α-Galactosidase A deficient mice: A model of fabry disease

Proceedings of the National Academy of Sciences of the United States of America

Volumn 94, Issue 6, 1997, Pages 2540-2544

  Ohshima, Toshio ^a,b   Murray, Gary J ^b   Swaim, William D ^a   Longenecker, Glenn ^a   Quirk, Jane M ^b   Cardarelli, Carol O ^c   Sugimoto, Yoshikazu ^d   Pastan, Ira ^c   Gottesman, Michael M ^c   Brady, Roscoe O ^b   Kulkarni, Ashok B ^a  

^a NATIONAL INSTITUTE OF DENTAL AND CRANIOFACIAL RESEARCH   (United States)

^b NATIONAL INSTITUTE OF NEUROLOGICAL DISORDERS AND STROKE   (United States)

^c NATIONAL CANCER INSTITUTE   (United States)

^d CANCER CHEMOTHERAPY CENTER   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA GALACTOSIDASE; CERAMIDE TRIHEXOSIDE; GLYCOSPHINGOLIPID;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL ULTRASTRUCTURE; CONTROLLED STUDY; FABRY DISEASE; GENE TARGETING; HEART INFARCTION; HISTOPATHOLOGY; KIDNEY FAILURE; LIPID ANALYSIS; MOUSE; NONHUMAN; PRIORITY JOURNAL; SIGNAL TRANSDUCTION; STROKE; VASCULAR ENDOTHELIUM;

ALPHA-GALACTOSIDASE; ANIMALS; CHIMERA; CROSSES, GENETIC; DISEASE MODELS, ANIMAL; FABRY DISEASE; FEMALE; GENE THERAPY; HUMANS; KIDNEY; LECTINS; LIVER; LYSOSOMES; MALE; MICE; MICE, KNOCKOUT; MICROSCOPY, ELECTRON; PLANT LECTINS;

ANIMALIA;

EID: 12644284502     PISSN: 00278424     EISSN: None     Source Type: Journal    
DOI: 10.1073/pnas.94.6.2540     Document Type: Article

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