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Journal of Cystic Fibrosis

Volumn 1, Issue 1, 2002, Pages 13-29

The cystic fibrosis transmembrane conductance regulator: An intriguing protein with pleiotropic functions

(3) Vankeerberghen, Anne a Cuppens, Harry a Cassiman, Jean Jacques a

a UNIVERSITY OF LEUVEN (Belgium)

Author keywords

CFTR mutations; Channel regulator; Chloride channel; Interacting protiens; Maturation

Indexed keywords

CHAPERONE; ELECTROLYTE; MEMBRANE PROTEIN; PROTEIN KINASE; SNARE PROTEIN; TRANSMEMBRANE CONDUCTANCE REGULATOR;

APICAL MEMBRANE; ARTICLE; ATROPHY; AUTOSOMAL RECESSIVE DISORDER; CELL MEMBRANE; CHLORIDE CHANNEL; CLINICAL RESEARCH; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; CORRELATION FUNCTION; CYSTIC FIBROSIS; CYTOSKELETON; ENVIRONMENTAL FACTOR; EPITHELIUM CELL; EXOCRINE GLAND; GENE MUTATION; GENETICS; HEREDITY; HUMAN; ION CONDUCTANCE; MEMBRANE TRANSPORT; METABOLISM; MUTATION; PATHOPHYSIOLOGY; PHENOTYPE; PHYSIOLOGY; PLEIOTROPY; PROTEIN DOMAIN; PROTEIN INTERACTION; REGULATORY MECHANISM; SECRETION; TRANSPORT AT THE CELLULAR LEVEL; VISCOSITY;

BIOLOGICAL TRANSPORT; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; ELECTROLYTES; HUMANS; MEMBRANE PROTEINS; MUTATION; PHENOTYPE; PROTEIN KINASES;

EID: 0036120193 PISSN: 15691993 EISSN: None Source Type: Journal
DOI: 10.1016/S1569-1993(01)00003-0 Document Type: Article

Times cited : (133)

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