Apoptosis accompanied by up-regulation of TNF-α death pathway genes in the brain of Niemann-Pick type C disease

Molecular Genetics and Metabolism

Volumn 84, Issue 1, 2005, Pages 9-17

  Wu, Yun Ping ^a,b   Mizukami, Hiroki ^b   Matsuda, Junko ^a   Saito, Yuko ^a   Proia, Richard L ^b   Suzuki, Kinuko ^a  

^a UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

^b NATIONAL INSTITUTES OF HEALTH   (United States)

Author keywords

Astrocyte; Neuronal death; Niemann Pick disease type C; TNF receptor

Indexed keywords

CASPASE 8; FAS ASSOCIATED DEATH DOMAIN PROTEIN; MESSENGER RNA; TUMOR NECROSIS FACTOR ALPHA;

ANIMAL EXPERIMENT; ANIMAL TISSUE; APOPTOSIS; ARTICLE; ASTROCYTE; AUTOSOMAL RECESSIVE INHERITANCE; BRAIN CORTEX; BRAIN REGION; CELL DEATH; CEREBELLUM CORTEX; CONTROLLED STUDY; DISEASE COURSE; ELECTRON MICROSCOPY; MOUSE; NICK END LABELING; NIEMANN PICK DISEASE; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; SPECIES COMPARISON; STORAGE DISEASE; UPREGULATION;

ANIMALS; APOPTOSIS; BRAIN; HUMANS; IN SITU NICK-END LABELING; MICE; MICE, INBRED BALB C; MICROSCOPY, ELECTRON; NEURONS; NIEMANN-PICK DISEASES; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; TUMOR NECROSIS FACTOR-ALPHA; UP-REGULATION;

MURINAE;

EID: 11444254013     PISSN: 10967192     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.ymgme.2004.08.017     Document Type: Article

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