEXED DRUG; ZAFIRLUKAST;

EID: 36248953255     PISSN: 1073449X     EISSN: 15354970     Source Type: Journal    
DOI: 10.1164/rccm.200705-664OC     Document Type: Article
Times cited : (593)

References (112)
  • 1
    • 36249001174 scopus 로고    scopus 로고
    • Cystic Fibrosis Foundation. Cystic Fibrosis Foundation Patient Registry
    • Bethesda, MD: Cystic Fibrosis Foundation;
    • Cystic Fibrosis Foundation. Cystic Fibrosis Foundation Patient Registry: 2005 Annual data report to the center directors. Bethesda, MD: Cystic Fibrosis Foundation; 2006.
    • (2005) Annual data report to the center directors
  • 3
    • 0028452511 scopus 로고
    • Consensus conference: Practical applications of Pulmozyme
    • Ramsey BW, Dorkin HL. Consensus conference: practical applications of Pulmozyme. Pediatr Pulmonol 1994;17:404-408.
    • (1994) Pediatr Pulmonol , vol.17 , pp. 404-408
    • Ramsey, B.W.1    Dorkin, H.L.2
  • 4
    • 0035318124 scopus 로고    scopus 로고
    • Harris RP, Helfand M, Woolf SH, Lohr KN, Mulrow CD, Teutsch SM, Atkins D; Methods Word Group, Third US Preventive Services Task Force. Current methods of the US Preventive Services Task Force: a review of the process. Am J Prev Med 2001;20(Suppl 3):21-35. Article reproduced on Agency for Healthcare Research and Quality website. Rockville, MD: AHRQ, Available from: http://www.ahrq.gov/clinic/ajpmsuppl/harris1.htm (cited 2007 Sep).
    • Harris RP, Helfand M, Woolf SH, Lohr KN, Mulrow CD, Teutsch SM, Atkins D; Methods Word Group, Third US Preventive Services Task Force. Current methods of the US Preventive Services Task Force: a review of the process. Am J Prev Med 2001;20(Suppl 3):21-35. Article reproduced on Agency for Healthcare Research and Quality website. Rockville, MD: AHRQ, Available from: http://www.ahrq.gov/clinic/ajpmsuppl/harris1.htm (cited 2007 Sep).
  • 5
    • 0036320272 scopus 로고    scopus 로고
    • Pseudomonas aeruginosa and other predictors of mortality and morbidity in young children with cystic fibrosis
    • Emerson J, Rosenfeld M, McNamara S, Ramsey B, Gibson RL. Pseudomonas aeruginosa and other predictors of mortality and morbidity in young children with cystic fibrosis. Pediatr Pulmonol 2002;34:91-100.
    • (2002) Pediatr Pulmonol , vol.34 , pp. 91-100
    • Emerson, J.1    Rosenfeld, M.2    McNamara, S.3    Ramsey, B.4    Gibson, R.L.5
  • 7
    • 0024331219 scopus 로고
    • Long-term effects of inhaled tobramycin in patients with cystic fibrosis colonized with Pseudomonas aeruginosa
    • MacLusky IB, Gold R, Corey M, Levison H. Long-term effects of inhaled tobramycin in patients with cystic fibrosis colonized with Pseudomonas aeruginosa. Pediatr Pulmonol 1989;7:42-48.
    • (1989) Pediatr Pulmonol , vol.7 , pp. 42-48
    • MacLusky, I.B.1    Gold, R.2    Corey, M.3    Levison, H.4
  • 9
    • 2642712510 scopus 로고    scopus 로고
    • Placebo-controlled, double-blind, randomized study of aerosolized tobramycin for early treatment of Pseudomonas aeruginosa colonization in cystic fibrosis
    • Wiesemann HG, Steinkamp G, Ratjen F, Bauernfeind A, Przyklenk B, Doring G, von der Hardt H. Placebo-controlled, double-blind, randomized study of aerosolized tobramycin for early treatment of Pseudomonas aeruginosa colonization in cystic fibrosis. Pediatr Pulmonol 1998;25:88-92.
    • (1998) Pediatr Pulmonol , vol.25 , pp. 88-92
    • Wiesemann, H.G.1    Steinkamp, G.2    Ratjen, F.3    Bauernfeind, A.4    Przyklenk, B.5    Doring, G.6    von der Hardt, H.7
  • 10
    • 0141613178 scopus 로고    scopus 로고
    • Nebulised anti-pseudomonal antibiotics for cystic fibrosis
    • updated 2006; accessed September 2007];3:CD001021. Available from
    • Ryan G, Mukhopadhyay S, Singh M. Nebulised anti-pseudomonal antibiotics for cystic fibrosis. Cochrane Database Syst Rev [serial on the Internet]. 2003 [updated 2006; accessed September 2007];3:CD001021. Available from http://www.cochrane.org/reviews/clibintro.htm
    • (2003) Cochrane Database Syst Rev [serial on the Internet]
    • Ryan, G.1    Mukhopadhyay, S.2    Singh, M.3
  • 13
    • 0023265976 scopus 로고
    • Colistin inhalation therapy in cystic fibrosis patients with chronic Pseudomonas aeruginosa lung infection
    • Jensen T, Pedersen SS, Garne S, Heilmann C, Høiby N, Koch C. Colistin inhalation therapy in cystic fibrosis patients with chronic Pseudomonas aeruginosa lung infection. J Antimicrob Chemother 1987;19:831-838.
    • (1987) J Antimicrob Chemother , vol.19 , pp. 831-838
    • Jensen, T.1    Pedersen, S.S.2    Garne, S.3    Heilmann, C.4    Høiby, N.5    Koch, C.6
  • 14
    • 0036736583 scopus 로고    scopus 로고
    • A randomised clinical trial of nebulised tobramycin or colistin in cystic fibrosis
    • Hodson ME, Gallagher CG, Govan JRW. A randomised clinical trial of nebulised tobramycin or colistin in cystic fibrosis. Eur Respir J 2002;20:658-664.
