A diet-induced mouse model for glutaric aciduria type I

Brain

Volumn 129, Issue 4, 2006, Pages 899-910

  Zinnanti, William J ^a   Lazovic, Jelena ^a   Wolpert, Ellen B ^a   Antonetti, David A ^a   Smith, Michael B ^a   Connor, James R ^a   Woontner, Michael ^c   Goodman, Stephen I ^c   Cheng, Keith C ^b  

^a PENN STATE COLLEGE OF MEDICINE   (United States)

^b PENN STATE CANCER INSTITUTE   (United States)

^c UNIVERSITY OF COLORADO   (United States)

Author keywords

Animal model; Blood brain barrier; Encephalopathy; Striatum; Subarachnoid haemorrhage

Indexed keywords

GLUTARIC ACID; GLUTARYL COENZYME A DEHYDROGENASE; LYSINE; PROTEIN;

ABNORMALLY HIGH SUBSTRATE CONCENTRATION IN BLOOD; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ASTROCYTOSIS; AUTOSOMAL RECESSIVE DISORDER; BLEEDING; BLOOD BRAIN BARRIER; BLOOD LEVEL; BRAIN DAMAGE; CELL LOSS; CONTROLLED STUDY; CORPUS STRIATUM; DEATH; DIETARY INTAKE; DISEASE ASSOCIATION; DISEASE MODEL; EDEMA; GLUTARIC ACIDURIA TYPE 1; LETHALITY; MOUSE; NERVE CELL; NONHUMAN; PARALYSIS; PRIORITY JOURNAL; PROTEIN DIET; PROTEIN INTAKE; SEIZURE; TISSUE LEVEL; WHITE MATTER;

AMINO ACID METABOLISM, INBORN ERRORS; ANIMALS; BLOOD-BRAIN BARRIER; CAPILLARY PERMEABILITY; CORPUS STRIATUM; DIET; DIETARY PROTEINS; DISEASE MODELS, ANIMAL; FEMALE; GLUTARATES; LYSINE; MAGNETIC RESONANCE IMAGING; MALE; MICE; MICE, INBRED C57BL; NEURONS; SURVIVAL ANALYSIS; TISSUE CULTURE TECHNIQUES;

EID: 33645087918     PISSN: 00068950     EISSN: 14602156     Source Type: Journal    
DOI: 10.1093/brain/awl009     Document Type: Article

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