Polycystic kidney disease: The complexity of planar cell polarity and signaling during tissue regeneration and cyst formation

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1812, Issue 10, 2011, Pages 1249-1255

  Happé, Hester ^a   de Heer, Emile ^a   Peters, Dorien J M ^a  

^a LEIDEN UNIVERSITY MEDICAL CENTER   (Netherlands)

Author keywords

ADPKD; Hippo signaling; Planar cell polarity; Polycystic kidney disease; Renal development; Renal epithelial regeneration

Indexed keywords

CYCLIC AMP; EPIDERMAL GROWTH FACTOR RECEPTOR 4; FIBROCYSTIN; GUANINE NUCLEOTIDE BINDING PROTEIN; IMMUNOGLOBULIN ENHANCER BINDING PROTEIN; JANUS KINASE 2; MAMMALIAN TARGET OF RAPAMYCIN; MITOGEN ACTIVATED PROTEIN KINASE; PHOSPHATIDYLINOSITOL 3 KINASE; POLYCYSTIN 1; POLYCYSTIN 2; PROTEIN P73; RAF PROTEIN; RAS PROTEIN; SMAD PROTEIN; STAT1 PROTEIN; STAT3 PROTEIN; TRANSCRIPTION FACTOR NFAT; TRANSCRIPTION FACTOR RUNX2; TRANSFORMING GROWTH FACTOR BETA; WNT9B PROTEIN;

AORTA DISSECTING ANEURYSM; BARDET BIEDL SYNDROME; CELL DIVISION; CELL MIGRATION; CELL POLARITY; CELL PROLIFERATION; DISEASE COURSE; DROSOPHILA; DYSOSTOSIS; GENE DELETION; GENE DISRUPTION; GENE EXPRESSION; GENETICS; HUMAN; KIDNEY CYST; KIDNEY DEVELOPMENT; KIDNEY POLYCYSTIC DISEASE; LIVER CYST; MECKEL SYNDROME; NEPHRONOPHTHISIS; NONHUMAN; PANCREAS CYST; PATHOGENESIS; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; RETINA DEGENERATION; REVIEW; SIGNAL TRANSDUCTION; TISSUE REGENERATION;

ANIMALS; CELL DIVISION; CELL POLARITY; DISEASE MODELS, ANIMAL; HUMANS; KIDNEY; MICE; POLYCYSTIC KIDNEY DISEASES; POLYCYSTIC KIDNEY, AUTOSOMAL DOMINANT; REGENERATION; SIGNAL TRANSDUCTION;

EID: 80052271567     PISSN: 09254439     EISSN: 1879260X     Source Type: Journal    
DOI: 10.1016/j.bbadis.2011.05.005     Document Type: Review

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