    • (2002) Eur Respir J , vol.20 , pp. 658-664
    • Hodson, M.E.1    Gallagher, C.G.2    Govan, J.R.W.3
  • 15
    • 84980270127 scopus 로고
    • Nebulized gentamicin in children and adolescents with cystic fibrosis
    • Kun P, Landau LI, Phelan PD. Nebulized gentamicin in children and adolescents with cystic fibrosis. Aust Paediatr J 1984;20:43-45.
    • (1984) Aust Paediatr J , vol.20 , pp. 43-45
    • Kun, P.1    Landau, L.I.2    Phelan, P.D.3
  • 16
    • 0023219505 scopus 로고
    • Inhaled ceftazidime compared with gentamicin and carbenicillin in older patients with cystic fibrosis infected with Pseudomonas aeruginosa
    • Stead RJ, Hodson ME, Batten JC. Inhaled ceftazidime compared with gentamicin and carbenicillin in older patients with cystic fibrosis infected with Pseudomonas aeruginosa. Br J Dis Chest 1987;81:272-279.
    • (1987) Br J Dis Chest , vol.81 , pp. 272-279
    • Stead, R.J.1    Hodson, M.E.2    Batten, J.C.3
  • 18
    • 0028129568 scopus 로고
    • Pulmozyme Study Group. Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis
    • Fuchs HJ, Borowitz DS, Christiansen DH, Morris EM, Nash ML, Ramsey BW, Rosenstein BJ, Smith AL, Wohl ME; Pulmozyme Study Group. Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. N Engl J Med 1994;331:637-642.
    • (1994) N Engl J Med , vol.331 , pp. 637-642
    • Fuchs, H.J.1    Borowitz, D.S.2    Christiansen, D.H.3    Morris, E.M.4    Nash, M.L.5    Ramsey, B.W.6    Rosenstein, B.J.7    Smith, A.L.8    Wohl, M.E.9
  • 20
    • 0029921953 scopus 로고    scopus 로고
    • Effects of 12-week administration of dornase alfa in patients with advanced cystic fibrosis lung disease
    • McCoy K, Hamilton S, Johnson C. Effects of 12-week administration of dornase alfa in patients with advanced cystic fibrosis lung disease. Chest 1996;110:889-895.
    • (1996) Chest , vol.110 , pp. 889-895
    • McCoy, K.1    Hamilton, S.2    Johnson, C.3
  • 24
    • 0027181325 scopus 로고
    • Efficacy and safety of short-term administration of aerosolised recombinant human DNase I in adults with stable stage cystic fibrosis
    • Ranasinha C, Assoufi B, Shak S, Christiansen D, Fuchs H, Empey D, Geddes D, Hodson M. Efficacy and safety of short-term administration of aerosolised recombinant human DNase I in adults with stable stage cystic fibrosis. Lancet 1993;342:199-202.
    • (1993) Lancet , vol.342 , pp. 199-202
    • Ranasinha, C.1    Assoufi, B.2    Shak, S.3    Christiansen, D.4    Fuchs, H.5    Empey, D.6    Geddes, D.7    Hodson, M.8
  • 25
    • 0030027655 scopus 로고    scopus 로고
    • In vivo effects of recombinant human DNase I on sputum in patients with cystic fibrosis
    • Shah PL, Scott SF, Knight RA, Marriott C, Ranasinha C, Hodson ME. In vivo effects of recombinant human DNase I on sputum in patients with cystic fibrosis. Thorax 1996;51:119-125.
    • (1996) Thorax , vol.51 , pp. 119-125
    • Shah, P.L.1    Scott, S.F.2    Knight, R.A.3    Marriott, C.4    Ranasinha, C.5    Hodson, M.E.6
  • 26
    • 0029067641 scopus 로고
    • Recombinant human DNase I in cystic fibrosis patients with severe pulmonary disease: A short-term, double-blind study followed by six months open-label treatment
    • Shah PI, Bush A, Canny GJ, Colin AA, Fuchs HJ, Geddes DM, Johnson CAC, Light MC, Scott SF, Tullis DE, et al. Recombinant human DNase I in cystic fibrosis patients with severe pulmonary disease: a short-term, double-blind study followed by six months open-label treatment. Eur Respir J 1995;8:954-958.
    • (1995) Eur Respir J , vol.8 , pp. 954-958
    • Shah, P.I.1    Bush, A.2    Canny, G.J.3    Colin, A.A.4    Fuchs, H.J.5    Geddes, D.M.6    Johnson, C.A.C.7    Light, M.C.8    Scott, S.F.9    Tullis, D.E.10
  • 27
    • 0034095691 scopus 로고    scopus 로고
    • Effect of a short course of rhDNase on cough and mucociliary clearance in patients with cystic fibrosis
    • Robinson M, Hemming AL, Moriarty C, Eberl S, Bye PTP. Effect of a short course of rhDNase on cough and mucociliary clearance in patients with cystic fibrosis. Pediatr Pulmonol 2000;30:16-24.
