-
1
-
-
0029024314
-
Cloning of the β cell high-affinity sulfonylurea receptor: A regulator of insulin secretion
-
Aguilar-Bryan, L., Nichols, C. G., Wechsler, S. W., Clement, J. P., Boyd, A. E., Gonzalez, G., Herrera-Sosa, H., Nguy, K., Bryan, J., and Nelson, D. A. (1995). Cloning of the β cell high-affinity sulfonylurea receptor: A regulator of insulin secretion. Science 268, 423-426.
-
(1995)
Science
, vol.268
, pp. 423-426
-
-
Aguilar-Bryan, L.1
Nichols, C.G.2
Wechsler, S.W.3
Clement, J.P.4
Boyd, A.E.5
Gonzalez, G.6
Herrera-Sosa, H.7
Nguy, K.8
Bryan, J.9
Nelson, D.A.10
-
2
-
-
0029165047
-
Chloride channels of intracellular organelles
-
Al-Awqati, Q. (1995). Chloride channels of intracellular organelles. Curr. Opin. Cell Biol. 7, 504-508.
-
(1995)
Curr. Opin. Cell Biol.
, vol.7
, pp. 504-508
-
-
Al-Awqati, Q.1
-
3
-
-
0343602237
-
Promiscuous coupling between the sulphonylurea receptor and inwardly rectifying potassium channels
-
Ämmälä, C., Moorhouse, A., Gribble, F., Ashfield, R., Proks, P., Smith, P. A., Sakura, H., Coles, B., Ashcroft, S. J. H., and Ashcroft, F. M. (1996). Promiscuous coupling between the sulphonylurea receptor and inwardly rectifying potassium channels. Nature 379,545-548.
-
(1996)
Nature
, vol.379
, pp. 545-548
-
-
Ämmälä, C.1
Moorhouse, A.2
Gribble, F.3
Ashfield, R.4
Proks, P.5
Smith, P.A.6
Sakura, H.7
Coles, B.8
Ashcroft, S.J.H.9
Ashcroft, F.M.10
-
4
-
-
0026667894
-
Regulation by ATP and ADP of CFTR chloride channels that contain mutant nucleotide-binding domains
-
Anderson, M. P., and Welsh, M. J. (1992). Regulation by ATP and ADP of CFTR chloride channels that contain mutant nucleotide-binding domains. Science 257, 1701-1704.
-
(1992)
Science
, vol.257
, pp. 1701-1704
-
-
Anderson, M.P.1
Welsh, M.J.2
-
5
-
-
0025868103
-
Demonstration that CFTR is a chloride channel by alteration of its anion selectivity
-
Anderson, M. P., Gregory, R. J., Thompson, S., Souza, D. W., Sucharita, P., Mulligan, R. C., Smith, A. E., and Welsh, M. J. (1991). Demonstration that CFTR is a chloride channel by alteration of its anion selectivity. Science 253, 202-205.
-
(1991)
Science
, vol.253
, pp. 202-205
-
-
Anderson, M.P.1
Gregory, R.J.2
Thompson, S.3
Souza, D.W.4
Sucharita, P.5
Mulligan, R.C.6
Smith, A.E.7
Welsh, M.J.8
-
6
-
-
0028346520
-
Receptor-mediated transcytosis of IgA in MDCK cells is via apical recycling endosomes
-
Apodaca, G., Katz, L. A., and Mostov, K. E. (1994). Receptor-mediated transcytosis of IgA in MDCK cells is via apical recycling endosomes. J. Cell Biol. 125, 67-86.
-
(1994)
J. Cell Biol.
, vol.125
, pp. 67-86
-
-
Apodaca, G.1
Katz, L.A.2
Mostov, K.E.3
-
7
-
-
0025604331
-
Protein kinase A regulates chloride conductance in endocytic vesicles from proximal tubule
-
Bae, H.-R., and Verkman, A. S. (1990). Protein kinase A regulates chloride conductance in endocytic vesicles from proximal tubule. Nature 348, 637-639.
-
(1990)
Nature
, vol.348
, pp. 637-639
-
-
Bae, H.-R.1
Verkman, A.S.2
-
8
-
-
0027763241
-
Defective acidification of the biosynthetic pathway in cystic fibrosis
-
Barasch, J., and Al-Awqati, Q. (1993). Defective acidification of the biosynthetic pathway in cystic fibrosis. J. Cell Sci. Suppl. 17, 229-233.
