Protein aggregation and defective RNA metabolism as mechanisms for motor neuron damage

CNS and Neurological Disorders - Drug Targets

Volumn 9, Issue 3, 2010, Pages 285-296

  Ticozzi, N ^a   Ratti, A ^a   Silani, V ^a  

^a UNIVERSITY OF MILAN   (Italy)

Author keywords

FUS; Motor neuron disease; mRNA metabolism; Proteinopathies; TDP 43

Indexed keywords

CARRIER PROTEIN; CHROMATIN MODIFYING PROTEIN 2B; DNA BINDING PROTEIN; FUSED IN SARCOMA TRANSLOCATED IN LIPOSARCOMA PROTEIN; PROGRANULIN; RNA; RNA BINDING PROTEIN; TAR DNA BINDING PROTEIN; UNCLASSIFIED DRUG; VALOSIN CONTAINING PROTEIN;

AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; CELLULAR DISTRIBUTION; CYTOPLASM; FAMILIAL DISEASE; GENE MUTATION; GENE OVEREXPRESSION; HUMAN; IMMUNOREACTIVITY; MOLECULAR INTERACTION; MOLECULAR MECHANICS; MOTONEURON; NERVE CELL LESION; NEUROPATHOLOGY; NONHUMAN; PROTEIN AGGREGATION; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN STRUCTURE; RNA METABOLISM; UBIQUITINATION;

EID: 77954372835     PISSN: 18715273     EISSN: None     Source Type: Journal    
DOI: 10.2174/187152710791292585     Document Type: Article

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