    • (2000) Pediatr Pulmonol , vol.30 , pp. 16-24
    • Robinson, M.1    Hemming, A.L.2    Moriarty, C.3    Eberl, S.4    Bye, P.T.P.5
  • 29
    • 0141501501 scopus 로고    scopus 로고
    • Recombinant human deoxyribonuclease for cystic fibrosis
    • updated 2005; accessed September 2007];3:CD001127. Available from
    • Jones AP, Wallis CE, Kearney CE. Recombinant human deoxyribonuclease for cystic fibrosis. Cochrane Database Syst Rev [serial on the Internet]. 2003 [updated 2005; accessed September 2007];3:CD001127. Available from http://www.cochrane.org/reviews/clibintro.htm
    • (2003) Cochrane Database Syst Rev [serial on the Internet]
    • Jones, A.P.1    Wallis, C.E.2    Kearney, C.E.3
  • 30
    • 0035666058 scopus 로고    scopus 로고
    • A two-year randomized, placebo-controlled trial of dornase alfa in young patients with cystic fibrosis with mild lung function abnormalities
    • Quan JM, Tiddens HAWM, Sy JP, McKenzie SG, Montgomery MD, Robinson PJ, Wohl MEB, Konstan MW. A two-year randomized, placebo-controlled trial of dornase alfa in young patients with cystic fibrosis with mild lung function abnormalities. J Pediatr 2001;139:813-820.
    • (2001) J Pediatr , vol.139 , pp. 813-820
    • Quan, J.M.1    Tiddens, H.A.W.M.2    Sy, J.P.3    McKenzie, S.G.4    Montgomery, M.D.5    Robinson, P.J.6    Wohl, M.E.B.7    Konstan, M.W.8
  • 32
    • 0035021689 scopus 로고    scopus 로고
    • Use of computerized tomography and chest x-rays in evaluating efficacy of aerosolized recombinant human DNase in cystic fibrosis patients younger than age 5 years: A preliminary study
    • Nasr SZ, Kuhns LR, Brown RW, Hurwitz ME, Sanders GM, Strouse PJ. Use of computerized tomography and chest x-rays in evaluating efficacy of aerosolized recombinant human DNase in cystic fibrosis patients younger than age 5 years: a preliminary study. Pediatr Pulmonol 2001;31:377-382.
    • (2001) Pediatr Pulmonol , vol.31 , pp. 377-382
    • Nasr, S.Z.1    Kuhns, L.R.2    Brown, R.W.3    Hurwitz, M.E.4    Sanders, G.M.5    Strouse, P.J.6
  • 36
    • 0036123981 scopus 로고    scopus 로고
    • Hypertonic saline and recombinant human DNase: A randomised crossover pilot study in patients with cystic fibrosis
    • Ballmann M, von der Hardt H. Hypertonic saline and recombinant human DNase: a randomised crossover pilot study in patients with cystic fibrosis. J Cyst Fibros 2002;1:35-37.
    • (2002) J Cyst Fibros , vol.1 , pp. 35-37
    • Ballmann, M.1    von der Hardt, H.2
  • 37
    • 0036793667 scopus 로고    scopus 로고
    • Effects of hypertonic saline, alternate day and daily rhDNase on healthcare use, costs and outcomes in children with cystic fibrosis
    • Suri R, Grieve R, Normand C, Metcalfe C, Thompson S, Wallis C, Bush A. Effects of hypertonic saline, alternate day and daily rhDNase on healthcare use, costs and outcomes in children with cystic fibrosis. Thorax 2002;57:841-846.
    • (2002) Thorax , vol.57 , pp. 841-846
    • Suri, R.1    Grieve, R.2    Normand, C.3    Metcalfe, C.4    Thompson, S.5    Wallis, C.6    Bush, A.7
  • 38
    • 32944463102 scopus 로고    scopus 로고
    • Nebulised hypertonic saline for cystic fibrosis
    • accessed September 2007];3:CD001506. Available from
    • Wark PA, McDonald V, Jones AP. Nebulised hypertonic saline for cystic fibrosis. Cochrane Database Syst Rev [serial on the Internet]. 2005 [accessed September 2007];3:CD001506. Available from http://www.cochrane.org/ reviews/clibintro.htm
    • (2005) Cochrane Database Syst Rev [serial on the Internet]
    • Wark, P.A.1    McDonald, V.2    Jones, A.P.3
  • 40
    • 0028015883 scopus 로고
    • Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation
    • Konstan MW, Hilliard KA, Norvell TM, Berger M. Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation. Am J Respir Crit Care Med 1994;150:448-454.
    • (1994) Am J Respir Crit Care Med , vol.150 , pp. 448-454
    • Konstan, M.W.1    Hilliard, K.A.2    Norvell, T.M.3    Berger, M.4
  • 42
    • 0030883124 scopus 로고    scopus 로고
    • Randomised controlled trial of inhaled corticosteroids (fluticasone propionate) in cystic fibrosis
    • Balfour-Lynn IM, Klein NJ, Dinwiddie R. Randomised controlled trial of inhaled corticosteroids (fluticasone propionate) in cystic fibrosis. Arch Dis Child 1997;77:124-130.
    • (1997) Arch Dis Child , vol.77 , pp. 124-130
    • Balfour-Lynn, I.M.1    Klein, N.J.2    Dinwiddie, R.3
  • 43
    • 0030062339 scopus 로고    scopus 로고
    • Pilot study to assess the effect of inhaled corticosteroids on lung function in patients with cystic fibrosis
    • Nikolaizik WH, Schöni MH. Pilot study to assess the effect of inhaled corticosteroids on lung function in patients with cystic fibrosis. J Pediatr 1996;128:271-274.
    • (1996) J Pediatr , vol.128 , pp. 271-274
    • Nikolaizik, W.H.1    Schöni, M.H.2
  • 44
    • 0020696950 scopus 로고
    • Chronic Pseudomonas aeruginosa lung infection in cystic fibrosis: A longitudinal study of immune complex activity and inflammatory response in sputum sol-phase of cystic fibrosis patients with chronic Pseudomonas aeruginosa lung infections: influence of local steroid treatment
    • Schiotz PO, Jorgensen M, Flensborg EW, Faero O, Husby S, Hoiby N, Jacobsen SV, Nielsen H, Svehag SE. Chronic Pseudomonas aeruginosa lung infection in cystic fibrosis: a longitudinal study of immune complex activity and inflammatory response in sputum sol-phase of cystic fibrosis patients with chronic Pseudomonas aeruginosa lung infections: influence of local steroid treatment. Acta Paediatr Scand 1983;72:283-287.