-
(1993)
J. Cell Sci. Suppl.
, vol.17
, pp. 229-233
-
-
Barasch, J.1
Al-Awqati, Q.2
-
9
-
-
0025784535
-
Defective acidification of intracellular organelles in cystic fibrosis
-
Barasch, J., Kiss, B., Prince, A., Salman, L., Gruenert, D., and Al-Awqati, Q. (1991). Defective acidification of intracellular organelles in cystic fibrosis. Nature 352, 70-73.
-
(1991)
Nature
, vol.352
, pp. 70-73
-
-
Barasch, J.1
Kiss, B.2
Prince, A.3
Salman, L.4
Gruenert, D.5
Al-Awqati, Q.6
-
10
-
-
0028009419
-
Basolateral to apical transcytosis in polarized cells is indirect and involves BFA and trimeric G protein sensitive passage through the apical endosome
-
Barroso, M., and Sztul, E. S. (1994). Basolateral to apical transcytosis in polarized cells is indirect and involves BFA and trimeric G protein sensitive passage through the apical endosome. J. Cell Biol. 124, 83-100.
-
(1994)
J. Cell Biol.
, vol.124
, pp. 83-100
-
-
Barroso, M.1
Sztul, E.S.2
-
11
-
-
0023608934
-
Biogenesis of the rat hepatocyte plasma membrane in vivo: Comparison of the pathways taken by apical and basolateral proteins using subcellular fractionation
-
Bartles, J. R., Feracci, H. M., Stieger, B., and Hubbard, A. L. (1987). Biogenesis of the rat hepatocyte plasma membrane in vivo: Comparison of the pathways taken by apical and basolateral proteins using subcellular fractionation. J. Cell Biol. 105, 1241-1251.
-
(1987)
J. Cell Biol.
, vol.105
, pp. 1241-1251
-
-
Bartles, J.R.1
Feracci, H.M.2
Stieger, B.3
Hubbard, A.L.4
-
13
-
-
0026532895
-
Purification and functional reconstitution of the cystic fibrosis transmembrane conductance regulator (CFTR)
-
Bear, C. E., Li, C., Kartner, N., Bridges, R. J., Jensen, T. J., Ramjeesingh, M., and Riordan, J. R. (1992). Purification and functional reconstitution of the cystic fibrosis transmembrane conductance regulator (CFTR). Cell 68, 809-818.
-
(1992)
Cell
, vol.68
, pp. 809-818
-
-
Bear, C.E.1
Li, C.2
Kartner, N.3
Bridges, R.J.4
Jensen, T.J.5
Ramjeesingh, M.6
Riordan, J.R.7
-
14
-
-
0028045712
-
Functional CFTR in endosomal compartment of CFTR-expressing fibroblasts and T^ cells
-
Biwersi, J., and Verkman, A. S. (1994). Functional CFTR in endosomal compartment of CFTR-expressing fibroblasts and T^ cells. Am. J. Physiol. 266, C149-C156.
-
(1994)
Am. J. Physiol.
, vol.266
-
-
Biwersi, J.1
Verkman, A.S.2
-
15
-
-
0002314552
-
Cystic fibrosis
-
C. L. Shriver, A. L. Beaudet, W. S. Sly, and D. Valles, Eds., 6th ed., McGraw-Hill, New York.
-
Boat, T. F., Welsh, M. J., and Beaudet, A. L. (1989). Cystic fibrosis. In "The Metabolic Basis of Inherited Disease" (C. L. Shriver, A. L. Beaudet, W. S. Sly, and D. Valles, Eds.), 6th ed., pp. 2649-2628. McGraw-Hill, New York.
-
(1989)
The Metabolic Basis of Inherited Disease
, pp. 2649-12628
-
-
Boat, T.F.1
Welsh, M.J.2
Beaudet, A.L.3
-
16
-
-
0022973473
-
Na+ transport in cystic fibrosis respiratory epithelia: Abnormal basal rate and response to adenylate cyclase activation
-
Boucher, R. C., Stutts, M. J., Knowles, M. R., Cantley, L., and Gatzy, J. T. (1986). Na+ transport in cystic fibrosis respiratory epithelia: Abnormal basal rate and response to adenylate cyclase activation. J. Clin. Invest. 78, 1245-1252.
