Disruption of brain redox homeostasis in glutaryl-CoA dehydrogenase deficient mice treated with high dietary lysine supplementation

Molecular Genetics and Metabolism

Volumn 108, Issue 1, 2013, Pages 30-39

  Seminotti, Bianca ^a   Amaral, Alexandre Umpierrez ^a   da Rosa, Mateus Struecker ^a   Fernandes, Carolina Gonçalves ^a   Leipnitz, Guilhian ^a   Olivera Bravo, Silvia ^b   Barbeito, Luis ^b   Ribeiro, César Augusto J ^a   de Souza, Diogo Onofre Gomes ^a   Woontner, Michael ^c   Goodman, Stephen I ^c   Koeller, David M ^d   Wajner, Moacir ^a,e  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^b INSTITUTO DE INVESTIGACIONES BIOLÓGICAS CLEMENTE ESTABLE   (Uruguay)

^c UNIVERSITY OF COLORADO SCHOOL OF MEDICINE   (United States)

^d OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

^e HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

Author keywords

Gcdh mice; Glutaric acid; Glutaric acidemia type I; High lysine diet; Oxidative stress

Indexed keywords

DICHLOROFLUORESCEIN; GLUTARYL COENZYME A DEHYDROGENASE; GLUTATHIONE; LYSINE; MALONALDEHYDE;

ANIMAL EXPERIMENT; ARTICLE; BRAIN CORTEX; BRAIN REDOX HOMEOSTASIS; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; CORPUS STRIATUM; DIET SUPPLEMENTATION; ENZYME ACTIVITY; HEART; HIPPOCAMPUS; HISTOPATHOLOGY; HOMEOSTASIS; LIPID OXIDATION; LIVER; MOUSE; NONHUMAN; OXIDATIVE STRESS; PRIORITY JOURNAL;

ANIMALS; BRAIN; DIETARY SUPPLEMENTS; GLUTARYL-COA DEHYDROGENASE; HOMEOSTASIS; LYSINE; MICE; MICE, KNOCKOUT; OXIDATION-REDUCTION; OXIDATIVE STRESS; THIOBARBITURIC ACID REACTIVE SUBSTANCES;

ANIMALIA; MUS;

EID: 84871713394     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2012.11.001     Document Type: Article

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