Hutchinson-Gilford progeria syndrome, cardiovascular disease and oxidative stress

Frontiers in Bioscience - Scholar

Volumn 3 S, Issue 4, 2011, Pages 1285-1297

  Trigueros Motos, Laia ^a   Gonzalez, Jose M ^a,b   Rivera, Jose ^a   Andres, Vicente ^a  

^a Laboratory of Molecular and Genetic Cardiovascular Pathophysiology   (Spain)

^b INSTITUTO DE BIOMEDICINA DE VALENCIA   (Spain)

Author keywords

A type lamins; Cardiovascular disease; Farnesyl transferase inhibitors; Hutchinson Gilford progeria syndrome; Laminopathies; Nuclear envelope; Oxidative stress; Reactive oxygen species; Restrictive dermopathy; Review

Indexed keywords

ADIPONECTIN; C REACTIVE PROTEIN; CHOLESTEROL; COLLAGEN; COLLAGEN FIBRIL; HIGH DENSITY LIPOPROTEIN CHOLESTEROL; LAMIN A; LONAFARNIB; N [[5 [(2 AMINO 3 MERCAPTOPROPYL)AMINO][1,1' BIPHENYL] 2 YL]CARBONYL]METHIONINE METHYL ESTER; PHOSPHORUS; PRAVASTATIN; PROTEOGLYCAN; SCH 6636; TRIACYLGLYCEROL; UNCLASSIFIED DRUG; ZOLEDRONIC ACID; BISPHOSPHONIC ACID DERIVATIVE; LMNA PROTEIN, HUMAN; MEMBRANE PROTEIN; METALLOPROTEINASE; NUCLEAR PROTEIN; OLIGONUCLEOTIDE; PRELAMIN A; PROTEIN PRECURSOR; TERPENE; ZMPSTE24 PROTEIN, MOUSE;

AGING; ALOPECIA; APOPTOSIS; ARTERIOSCLEROSIS; ATHEROSCLEROSIS; AUTOPHAGY; BONE MARROW TRANSPLANTATION; BRAIN INFARCTION; CARDIOVASCULAR DISEASE; CARDIOVASCULAR RISK; CELL AGING; CEREBROVASCULAR ACCIDENT; CODON; CYANOSIS; DNA REPAIR; ELECTROCARDIOGRAPHY; ENDOTHELIUM CELL; FAILURE TO THRIVE; GENE MUTATION; GROWTH RETARDATION; HEART INFARCTION; HEART LEFT VENTRICLE HYPERTROPHY; HISTONE MODIFICATION; HUMAN; JOINT CONTRACTURE; MUSCLE WEAKNESS; NONHUMAN; NUCLEIC ACID BASE SUBSTITUTION; OXIDATIVE STRESS; PHOSPHATE BLOOD LEVEL; PROGERIA; PROTHROMBIN TIME; REVIEW; SCLERODERMA; SKELETON MALFORMATION; THROMBOCYTE COUNT; TOOTH MALFORMATION; ALTERNATIVE RNA SPLICING; ANIMAL; BIOSYNTHESIS; GENE THERAPY; GENETICS; METABOLISM; METHODOLOGY; MOUSE; MOUSE MUTANT; PATHOPHYSIOLOGY; PHYSIOLOGY;

ANIMALIA; MAMMALIA;

AGING; ALTERNATIVE SPLICING; ANIMALS; CARDIOVASCULAR DISEASES; CHOLESTEROL; DIPHOSPHONATES; GENE THERAPY; HUMANS; LAMIN TYPE A; MEMBRANE PROTEINS; METALLOENDOPEPTIDASES; MICE; MICE, KNOCKOUT; NUCLEAR PROTEINS; OLIGONUCLEOTIDES; OXIDATIVE STRESS; PROGERIA; PROTEIN PRECURSORS; TERPENES;

EID: 80053113014     PISSN: 19450516     EISSN: 19450524     Source Type: Journal    
DOI: None     Document Type: Review

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