Correction of both NBD1 energetics and domain interface is required to restore Δf508 CFTR folding and function

Cell

Volumn 148, Issue 1-2, 2012, Pages 150-163

  Rabeh, Wael M ^a,c   Bossard, Florian ^a   Xu, Haijin ^a   Okiyoneda, Tsukasa ^a   Bagdany, Miklos ^a   Mulvihill, Cory M ^a   Du, Kai ^a   Di Bernardo, Salvatore ^a   Liu, Yuhong ^b   Konermann, Lars ^b   Roldan, Ariel ^a   Lukacs, Gergely L ^a  

^a MCGILL UNIVERSITY   (Canada)

^b UNIVERSITY OF WESTERN ONTARIO   (Canada)

^c NEW YORK UNIVERSITY ABU DHABI   (United Arab Emirates)

Author keywords

[No Author keywords available]

Indexed keywords

TRANSMEMBRANE CONDUCTANCE REGULATOR;

ARTICLE; BIOGENESIS; CONTROLLED STUDY; ENERGY TRANSFER; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN ASSEMBLY; PROTEIN DOMAIN; PROTEIN FOLDING; PROTEIN FUNCTION; PROTEIN PROCESSING; PROTEIN SYNTHESIS; PROTEIN TRANSPORT; THERMODYNAMICS;

EID: 84862908028     PISSN: 00928674     EISSN: 10974172     Source Type: Journal    
DOI: 10.1016/j.cell.2011.11.024     Document Type: Article

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