    • (1983) Acta Paediatr Scand , vol.72 , pp. 283-287
    • Schiotz, P.O.1    Jorgensen, M.2    Flensborg, E.W.3    Faero, O.4    Husby, S.5    Hoiby, N.6    Jacobsen, S.V.7    Nielsen, H.8    Svehag, S.E.9
  • 45
    • 0032721113 scopus 로고    scopus 로고
    • Effects of short-term inhaled fluticasone on oxidative burst of sputum cells in cystic fibrosis patients
    • Dauletbaev N, Viel K, Behr J, Loitsch S, Buhl R, Wagner TOF, Bargon J. Effects of short-term inhaled fluticasone on oxidative burst of sputum cells in cystic fibrosis patients. Eur Respir J 1999;14:1150-1155.
    • (1999) Eur Respir J , vol.14 , pp. 1150-1155
    • Dauletbaev, N.1    Viel, K.2    Behr, J.3    Loitsch, S.4    Buhl, R.5    Wagner, T.O.F.6    Bargon, J.7
  • 47
    • 0028936456 scopus 로고
    • The effects of the inhaled corticosteroid budesonide on lung function and bronchial hyperresponsiveness in adult patients with cystic fibrosis
    • van Haren EHJ, Lammers J-WJ, Festen J, Heijerman HGM, Groot CAR, van Herwaarden CLA. The effects of the inhaled corticosteroid budesonide on lung function and bronchial hyperresponsiveness in adult patients with cystic fibrosis. Respir Med 1995;89:209-214.
    • (1995) Respir Med , vol.89 , pp. 209-214
    • van Haren, E.H.J.1    Lammers, J.-W.J.2    Festen, J.3    Heijerman, H.G.M.4    Groot, C.A.R.5    van Herwaarden, C.L.A.6
  • 48
    • 84921430420 scopus 로고    scopus 로고
    • Inhaled corticosteroids for cystic fibrosis
    • updated 2006; accessed September 2007];2:CD001915. Available from
    • Balfour-Lynn I, Walters S, Dezateux C. Inhaled corticosteroids for cystic fibrosis. Cochrane Database Syst Rev [serial on the Internet]. 2000 [updated 2006; accessed September 2007];2:CD001915. Available from http://www.cochrane.org/reviews/clibintro.htm
    • (2000) Cochrane Database Syst Rev [serial on the Internet]
    • Balfour-Lynn, I.1    Walters, S.2    Dezateux, C.3
  • 49
    • 0021970474 scopus 로고
    • Alternate-day prednisone reduces morbidity and improves pulmonary function in cystic fibrosis
    • Auerbach HS, Williams M, Kirkpatrick JA, Colten HR. Alternate-day prednisone reduces morbidity and improves pulmonary function in cystic fibrosis. Lancet 1985;2:686-688.
    • (1985) Lancet , vol.2 , pp. 686-688
    • Auerbach, H.S.1    Williams, M.2    Kirkpatrick, J.A.3    Colten, H.R.4
  • 50
    • 0028169953 scopus 로고
    • Interleukin-1α, soluble interleukin-2 receptor, and IgG concentrations in cystic fibrosis treated with prednisolone
    • Greally P, Hussain MJ, Vergani D, Price JF. Interleukin-1α, soluble interleukin-2 receptor, and IgG concentrations in cystic fibrosis treated with prednisolone. Arch Dis Child 1994;71:35-39.
    • (1994) Arch Dis Child , vol.71 , pp. 35-39
    • Greally, P.1    Hussain, M.J.2    Vergani, D.3    Price, J.F.4
  • 51
    • 0028969594 scopus 로고
    • Cystic Fibrosis Foundation Prednisone Trial Group. A multicenter study of alternate-day prednisone therapy in patients with cystic fibrosis
    • Eigen H, Rosenstein BJ, FitzSimmons S, Schidlow DV; Cystic Fibrosis Foundation Prednisone Trial Group. A multicenter study of alternate-day prednisone therapy in patients with cystic fibrosis. J Pediatr 1995;126:515-523.
    • (1995) J Pediatr , vol.126 , pp. 515-523
    • Eigen, H.1    Rosenstein, B.J.2    FitzSimmons, S.3    Schidlow, D.V.4
  • 52
    • 84921431158 scopus 로고    scopus 로고
    • Oral steroids for cystic fibrosis
    • updated 2006; accessed September 2007];2:CD000407. Available from
    • Cheng K, Ashby D, Smyth R. Oral steroids for cystic fibrosis. Cochrane Database Syst Rev [serial on the Internet]. 2000 [updated 2006; accessed September 2007];2:CD000407. Available from http://www.cochrane.org/reviews/ clibintro.htm
    • (2000) Cochrane Database Syst Rev [serial on the Internet]
    • Cheng, K.1    Ashby, D.2    Smyth, R.3
  • 53
    • 0022638834 scopus 로고
    • Prednisolone in the treatment of airflow obstruction in adults with cystic fibrosis
    • Pantin CFA, Stead RJ, Hodson ME, Batten JC. Prednisolone in the treatment of airflow obstruction in adults with cystic fibrosis. Thorax 1986;41:34-38.
    • (1986) Thorax , vol.41 , pp. 34-38
    • Pantin, C.F.A.1    Stead, R.J.2    Hodson, M.E.3    Batten, J.C.4
  • 54
    • 0025763746 scopus 로고
    • Ibuprofen in children with cystic fibrosis: Pharmacokinetics and adverse effects
    • Konstan MW, Hoppel CL, Chai B, Davis PB. Ibuprofen in children with cystic fibrosis: pharmacokinetics and adverse effects. J Pediatr 1991;118:956-964.