-
(1986)
J. Clin. Invest.
, vol.78
, pp. 1245-1252
-
-
Boucher, R.C.1
Stutts, M.J.2
Knowles, M.R.3
Cantley, L.4
Gatzy, J.T.5
-
18
-
-
0026581842
-
Regulation of plasma membrane recycling by CFTR
-
Bradbury, N. A., Jilling, T., Berta, G., Sorscher, E., Bridges, R. J., and Kirk, K. L. (1992b). Regulation of plasma membrane recycling by CFTR. Science 256, 530-532.
-
(1992)
Science
, vol.256
, pp. 530-532
-
-
Bradbury, N.A.1
Jilling, T.2
Berta, G.3
Sorscher, E.4
Bridges, R.J.5
Kirk, K.L.6
-
19
-
-
0028322331
-
Biochemical and biophysical identification of CFTR chloride channels as components of endocytic clathrin-coated vesicles
-
Bradbury, N. A., Cohn, J. A., Venglarik, C. J., and Bridges, R. J. (1994). Biochemical and biophysical identification of CFTR chloride channels as components of endocytic clathrin-coated vesicles. J. Biol. Chem. 269, 8296-8302.
-
(1994)
J. Biol. Chem.
, vol.269
, pp. 8296-8302
-
-
Bradbury, N.A.1
Cohn, J.A.2
Venglarik, C.J.3
Bridges, R.J.4
-
20
-
-
0024437936
-
A restricted set of apical proteins recycle through the trans-Golgi network in MDCK cells
-
Brändi, A. W., and Simons, K. (1989). A restricted set of apical proteins recycle through the trans-Golgi network in MDCK cells. EMBO J. 8, 3207-3213.
-
(1989)
EMBO J.
, vol.8
, pp. 3207-3213
-
-
Brändi, A.W.1
Simons, K.2
-
21
-
-
0027748886
-
Endosomal pathways for water channel and proton pump recycling in kidney epithelial cells
-
Brown, D., and Sabolic, I. (1993). Endosomal pathways for water channel and proton pump recycling in kidney epithelial cells. J. Cell Sci. 17, 49-59.
-
(1993)
J. Cell Sci.
, vol.17
, pp. 49-59
-
-
Brown, D.1
Sabolic, I.2
-
22
-
-
0026744303
-
The small GTPase rab5 functions as a regulatory factor in the early endocytic pathway
-
Bucci, C., Parton, R. G., Mather, I. H., Stunnenberg, H., Simons, K., Hoflock, B., and Zerial, M. (1992). The small GTPase rab5 functions as a regulatory factor in the early endocytic pathway. Cell 70, 715-728.
-
(1992)
Cell
, vol.70
, pp. 715-728
-
-
Bucci, C.1
Parton, R.G.2
Mather, I.H.3
Stunnenberg, H.4
Simons, K.5
Hoflock, B.6
Zerial, M.7
-
24
-
-
0028906612
-
The two nucleotide-binding domains of cystic fibrosis transmembrane conductance regulator (CFTR) have distinct functions in controlling channel activity
-
Carson, M. R., Travis, S. M., and Welsh, M. J. (1995). The two nucleotide-binding domains of cystic fibrosis transmembrane conductance regulator (CFTR) have distinct functions in controlling channel activity. J. Biol. Chem. 270, 1711-1717.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 1711-1717
-
-
Carson, M.R.1
Travis, S.M.2
Welsh, M.J.3
-
25
-
-
0029060107
-
- channel activity compensates for defective processing in a cystic fibrosis mutant corresponding to a mild form of the disease
-
- channel activity compensates for defective processing in a cystic fibrosis mutant corresponding to a mild form of the disease. EMBO J. 14, 2417-2423.
-
(1995)
EMBO J.
, vol.14
, pp. 2417-2423
-
-
Champigny, G.1
Imler, J.-L.2
Puchelle, E.3
Dalemans, W.4
Gribkoff, V.5
Hinnrasky, J.6
Dott, K.7
Barbry, P.8
Pavirani, A.9
Lazdunski, M.10
-
26
-
-
0027311276
-
Protein kinase A (PKA) still activates CFTR chloride channel after mutagenesis of all 10 PKA consensus phosphorylation sites
-
Chang, X.-B., Tabcharani, J. A., Hou, Y.-X., Jensen, T. J., Kartner, N., Alon, N., Hanrahan, J. W., and Riordan, J. R. (1993). Protein kinase A (PKA) still activates CFTR chloride channel after mutagenesis of all 10 PKA consensus phosphorylation sites. J. Biol. Chem. 268, 11304-11311.
