Restoration of domain folding and interdomain assembly by second-site suppressors of the ΔF508 mutation in CFTR

FASEB Journal

Volumn 24, Issue 8, 2010, Pages 3103-3112

  He, Lihua ^a   Aleksandrov, Luba A ^a   Cui, Liying ^a   Jensen, Timothy J ^a   Nesbitt, Kenneth L ^a   Riordan, John R ^a  

^a UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

Author keywords

Cysteine accessibility; Cysteine cross linking; Cystic fibrosis; Interdomain interactions

Indexed keywords

MUTANT PROTEIN; TRANSMEMBRANE CONDUCTANCE REGULATOR; TUMOR SUPPRESSOR PROTEIN;

ANIMAL CELL; ARTICLE; BIOSYNTHESIS; CARBOXY TERMINAL SEQUENCE; CELL STRAIN HEK293; CONFORMATIONAL TRANSITION; CYTOPLASM; EMBRYO; GENE MUTATION; HUMAN; HUMAN CELL; NONHUMAN; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN CONFORMATION; PROTEIN DOMAIN; PROTEIN EXPRESSION; PROTEIN FOLDING; PROTEIN INTERACTION; PROTEIN PROCESSING;

CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; HUMANS; PROTEIN CONFORMATION; PROTEIN FOLDING; SEQUENCE DELETION;

EID: 77954983869     PISSN: 08926638     EISSN: 15306860     Source Type: Journal    
DOI: 10.1096/fj.09-141788     Document Type: Article

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