    • (1991) J Pediatr , vol.118 , pp. 956-964
    • Konstan, M.W.1    Hoppel, C.L.2    Chai, B.3    Davis, P.B.4
  • 55
    • 0028914667 scopus 로고
    • Effect of high-dose ibuprofen in patients with cystic fibrosis
    • Konstan MW, Byard PJ, Hoppel CL, Davis PB. Effect of high-dose ibuprofen in patients with cystic fibrosis. N Engl J Med 1995;332:848-854.
    • (1995) N Engl J Med , vol.332 , pp. 848-854
    • Konstan, M.W.1    Byard, P.J.2    Hoppel, C.L.3    Davis, P.B.4
  • 56
    • 0028137161 scopus 로고
    • A preliminary study on the effect of anti-inflammatory treatment in cystic fibrosis patients with Pseudomonas aeruginosa lung infection
    • Sordelli DO, Macri CN, Maillie AJ, Cerquetti MC. A preliminary study on the effect of anti-inflammatory treatment in cystic fibrosis patients with Pseudomonas aeruginosa lung infection. Int J Immunopathol Pharmacol 1994;7:109-117.
    • (1994) Int J Immunopathol Pharmacol , vol.7 , pp. 109-117
    • Sordelli, D.O.1    Macri, C.N.2    Maillie, A.J.3    Cerquetti, M.C.4
  • 57
    • 44949151079 scopus 로고    scopus 로고
    • Oral non-steroidal anti-inflammatory drug therapy for cystic fibrosis
    • updated 2005; accessed September 2007];2:CD001505. Available from
    • Lands LC, Dezateux C, Crighton A. Oral non-steroidal anti-inflammatory drug therapy for cystic fibrosis. Cochrane Database Syst Rev [serial on the Internet]. 1999 [updated 2005; accessed September 2007];2:CD001505. Available from http://www.cochrane.org/reviews/clibintro.htm
    • (1999) Cochrane Database Syst Rev [serial on the Internet]
    • Lands, L.C.1    Dezateux, C.2    Crighton, A.3
  • 59
    • 4143087044 scopus 로고    scopus 로고
    • Effect of montelukast on lung function and clinical symptoms in patients with cystic fibrosis]
    • Stelmach I, Korzeniewska A, Smejda K, Jarosz I, Stelmach W. [Effect of montelukast on lung function and clinical symptoms in patients with cystic fibrosis]. Pneumonol Alergol Pol 2004;72:85-89.
    • (2004) Pneumonol Alergol Pol , vol.72 , pp. 85-89
    • Stelmach, I.1    Korzeniewska, A.2    Smejda, K.3    Jarosz, I.4    Stelmach, W.5
  • 60
    • 0038102862 scopus 로고    scopus 로고
    • A pilot study of zafirlukast as an anti-inflammatory agent in the treatment of adults with cystic fibrosis
    • Conway SP, Etherington C, Peckham DG, Whitehead A. A pilot study of zafirlukast as an anti-inflammatory agent in the treatment of adults with cystic fibrosis. J Cyst Fibros 2003;2:25-28.
    • (2003) J Cyst Fibros , vol.2 , pp. 25-28
    • Conway, S.P.1    Etherington, C.2    Peckham, D.G.3    Whitehead, A.4
  • 62
    • 0021962057 scopus 로고
    • Sodium cromoglycate-induced changes in the dose-response curve of inhaled methacholine in cystic fibrosis
    • Mitchell I. Sodium cromoglycate-induced changes in the dose-response curve of inhaled methacholine in cystic fibrosis. Ann Allergy 1985;54:233-235.
    • (1985) Ann Allergy , vol.54 , pp. 233-235
    • Mitchell, I.1
  • 63
    • 0027687886 scopus 로고
    • Comparison of efficacy of salbutamol and sodium cromoglycate in the prevention of ticarcillin-induced bronchoconstriction
    • Chua HL, Walker SL, LeSouef PN, Sly PD. Comparison of efficacy of salbutamol and sodium cromoglycate in the prevention of ticarcillin-induced bronchoconstriction. Pediatr Pulmonol 1993;16:311-315.
    • (1993) Pediatr Pulmonol , vol.16 , pp. 311-315
    • Chua, H.L.1    Walker, S.L.2    LeSouef, P.N.3    Sly, P.D.4
  • 64
    • 0025341898 scopus 로고
    • A double-blind, randomized study of sodium cromoglycate versus placebo in patients with cystic fibrosis and bronchial hyperreactivity
    • Sivan Y, Arce P, Eigen H, Nickerson BG, Newth CJ. A double-blind, randomized study of sodium cromoglycate versus placebo in patients with cystic fibrosis and bronchial hyperreactivity. J Allergy Clin Immunol 1990;85:649-654.
    • (1990) J Allergy Clin Immunol , vol.85 , pp. 649-654
    • Sivan, Y.1    Arce, P.2    Eigen, H.3    Nickerson, B.G.4    Newth, C.J.5
  • 65
    • 0030869812 scopus 로고    scopus 로고
    • Erythromycin and diffuse panbronchiolitis
    • Koyama H, Geddes DM. Erythromycin and diffuse panbronchiolitis. Thorax 1997;52:915-918.
    • (1997) Thorax , vol.52 , pp. 915-918
    • Koyama, H.1    Geddes, D.M.2
  • 66
    • 0034961483 scopus 로고    scopus 로고
    • Effect of clarithromycin on airway obstruction and inflammatory markers in induced sputum in cystic fibrosis: A pilot study
    • Ordoñez CL, Stulbarg M, Grundland H, Liu JT, Boushey HA. Effect of clarithromycin on airway obstruction and inflammatory markers in induced sputum in cystic fibrosis: a pilot study. Pediatr Pulmonol 2001;32:29-37.