-
(1993)
J. Biol. Chem.
, vol.268
, pp. 11304-11311
-
-
Chang, X.-B.1
Tabcharani, J.A.2
Hou, Y.-X.3
Jensen, T.J.4
Kartner, N.5
Alon, N.6
Hanrahan, J.W.7
Riordan, J.R.8
-
27
-
-
0025242929
-
Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis
-
Cheng, S. H., Gregory, R. J., Marshall, J., Paul, S., Souza, D. W., White, G. A., O'Riordan, C. R., and Smith, A. E. (1990). Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis. Cell 63, 827-834.
-
(1990)
Cell
, vol.63
, pp. 827-834
-
-
Cheng, S.H.1
Gregory, R.J.2
Marshall, J.3
Paul, S.4
Souza, D.W.5
White, G.A.6
O'Riordan, C.R.7
Smith, A.E.8
-
28
-
-
0025987020
-
Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channel
-
Cheng, S. H., Rich, D. P., Marshall, J., Gregory, R. J., Welsh, M. J., and Smith, A. E. (1991). Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channel. Cell 66, 1027-1036.
-
(1991)
Cell
, vol.66
, pp. 1027-1036
-
-
Cheng, S.H.1
Rich, D.P.2
Marshall, J.3
Gregory, R.J.4
Welsh, M.J.5
Smith, A.E.6
-
29
-
-
0024331983
-
100-KDa polypeptides in peripheral clathrin-coated vesicles are required for receptor-mediated endocytosis
-
Chin, D. J., Straubinger, R. M., Acton, S., Näthke, I., and Brodsky, F. M. (1989). 100-KDa polypeptides in peripheral clathrin-coated vesicles are required for receptor-mediated endocytosis. Proc. Nail. Acad. Sci. USA 86, 9289-9293.
-
(1989)
Proc. Nail. Acad. Sci. USA
, vol.86
, pp. 9289-9293
-
-
Chin, D.J.1
Straubinger, R.M.2
Acton, S.3
Näthke, I.4
Brodsky, F.M.5
-
30
-
-
0026656343
-
Extensive posttranscriptional deletion of the coding sequences for part of nucleotide-binding fold 1 in respiratory epithelial mRNA transcripts of the cystic fibrosis transmembrane conductance regulator gene is not associated with the clinical manifestations of cystic fibrosis
-
Chu, C. S.,Trapnell, B. C, Curristin, S. M., Cutting, R. G., and Crystal, R. G. (1992). Extensive posttranscriptional deletion of the coding sequences for part of nucleotide-binding fold 1 in respiratory epithelial mRNA transcripts of the cystic fibrosis transmembrane conductance regulator gene is not associated with the clinical manifestations of cystic fibrosis. J. Clin. Invest. 90, 785-790.
-
(1992)
J. Clin. Invest.
, vol.90
, pp. 785-790
-
-
Chu, C.S.1
Trapnell, B.C.2
Curristin, S.M.3
Cutting, R.G.4
Crystal, R.G.5
-
31
-
-
0028018268
-
The ubiquitin-proteasome proteolytic pathway
-
Ciechanover, A. (1994). The ubiquitin-proteasome proteolytic pathway. Cell 79, 13-21.
-
(1994)
Cell
, vol.79
, pp. 13-21
-
-
Ciechanover, A.1
-
33
-
-
0026647515
-
Cyclic AMP-activated chloride channels in CFTR-transfected cystic fibrosis pancreatic epithelial cells
-
Cliff, W. H., Schoumacher, R. A., and Frizzell, R. A. (1992). Cyclic AMP-activated chloride channels in CFTR-transfected cystic fibrosis pancreatic epithelial cells. Am. J. Physiol. 262, C1154-C1160.
-
(1992)
Am. J. Physiol.
, vol.262
-
-
Cliff, W.H.1
Schoumacher, R.A.2
Frizzell, R.A.3
-
34
-
-
0026545547
-
Characterization of the cystic fibrosis transmembrane conductance regulator in a colonocyte cell line
-
Cohn, J. A., Nairn, A. C, Marino, C. R., Melhus, O., and Kole, J. (1992). Characterization of the cystic fibrosis transmembrane conductance regulator in a colonocyte cell line. Proc. Natl. Acad. Sci. USA 89, 2340-2344.
