Mouse models for Aicardi-Goutières syndrome provide clues to the molecular pathogenesis of systemic autoimmunity

Clinical and Experimental Immunology

Volumn 175, Issue 1, 2014, Pages 9-16

  Behrendt, R ^a   Roers, A ^a  

^a DRESDEN UNIVERSITY OF TECHNOLOGY   (Germany)

Author keywords

Aicardi Gouti res syndrome; Interferon; Nucleic acid sensing; SLE

Indexed keywords

ADENOSINE DEAMINASE; ADENOSINE DEAMINASE ACTING ON RNA 1; ESTERASE; EXONUCLEASE; GENOMIC DNA; HD DOMAIN CONTAINING PROTEIN 1; INTERFERON; INTERFERON REGULATORY FACTOR 3; MAMMALIAN TARGET OF RAPAMYCIN COMPLEX 1; NUCLEIC ACID; PROTEIN; RIBONUCLEASE H2; THREE PRIME REPAIR EXONUCLEASE 1; UNCLASSIFIED DRUG;

AICARDI GOUTIERES SYNDROME; ARTICLE; AUTOIMMUNITY; BIOACCUMULATION; CYTOKINE RESPONSE; DNA DAMAGE; GENE INDUCTION; GENE MUTATION; GENOMIC INSTABILITY; HUMAN; HUMAN IMMUNODEFICIENCY VIRUS 1; MOLECULAR PATHOLOGY; MOUSE MODEL; MOUSE MUTANT; NONHUMAN; NUCLEIC ACID METABOLISM; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEPLETION; RNA EDITING; SYSTEMIC LUPUS ERYTHEMATOSUS; VIRUS REPLICATION;

AICARDI-GOUTIÈRES SYNDROME; INTERFERON; NUCLEIC ACID SENSING; SLE;

ANIMALS; AUTOIMMUNE DISEASES OF THE NERVOUS SYSTEM; AUTOIMMUNITY; DISEASE MODELS, ANIMAL; GENE TARGETING; HUMANS; INTERFERON TYPE I; LUPUS ERYTHEMATOSUS, SYSTEMIC; MICE; MICE, MUTANT STRAINS; NERVOUS SYSTEM MALFORMATIONS;

EID: 84884284893     PISSN: 00099104     EISSN: 13652249     Source Type: Journal    
DOI: 10.1111/cei.12147     Document Type: Article

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