    • (2001) Pediatr Pulmonol , vol.32 , pp. 29-37
    • Ordoñez, C.L.1    Stulbarg, M.2    Grundland, H.3    Liu, J.T.4    Boushey, H.A.5
  • 68
    • 0036185807 scopus 로고    scopus 로고
    • Effect of long term treatment with azithromycin on disease parameters in cystic fibrosis: A randomised trial
    • Wolter J, Seeney S, Bell S, Bowler S, Masel P, McCormack J. Effect of long term treatment with azithromycin on disease parameters in cystic fibrosis: a randomised trial. Thorax 2002;57:212-216.
    • (2002) Thorax , vol.57 , pp. 212-216
    • Wolter, J.1    Seeney, S.2    Bell, S.3    Bowler, S.4    Masel, P.5    McCormack, J.6
  • 69
    • 0037190575 scopus 로고    scopus 로고
    • Long term azithromycin in children with cystic fibrosis: A randomised, placebo-controlled crossover trial
    • Equi A, Balfour-Lynn IM, Bush A, Rosenthal M. Long term azithromycin in children with cystic fibrosis: a randomised, placebo-controlled crossover trial. Lancet 2002;360:978-984.
    • (2002) Lancet , vol.360 , pp. 978-984
    • Equi, A.1    Balfour-Lynn, I.M.2    Bush, A.3    Rosenthal, M.4
  • 70
    • 3843141848 scopus 로고    scopus 로고
    • Macrolide antibiotics for cystic fibrosis
    • updated 2005; accessed September 2007];2:CD002203. Available from
    • Southern KW, Barker PM, Solis A. Macrolide antibiotics for cystic fibrosis. Cochrane Database Syst Rev [serial on the Internet]. 2004 [updated 2005; accessed September 2007];2:CD002203. Available from http://www.cochrane.org/reviews/clibintro.htm
    • (2004) Cochrane Database Syst Rev [serial on the Internet]
    • Southern, K.W.1    Barker, P.M.2    Solis, A.3
  • 72
    • 0018294305 scopus 로고
    • A placebo-controlled trial of cephalexin therapy in the ambulatory management of patients with cystic fibrosis
    • Loening-Baucke VA, Mischler E, Myers MG. A placebo-controlled trial of cephalexin therapy in the ambulatory management of patients with cystic fibrosis. J Pediatr 1979;95:630-637.
    • (1979) J Pediatr , vol.95 , pp. 630-637
    • Loening-Baucke, V.A.1    Mischler, E.2    Myers, M.G.3
  • 73
    • 0036220978 scopus 로고    scopus 로고
    • Antibiotic prophylaxis in infants and young children with cystic fibrosis: A randomized controlled trial
    • Stutman HR, Lieberman JM, Nussbaum E, Marks MI. Antibiotic prophylaxis in infants and young children with cystic fibrosis: a randomized controlled trial. J Pediatr 2002;140:299-305.
    • (2002) J Pediatr , vol.140 , pp. 299-305
    • Stutman, H.R.1    Lieberman, J.M.2    Nussbaum, E.3    Marks, M.I.4
  • 75
    • 84922260138 scopus 로고    scopus 로고
    • Prophylactic anti-staphylococcal antibiotics for cystic fibrosis
    • updated 2006; accessed September 2007];3:CD001912. Available from
    • Smyth A, Walters S. Prophylactic anti-staphylococcal antibiotics for cystic fibrosis. Cochrane Database Syst Rev [serial on the Internet]. 2003 [updated 2006; accessed September 2007];3:CD001912. Available from http://www.cochrane.org/reviews/clibintro.htm
    • (2003) Cochrane Database Syst Rev [serial on the Internet]
    • Smyth, A.1    Walters, S.2
  • 76
    • 33644875016 scopus 로고    scopus 로고
    • Inhaled bronchodilators for cystic fibrosis
    • accessed September 2007];4:CD003428. Available from
    • Halfhide C, Evans HJ, Couriel J. Inhaled bronchodilators for cystic fibrosis. Cochrane Database Syst Rev [serial on the Internet]. 2005 [accessed September 2007];4:CD003428. Available from http://www.cochrane.org/ reviews/clibintro.htm
    • (2005) Cochrane Database Syst Rev [serial on the Internet]
    • Halfhide, C.1    Evans, H.J.2    Couriel, J.3
  • 77
    • 36249030008 scopus 로고
    • Improvement in lung function after nebulised salbutamol and ipratropium in children with cystic fibrosis. Abstract
    • presented at the, Brussels, Belgium
    • Pitcher-Wilmott R, Matthew DJ, Ingram D, Tyson SL. Improvement in lung function after nebulised salbutamol and ipratropium in children with cystic fibrosis. Abstract presented at the 11th European Cystic Fibrosis Conference, Brussels, Belgium, 1982.
    • (1982) 11th European Cystic Fibrosis Conference
    • Pitcher-Wilmott, R.1    Matthew, D.J.2    Ingram, D.3    Tyson, S.L.4
  • 78
    • 36248964724 scopus 로고
    • The use of bronchodilators as an adjunct to physiotherapy in adults with cystic fibrosis. Abstract
    • presented at the, Brussels, Belgium
    • Duncan FR, Penketh ARL, Hodson ME, Batten JC. The use of bronchodilators as an adjunct to physiotherapy in adults with cystic fibrosis. Abstract presented at the 11th European Cystic Fibrosis Conference, Brussels, Belgium, 1982.
    • (1982) 11th European Cystic Fibrosis Conference
    • Duncan, F.R.1    Penketh, A.R.L.2    Hodson, M.E.3    Batten, J.C.4
  • 79
    • 0026858516 scopus 로고
    • Efficacy of salbutamol and ipratropium bromide in decreasing bronchial hyperreactivity in children with cystic fibrosis
    • Avital A, Sanchez I, Chernick V. Efficacy of salbutamol and ipratropium bromide in decreasing bronchial hyperreactivity in children with cystic fibrosis. Pediatr Pulmonol 1992;13:34-37.