-
(1992)
Proc. Natl. Acad. Sci. USA
, vol.89
, pp. 2340-2344
-
-
Cohn, J.A.1
Nairn, A.C.2
Marino, C.R.3
Melhus, O.4
Kole, J.5
-
35
-
-
33645880531
-
Rapid internalization of CFTR is mediated by amino- And carboxy-terminal tail signals
-
[Abstract]
-
Copeland, S. J., Collawn, J. F., Davis, C. D., Marchase, R. B., and Prince, L. S. (1995). Rapid internalization of CFTR is mediated by amino- and carboxy-terminal tail signals. Pediatr. Pulinonol. Suppl. 12, 185. [Abstract]
-
(1995)
Pediatr. Pulinonol. Suppl.
, vol.12
, pp. 185
-
-
Copeland, S.J.1
Collawn, J.F.2
Davis, C.D.3
Marchase, R.B.4
Prince, L.S.5
-
36
-
-
0028878728
-
The genetic advantage hypothesis in cystic fibrosis heterozygotes: A murine study
-
Cuthbert, A. W., Halstead, J., Ratcliff, R., Colledge, W. H., and Evans, M. J. (1995). The genetic advantage hypothesis in cystic fibrosis heterozygotes: A murine study. J. Physiol. (London) 482(2), 449-454.
-
(1995)
J. Physiol. (London)
, vol.482
, Issue.2
, pp. 449-454
-
-
Cuthbert, A.W.1
Halstead, J.2
Ratcliff, R.3
Colledge, W.H.4
Evans, M.J.5
-
37
-
-
0025310336
-
A cluster of cystic fibrosis mutations in the first nucleotide-binding fold of the cystic fibrosis conductance regulator protein
-
Cutting, G. R., Kasch, L. M., Rosenstein, B. J., Zielenski, J., Tsui, L.-C, Antonarakis, S. E., and Kazozian, H. H. (1990). A cluster of cystic fibrosis mutations in the first nucleotide-binding fold of the cystic fibrosis conductance regulator protein. Nature 346, 366-369.
-
(1990)
Nature
, vol.346
, pp. 366-369
-
-
Cutting, G.R.1
Kasch, L.M.2
Rosenstein, B.J.3
Zielenski, J.4
Tsui, L.-C.5
Antonarakis, S.E.6
Kazozian, H.H.7
-
38
-
-
0026325533
-
Altered chloride ion channel kinetics associated with the ΔF508 cystic fibrosis mutation
-
Dalemans, W., Barbry, P., Champigny, G., Jallat, S., Dott, K., Dreyer, D., Crystal, R. G., Pavirani, A., Lecocq, J.-P., and Lazdunski, M. (1991). Altered chloride ion channel kinetics associated with the ΔF508 cystic fibrosis mutation. Nature 354, 526-528.
-
(1991)
Nature
, vol.354
, pp. 526-528
-
-
Dalemans, W.1
Barbry, P.2
Champigny, G.3
Jallat, S.4
Dott, K.5
Dreyer, D.6
Crystal, R.G.7
Pavirani, A.8
Lecocq, J.-P.9
Lazdunski, M.10
-
39
-
-
0028036513
-
Induction of mutant dynamin specifically blocks endocytic coated vesicle formation
-
Damke, H., Baba, T., Warnock, D. E., and Schmid, S. L. (1994). Induction of mutant dynamin specifically blocks endocytic coated vesicle formation. J. Cell Biol. 127, 915-934.
-
(1994)
J. Cell Biol.
, vol.127
, pp. 915-934
-
-
Damke, H.1
Baba, T.2
Warnock, D.E.3
Schmid, S.L.4
-
40
-
-
0027179841
-
Receptor and protein kinase C-mediated regulation of ARF binding to the Golgi complex
-
De-Matteis, M. A., Santini, G., Kahn, R. A., Di-Tullio, G., and Luini, A. (1993). Receptor and protein kinase C-mediated regulation of ARF binding to the Golgi complex. Nature 364, 818-821.
