Glycosphingolipid storage leads to the enhanced degradation of the B cell receptor in Sandhoff disease mice

Journal of Inherited Metabolic Disease

Volumn 33, Issue 3, 2010, Pages 261-270

  Te Vruchte, Danielle ^a   Jeans, Aruna ^a   Platt, Frances M ^a   Sillence, Daniel John ^b  

^a UNIVERSITY OF OXFORD   (United Kingdom)

^b DE MONTFORT UNIVERSITY   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

B LYMPHOCYTE RECEPTOR; CD19 ANTIGEN; CD40 ANTIGEN; COMPLEMENT COMPONENT C3D RECEPTOR; GLYCOSPHINGOLIPID; MAJOR HISTOCOMPATIBILITY ANTIGEN CLASS 2; CHOLESTEROL; FC RECEPTOR; IMMUNOGLOBULIN M RECEPTOR; LYMPHOCYTE ANTIGEN RECEPTOR; OLIGOSACCHARIDE;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; B LYMPHOCYTE; CELL SURFACE; CONTROLLED STUDY; ENDOCYTOSIS; LIPID RAFT; LIPID STORAGE; LYMPHOBLAST; MOUSE; NONHUMAN; PROTEIN DEGRADATION; PROTEIN EXPRESSION; SANDHOFF DISEASE; ANIMAL; BAGG ALBINO MOUSE; C57BL MOUSE; CELL MEMBRANE; CHEMISTRY; CYTOLOGY; DISEASE MODEL; GENETICS; LYSOSOME; METABOLISM; TRANSGENIC MOUSE;

ANIMALS; B-LYMPHOCYTES; CHOLESTEROL; DISEASE MODELS, ANIMAL; GLYCOSPHINGOLIPIDS; LYSOSOMES; MEMBRANE MICRODOMAINS; MICE; MICE, INBRED BALB C; MICE, INBRED C57BL; MICE, TRANSGENIC; OLIGOSACCHARIDES; RECEPTORS, ANTIGEN, B-CELL; RECEPTORS, FC; SANDHOFF DISEASE;

EID: 77953231922     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-010-9109-3     Document Type: Article

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