    • (1992) Pediatr Pulmonol , vol.13 , pp. 34-37
    • Avital, A.1    Sanchez, I.2    Chernick, V.3
  • 81
    • 0036785093 scopus 로고    scopus 로고
    • Effectiveness and tolerability of high-dose salmeterol in cystic fibrosis
    • Hordvik NL, Sammut PH, Judy CG, Colombo JL. Effectiveness and tolerability of high-dose salmeterol in cystic fibrosis. Pediatr Pulmonol 2002;34:287-296.
    • (2002) Pediatr Pulmonol , vol.34 , pp. 287-296
    • Hordvik, N.L.1    Sammut, P.H.2    Judy, C.G.3    Colombo, J.L.4
  • 82
    • 0026500244 scopus 로고
    • Acute bronchodilator response to a combination of β-adrenergic and anticholinergic agents in patients with cystic fibrosis
    • Sanchez I, Holbrow J, Chernick V. Acute bronchodilator response to a combination of β-adrenergic and anticholinergic agents in patients with cystic fibrosis. J Pediatr 1992;120:486-488.
    • (1992) J Pediatr , vol.120 , pp. 486-488
    • Sanchez, I.1    Holbrow, J.2    Chernick, V.3
  • 83
    • 0035022142 scopus 로고    scopus 로고
    • Bronchodilatory effects of salbutamol, ipratropium bromide, and their combination: Double-blind, placebo-controlled crossover study in cystic fibrosis
    • Ziebach R, Pietsch-Breitfeld B, Bichler M, Busch A, Riethmuller J, Stern M. Bronchodilatory effects of salbutamol, ipratropium bromide, and their combination: double-blind, placebo-controlled crossover study in cystic fibrosis. Pediatr Pulmonol 2001;31:431-435.
    • (2001) Pediatr Pulmonol , vol.31 , pp. 431-435
    • Ziebach, R.1    Pietsch-Breitfeld, B.2    Bichler, M.3    Busch, A.4    Riethmuller, J.5    Stern, M.6
  • 85
    • 0032947760 scopus 로고    scopus 로고
    • Effects of standard and high doses of salmeterol on lung function of hospitalized patients with cystic fibrosis
    • Hordvik NL, Sammut PH, Judy CG, Colombo JL. Effects of standard and high doses of salmeterol on lung function of hospitalized patients with cystic fibrosis. Pediatr Pulmonol 1999;27:43-53.
    • (1999) Pediatr Pulmonol , vol.27 , pp. 43-53
    • Hordvik, N.L.1    Sammut, P.H.2    Judy, C.G.3    Colombo, J.L.4
  • 86
    • 2642660456 scopus 로고    scopus 로고
    • A placebo-controlled, double-blind trial of the long-term effects of albuterol administration in patients with cystic fibrosis
    • Konig P, Poehler J, Barbero GJ. A placebo-controlled, double-blind trial of the long-term effects of albuterol administration in patients with cystic fibrosis. Pediatr Pulmonol 1998;25:32-36.
    • (1998) Pediatr Pulmonol , vol.25 , pp. 32-36
    • Konig, P.1    Poehler, J.2    Barbero, G.J.3
  • 87
    • 0027197981 scopus 로고
    • The effect of high doses of inhaled salbutamol and ipratropium bromide in patients with stable cystic fibrosis
    • Sanchez I, De Koster J, Holbrow J, Chernick V. The effect of high doses of inhaled salbutamol and ipratropium bromide in patients with stable cystic fibrosis. Chest 1993;104:842-846.
    • (1993) Chest , vol.104 , pp. 842-846
    • Sanchez, I.1    De Koster, J.2    Holbrow, J.3    Chernick, V.4
  • 89
    • 20944451267 scopus 로고    scopus 로고
    • Inhaled β-agonists improve lung function but not maximal exercise capacity in cystic fibrosis
    • Dodd JD, Barry SC, Daly LE, Gallagher CG. Inhaled β-agonists improve lung function but not maximal exercise capacity in cystic fibrosis. J Cyst Fibros 2005;4:101-105.
    • (2005) J Cyst Fibros , vol.4 , pp. 101-105
    • Dodd, J.D.1    Barry, S.C.2    Daly, L.E.3    Gallagher, C.G.4
  • 90
    • 0036298101 scopus 로고    scopus 로고
    • Effects of salmeterol on arterial oxyhemoglobin saturations in patients with cystic fibrosis
    • Salvatore D, D'Andria M. Effects of salmeterol on arterial oxyhemoglobin saturations in patients with cystic fibrosis. Pediatr Pulmonol 2002;34:11-15.
    • (2002) Pediatr Pulmonol , vol.34 , pp. 11-15
    • Salvatore, D.1    D'Andria, M.2
  • 91
    • 0032987387 scopus 로고    scopus 로고
    • Systematic review of N-acetylcysteine in cystic fibrosis
    • Duijvestijn YC, Brand PL. Systematic review of N-acetylcysteine in cystic fibrosis. Acta Paediatr 1999;88:38-41.
    • (1999) Acta Paediatr , vol.88 , pp. 38-41
    • Duijvestijn, Y.C.1    Brand, P.L.2
  • 92
    • 33845975311 scopus 로고    scopus 로고
    • Maintenance azithromycin treatment in pediatric patients with cystic fibrosis: Long-term outcomes related to macrolide resistance and pulmonary function
    • Tramper-Stranders GA, Wolfs TF, Fleer A, Kimpen JL, van der Ent CK. Maintenance azithromycin treatment in pediatric patients with cystic fibrosis: long-term outcomes related to macrolide resistance and pulmonary function. Pediatr Infect Dis J 2007;26:8-12.