-
(1993)
Nature
, vol.364
, pp. 818-821
-
-
De-Matteis, M.A.1
Santini, G.2
Kahn, R.A.3
Di-Tullio, G.4
Luini, A.5
-
41
-
-
0026547330
-
Localization of cystic fibrosis transmembrane conductance regulator in chloride secretory epithelia
-
Denning, G. M., Ostedgaard, L. S., Cheng, S. H., Smith, A. E., and Welsh, M. J. (1992a). Localization of cystic fibrosis transmembrane conductance regulator in chloride secretory epithelia. J. Clin. Invest. 89, 339-349.
-
(1992)
J. Clin. Invest.
, vol.89
, pp. 339-349
-
-
Denning, G.M.1
Ostedgaard, L.S.2
Cheng, S.H.3
Smith, A.E.4
Welsh, M.J.5
-
42
-
-
0026781952
-
Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive
-
Denning, G. M., Anderson, M. P., Amara, J. F., Marshall, J., Smith, E., and Welsh, M. J. (1992b). Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive. Nature 358, 761-764.
-
(1992)
Nature
, vol.358
, pp. 761-764
-
-
Denning, G.M.1
Anderson, M.P.2
Amara, J.F.3
Marshall, J.4
Smith, E.5
Welsh, M.J.6
-
43
-
-
33645881751
-
Plasma membrane recycling in CFTR-expressing CHO cells
-
Dho, S., Grinstein, S., and Foskett, J. K. (1993). Plasma membrane recycling in CFTR-expressing CHO cells. Nature 364, 818-821.
-
(1993)
Nature
, vol.364
, pp. 818-821
-
-
Dho, S.1
Grinstein, S.2
Foskett, J.K.3
-
44
-
-
0025820979
-
Cystic fibrosis with three mutations in the cystic fibrosis transmembrane conductance regulator gene
-
Dork, T., Wulbrand, U., Richter, T., Neumann, T., Wolfes, H., Wulf, B., Maass, G., and Tummler, B. (1991). Cystic fibrosis with three mutations in the cystic fibrosis transmembrane conductance regulator gene. Hum. Genet. 87, 441-446.
-
(1991)
Hum. Genet.
, vol.87
, pp. 441-446
-
-
Dork, T.1
Wulbrand, U.2
Richter, T.3
Neumann, T.4
Wolfes, H.5
Wulf, B.6
Maass, G.7
Tummler, B.8
-
45
-
-
0028133685
-
Heterologous expression of delta F508 CFTR results in decreased sialylation of membrane glycoconjugates
-
Dosanjh, A., Lencer, W., Brown, D., Ausiello, D. A., and Stow, J. L. (1994). Heterologous expression of delta F508 CFTR results in decreased sialylation of membrane glycoconjugates. Am. J. Physiol. 266, C360-C366.
-
(1994)
Am. J. Physiol.
, vol.266
-
-
Dosanjh, A.1
Lencer, W.2
Brown, D.3
Ausiello, D.A.4
Stow, J.L.5
-
46
-
-
0025315397
-
Antibodies to clathrin inhibit endocytosis but not recycling to the Irans Golgi network in vitro
-
Draper, R. K., Goda, Y., Brodsky, F. M., and Pfeffer, S. R. (1990). Antibodies to clathrin inhibit endocytosis but not recycling to the Irans Golgi network in vitro. Science 248, 1539-1541.
-
(1990)
Science
, vol.248
, pp. 1539-1541
-
-
Draper, R.K.1
Goda, Y.2
Brodsky, F.M.3
Pfeffer, S.R.4
-
47
-
-
0025094612
-
Correction of the cystic fibrosis defect in vitro by retrovirus-mediated gene transfer
-
Drumm, M. L., Pope, H. A., Cliff, W. H., Rommens, J. M., Marvin, S. A., Tsui, L.-C., Collins, F. S., Frizzell, R. A., and Wilson, J. M. (1990). Correction of the cystic fibrosis defect in vitro by retrovirus-mediated gene transfer. Cell 62, 1227-1233.
-
(1990)
Cell
, vol.62
, pp. 1227-1233
-
-
Drumm, M.L.1
Pope, H.A.2
Cliff, W.H.3
Rommens, J.M.4
Marvin, S.A.5
Tsui, L.-C.6
Collins, F.S.7
Frizzell, R.A.8
Wilson, J.M.9
-
48
-
-
0028111942
-
Regulation of endocytic trafficking and acidification are independent of the cystic fibrosis transmembrane regulator
-
Dunn, K. W., Park, J., Semrad, C. E., Gelman, D. L., Shevell, T., and McGraw, T. E. (1994). Regulation of endocytic trafficking and acidification are independent of the cystic fibrosis transmembrane regulator. J. Biol. Chem. 269, 5336-5345.
