Fatal pulmonary hypertension associated with an atypical case of Hunchinson-Gilford progeria

Pediatric Cardiology

Volumn 22, Issue 6, 2001, Pages 530-533

  Shiraishi, I ^a   Hayashi, S ^a   Hirai, E ^a   Onouchi, Z ^a   Hamaoka, K ^a  

^a KYOTO PREFECTURAL UNIVERSITY OF MEDICINE   (Japan)

Author keywords

Atherosclerosis; Collagen; Extracellular matrix

Indexed keywords

COLLAGEN;

ADOLESCENT; ARTERIOLE; ARTERY INTIMA; ARTICLE; ATHEROSCLEROSIS; CASE REPORT; CLINICAL FEATURE; CORONARY ARTERY; DISEASE ASSOCIATION; DISEASE COURSE; ELASTIC FIBER; GROWTH RETARDATION; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; MALE; PROGERIA; PULMONARY ARTERY; PULMONARY HYPERTENSION;

CHILD; FATAL OUTCOME; HUMANS; HYPERTENSION, PULMONARY; MALE; PROGERIA;

EID: 0035209320     PISSN: 01720643     EISSN: None     Source Type: Journal    
DOI: 10.1007/s002460010292     Document Type: Article

References (12)

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3. Active collagen synthesis by pulmonary arteries in human primary hypertension
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5. The Hunchinson-Gilford progeria syndrome. Report of 4 cases and review of the literature
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8. Patient with unusual Hunchinson-Gilford syndrome (progeria)
9. Elastin structure, bio-synthesis, and relation to disease states
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11. Reduced DNA repair in progeria cells and effects of γ-ray irradiation on UV-induced unscheduled DNA synthesis in normal and progeria cells