    • (2007) Pediatr Infect Dis J , vol.26 , pp. 8-12
    • Tramper-Stranders, G.A.1    Wolfs, T.F.2    Fleer, A.3    Kimpen, J.L.4    van der Ent, C.K.5
  • 94
    • 33644676982 scopus 로고    scopus 로고
    • A crossover, randomized, controlled trial of dornase alfa before versus after physiotherapy in cystic fibrosis
    • Fitzgerald DA, Hilton J, Jepson B, Smith L. A crossover, randomized, controlled trial of dornase alfa before versus after physiotherapy in cystic fibrosis. Pediatrics 2005;116:e549-e554.
    • (2005) Pediatrics , vol.116
    • Fitzgerald, D.A.1    Hilton, J.2    Jepson, B.3    Smith, L.4
  • 95
    • 0034835277 scopus 로고    scopus 로고
    • Microbiological and immunologic considerations with aerosolized drug delivery
    • LiPuma JJ. Microbiological and immunologic considerations with aerosolized drug delivery. Chest 2001;120:118S-123S.
    • (2001) Chest , vol.120
    • LiPuma, J.J.1
  • 96
    • 0029958486 scopus 로고    scopus 로고
    • Pharmacokinetics of inhaled drugs
    • Lipworth BJ. Pharmacokinetics of inhaled drugs. Br J Clin Pharmacol 1996;42:697-705.
    • (1996) Br J Clin Pharmacol , vol.42 , pp. 697-705
    • Lipworth, B.J.1
  • 97
    • 0003563693 scopus 로고    scopus 로고
    • Clinical Practice Guidelines for Cystic Fibrosis Committee, Bethesda, MD: Cystic Fibrosis Foundation;
    • Clinical Practice Guidelines for Cystic Fibrosis Committee. Clinical practice guidelines for cystic fibrosis. Bethesda, MD: Cystic Fibrosis Foundation; 1997.
    • (1997) Clinical practice guidelines for cystic fibrosis
  • 101
    • 0026602608 scopus 로고
    • Recombinant human DNase inhalation in normal subjects and patients with cystic fibrosis: A phase 1 study
    • Aitken ML, Burke W, McDonald G, Shak S, Montgomery AB, Smith A. Recombinant human DNase inhalation in normal subjects and patients with cystic fibrosis: a phase 1 study. JAMA 1992;267:1947-1951.
    • (1992) JAMA , vol.267 , pp. 1947-1951
    • Aitken, M.L.1    Burke, W.2    McDonald, G.3    Shak, S.4    Montgomery, A.B.5    Smith, A.6
  • 104
    • 0029037178 scopus 로고
    • Effect of rhDNase on lung function and quality of life in adult cystic fibrosis patients
    • Heijerman HGM, van Rossem RN, Bakker W. Effect of rhDNase on lung function and quality of life in adult cystic fibrosis patients. Neth J Med 1995;46:293-297.
    • (1995) Neth J Med , vol.46 , pp. 293-297
    • Heijerman, H.G.M.1    van Rossem, R.N.2    Bakker, W.3
  • 105
    • 0031973136 scopus 로고    scopus 로고
    • Prevalence and mechanisms of gastro-oesophageal reflux in adult cystic fibrosis patients
    • Ledson MJ, Tran J, Walshaw MJ. Prevalence and mechanisms of gastro-oesophageal reflux in adult cystic fibrosis patients. J R Soc Med 1998;91:7-9.
    • (1998) J R Soc Med , vol.91 , pp. 7-9
    • Ledson, M.J.1    Tran, J.2    Walshaw, M.J.3
  • 106
    • 0029093124 scopus 로고
    • Two years experience with recombinant human DNase I in the treatment of pulmonary disease in cystic fibrosis
    • Shah PL, Scott SF, Geddes DM, Hodson ME. Two years experience with recombinant human DNase I in the treatment of pulmonary disease in cystic fibrosis. Respir Med 1995;89:499-502.
    • (1995) Respir Med , vol.89 , pp. 499-502
    • Shah, P.L.1    Scott, S.F.2    Geddes, D.M.3    Hodson, M.E.4
  • 109
    • 0023936587 scopus 로고
    • The clinical effect and the effect on the ciliary motility of oral N-acetylcysteine in patients with cystic fibrosis and primary ciliary dyskinesia
    • Stafanger G, Garne S, Howitz P, Morkassel E, Koch C. The clinical effect and the effect on the ciliary motility of oral N-acetylcysteine in patients with cystic fibrosis and primary ciliary dyskinesia. Eur Respir J 1988;1:161-167.
    • (1988) Eur Respir J , vol.1 , pp. 161-167
    • Stafanger, G.1    Garne, S.2    Howitz, P.3    Morkassel, E.4    Koch, C.5
  • 110
    • 0022378715 scopus 로고
    • A double-blind placebo controlled trial with oral ambroxol and N-acetylcysteine for mucolytic treatment in cystic fibrosis
    • Ratjen F, Wonne R, Posselt HG, Stover B, Hofmann D, Bender SW. A double-blind placebo controlled trial with oral ambroxol and N-acetylcysteine for mucolytic treatment in cystic fibrosis. Eur J Pediatr 1985;144:374-378.
    • (1985) Eur J Pediatr , vol.144 , pp. 374-378
    • Ratjen, F.1    Wonne, R.2    Posselt, H.G.3    Stover, B.4    Hofmann, D.5    Bender, S.W.6
  • 111
    • 84980301034 scopus 로고
    • Controlled trial of oral N-acetylcysteine in cystic fibrosis
    • Mitchell EA, Elliott RB. Controlled trial of oral N-acetylcysteine in cystic fibrosis. Aust Paediatr J 1982;18:40-42.
    • (1982) Aust Paediatr J , vol.18 , pp. 40-42
    • Mitchell, E.A.1    Elliott, R.B.2


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.