-
(1994)
J. Biol. Chem.
, vol.269
, pp. 5336-5345
-
-
Dunn, K.W.1
Park, J.2
Semrad, C.E.3
Gelman, D.L.4
Shevell, T.5
McGraw, T.E.6
-
49
-
-
0027256659
-
Glycan microheterogeneity of ai-antitrypsin in serum and meconium from normal and cystic fibrosis patients by crossed immunoaffinoelectrophoresis with different lectins (ConA, LCA, WGA)
-
Duthel, S., and Revol, A. (1993). Glycan microheterogeneity of ai-antitrypsin in serum and meconium from normal and cystic fibrosis patients by crossed immunoaffinoelectrophoresis with different lectins (ConA, LCA, WGA). Clin. Chim. Acta 215, 173-187.
-
(1993)
Clin. Chim. Acta
, vol.215
, pp. 173-187
-
-
Duthel, S.1
Revol, A.2
-
50
-
-
0015323554
-
Effect of cholera enterotoxin on ion transport across isolated ileal mucosa
-
Field, M., Fromm, D., Al-Awqati, Q., and Greenough, W. B. (1972). Effect of cholera enterotoxin on ion transport across isolated ileal mucosa. J. Clin. Invest. 51, 796-804.
-
(1972)
J. Clin. Invest.
, vol.51
, pp. 796-804
-
-
Field, M.1
Fromm, D.2
Al-Awqati, Q.3
Greenough, W.B.4
-
52
-
-
0027395872
-
The changing epidemiology of cystic fibrosis
-
Fitzsimmons, S. C. (1993). The changing epidemiology of cystic fibrosis. J. Pediatr. 122, 1-9.
-
(1993)
J. Pediatr.
, vol.122
, pp. 1-9
-
-
Fitzsimmons, S.C.1
-
53
-
-
0020683593
-
Mucus glycoproteins secreted by respiratory epithelial tissue from cystic fibrosis patients
-
Frates, R. J., Kaizu, T. T., and Last, J. A. (1983). Mucus glycoproteins secreted by respiratory epithelial tissue from cystic fibrosis patients. Pediatr. Res. 17, 30-34.
-
(1983)
Pediatr. Res.
, vol.17
, pp. 30-34
-
-
Frates, R.J.1
Kaizu, T.T.2
Last, J.A.3
-
54
-
-
0028784412
-
Isotype-specific activation of cystic fibrosis transmembrane conductance regulator-chloride channels by cGMP-dependent protein kinase II
-
French, P. J., Bijman, J., Edixhoven, M., Vaandrager, A. B., Schölte, B. J., Lohmann, S. M., Nairn, A. C., and deJonge, H. R. (1995). Isotype-specific activation of cystic fibrosis transmembrane conductance regulator-chloride channels by cGMP-dependent protein kinase II. J. Biol. Chem. 270, 26626-26631.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 26626-26631
-
-
French, P.J.1
Bijman, J.2
Edixhoven, M.3
Vaandrager, A.B.4
Schölte, B.J.5
Lohmann, S.M.6
Nairn, A.C.7
DeJonge, H.R.8
-
55
-
-
77957080918
-
Chloride channels in epithelial cell
-
F. Bronner, S. I. Helman, and W. Van Driessche, Eds., Academic Press, New York
-
Frizzell, R. A., and Halm, D. R. (1990). Chloride channels in epithelial cell. In "Current Topics in Membranes and Transport" (F. Bronner, S. I. Helman, and W. Van Driessche, Eds.), Vol. 37, pp. 247-282. Academic Press, New York.
-
(1990)
Current Topics in Membranes and Transport
, vol.37
, pp. 247-282
-
-
Frizzell, R.A.1
Halm, D.R.2
-
57
-
-
0023039366
-
Transferrin receptor polarity and recycling accuracy in "tight" and "leaky" strains of Madin-Darby canine kidney cells
-
Fuller, S. D., and Simons, K. (19S6). Transferrin receptor polarity and recycling accuracy in "tight" and "leaky" strains of Madin-Darby canine kidney cells. J. Cell Biol. 103, 1767-1779.
