Protein quality control mechanisms and neurodegenerative disorders: Checks, balances and deadlocks

Neuroscience Research

Volumn 68, Issue 3, 2010, Pages 159-166

  Mittal, Shuchi ^a   Ganesh, Subramaniam ^a  

^a INDIAN INSTITUTE OF TECHNOLOGY KANPUR   (India)

Author keywords

Autophagosome lysosome; Neurodegeneration; Neuronal inclusions; Protein aggregation; Ubiquitin proteasome

Indexed keywords

ALPHA SYNUCLEIN; ANDROGEN RECEPTOR; ATAXIN 1; ATAXIN 2; ATAXIN 7; ATROPHIN 1 PROTEIN; CALCIUM BINDING PROTEIN; CYSTATIN B; HUNTINGTIN; HYDROLASE; MUCOLIPIN 1; PALMITOYL PROTEIN THIOESTERASE; PALMITOYL PROTEIN THIOESTERASE 1; PARKIN; PARKIN 2; PARKIN 5; PROTEASOME; PROTEIN; SIALIDASE; SUPEROXIDE DISMUTASE; TATA BINDING PROTEIN; UBIQUITIN; UBIQUITIN B; UBIQUITIN PROTEIN LIGASE E3; UNCLASSIFIED DRUG;

ALZHEIMER DISEASE; AMYOTROPHIC LATERAL SCLEROSIS; AUTOPHAGY; CELL SURVIVAL; DEGENERATIVE DISEASE; DENTATORUBROPALLIDOLUYSIAN ATROPHY; GAIN OF FUNCTION MUTATION; GENE MUTATION; HUMAN; HUNTINGTON CHOREA; KENNEDY DISEASE; LOSS OF FUNCTION MUTATION; LYSOSOME; MOLECULAR DYNAMICS; MOLECULAR MECHANICS; MUCOLIPIDOSIS; MYOCLONUS EPILEPSY; NERVE CELL; NEURONAL CEROID LIPOFUSCINOSIS; NEUROPATHOLOGY; NEUROTOXICITY; NIEMANN PICK DISEASE; NONHUMAN; PARKINSON DISEASE; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN DEGRADATION; PROTEIN DEPLETION; PROTEIN FOLDING; PROTEIN PROTEIN INTERACTION; PROTEIN QUALITY; REVIEW; SIALIDOSIS; SIGNAL TRANSDUCTION; SPINOCEREBELLAR DEGENERATION;

BRAIN; HUMANS; NEURODEGENERATIVE DISEASES; NEURONS; PROTEASOME ENDOPEPTIDASE COMPLEX; SUPEROXIDE DISMUTASE; UBIQUITIN;

EID: 77957659886     PISSN: 01680102     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.neures.2010.08.002     Document Type: Review

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