Induction of oxidative stress in brain of glutaryl-CoA dehydrogenase deficient mice by acute lysine administration

Molecular Genetics and Metabolism

Volumn 106, Issue 1, 2012, Pages 31-38

  Seminotti, Bianca ^a   da Rosa, Mateus Struecker ^a   Fernandes, Carolina Gonçalves ^a   Amaral, Alexandre Umpierrez ^a   Braga, Luisa Macedo ^b   Leipnitz, Guilhian ^a   de Souza, Diogo Onofre Gomes ^a   Woontner, Michael ^c   Koeller, David M ^d,e   Goodman, Stephen ^c   Wajner, Moacir ^a,f  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^b Fundacao Estadual de Producao e Pesquisa em Saude   (Brazil)

^c UNIVERSITY OF COLORADO SCHOOL OF MEDICINE   (United States)

^d OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

^e OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

^f HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

Author keywords

3 Hydroxyglutaric acid; Gcdh mice; Glutaric acid; Glutaric acidemia type I; Oxidative stress

Indexed keywords

2 OXOGLUTARIC ACID; CATALASE; DICHLOROFLUORESCEIN; GLUCOSE 6 PHOSPHATE DEHYDROGENASE; GLUTARIC ACID; GLUTARYL COENZYME A DEHYDROGENASE; GLUTATHIONE; GLUTATHIONE PEROXIDASE; GLUTATHIONE REDUCTASE; LYSINE; SUPEROXIDE DISMUTASE; THIOBARBITURIC ACID; THIOL DERIVATIVE;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN; BRAIN CORTEX; BRAIN DAMAGE; CONTROLLED STUDY; CORPUS STRIATUM; ENZYME ACTIVITY; HEART; HIPPOCAMPUS; LIPID PEROXIDATION; LIVER; MALE; MOUSE; NONHUMAN; OXIDATION; OXIDATIVE STRESS; PRIORITY JOURNAL;

ANIMALS; ANTIOXIDANTS; BRAIN; GLUTARYL-COA DEHYDROGENASE; LIPID PEROXIDATION; LIVER; LYSINE; MICE; MICE, TRANSGENIC; MYOCARDIUM; OXIDATIVE STRESS; TISSUE DISTRIBUTION;

ANIMALIA; MUS;

EID: 84860198994     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2012.03.002     Document Type: Article

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