-
(1996)
J. Cell Biol.
, vol.103
, pp. 1767-1779
-
-
Fuller, S.D.1
Simons, K.2
-
58
-
-
0028969528
-
Newly synthesized transferrin receptors can be detected in the endosome before they appear on the cell surface
-
Futter, C. E., Connolly, C. N., Cutler, D. F., and Hopkins, C. R. (1995). Newly synthesized transferrin receptors can be detected in the endosome before they appear on the cell surface. J. Biol. Chem. 270, 10999-11003.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 10999-11003
-
-
Futter, C.E.1
Connolly, C.N.2
Cutler, D.F.3
Hopkins, C.R.4
-
59
-
-
0027191065
-
CFTR and outward rectifying chloride channels are distinct proteins with a regulatory relationship
-
Gabriel, S. E., Clarke, L. L., Boucher, R. C, and Stutts, M. J. (1993). CFTR and outward rectifying chloride channels are distinct proteins with a regulatory relationship. Nature 363, 263-266.
-
(1993)
Nature
, vol.363
, pp. 263-266
-
-
Gabriel, S.E.1
Clarke, L.L.2
Boucher, R.C.3
Stutts, M.J.4
-
60
-
-
0028062781
-
Cystic fibrosis heterozygote resistance to cholera toxin in the cystic fibrosis mouse model
-
Gabriel, S. E., Brigman, K. N., Koller, B. H., Boucher, R. C, and Stutts, M. J. (1994). Cystic fibrosis heterozygote resistance to cholera toxin in the cystic fibrosis mouse model. Science 266, 107-109.
-
(1994)
Science
, vol.266
, pp. 107-109
-
-
Gabriel, S.E.1
Brigman, K.N.2
Koller, B.H.3
Boucher, R.C.4
Stutts, M.J.5
-
61
-
-
0028085865
-
Quantification of low density lipoprotein and transferrin endocytic sorting in Hep2 cells using confocal microscopy
-
Ghosh, R. N., Gelman, D. L., and Maxfield, F. R. (1994). Quantification of low density lipoprotein and transferrin endocytic sorting in Hep2 cells using confocal microscopy. J. Cell Sci. 107, 2177-2189.
-
(1994)
J. Cell Sci.
, vol.107
, pp. 2177-2189
-
-
Ghosh, R.N.1
Gelman, D.L.2
Maxfield, F.R.3
-
62
-
-
9244225677
-
Test for concentration of electrolytes in sweat in cystic fibrosis of the pancreas utilizing pilocarpine by iontophoresis
-
Gibson, L. E., and Cooke, R. E. (1959). Test for concentration of electrolytes in sweat in cystic fibrosis of the pancreas utilizing pilocarpine by iontophoresis. Pediatrics 23, 545.
-
(1959)
Pediatrics
, vol.23
, pp. 545
-
-
Gibson, L.E.1
Cooke, R.E.2
-
63
-
-
0023782863
-
Secretin-regulated chloride channel on the apical plasma membrane of pancreatic duct cells
-
Gray, M. A., Greenwell, J. R., and Argent, B. E. (1988). Secretin-regulated chloride channel on the apical plasma membrane of pancreatic duct cells. J. Membr. Biol. 105, 131-142.
-
(1988)
J. Membr. Biol.
, vol.105
, pp. 131-142
-
-
Gray, M.A.1
Greenwell, J.R.2
Argent, B.E.3
-
64
-
-
0028047688
-
CFTR and calcium-activated chloride currents in pancreatic duct cells of a transgenic CF mouse
-
Gray, M. A., Winpenny, J. P., Porteous, D. J., Dorin, J. R., and Argent, B. E. (1994). CFTR and calcium-activated chloride currents in pancreatic duct cells of a transgenic CF mouse. Am. J. Physiol. 266, C213-C221.
-
(1994)
Am. J. Physiol.
, vol.266
-
-
Gray, M.A.1
Winpenny, J.P.2
Porteous, D.J.3
Dorin, J.R.4
Argent, B.E.5
-
66
-
-
0028208810
-
Gates of Janus: Cystic fibrosis and diarrhea
-
Guggino, S. E. (1994). Gates of Janus: Cystic fibrosis and diarrhea. Trends Microbiol. 2, 91-94.
-
(1994)
Trends Microbiol.
, vol.2
, pp. 91-94
-
-
Guggino, S.E.1
-
67
-
-
0029117303
-
Conformational states of CFTR associated with channel gating: The role of ATP binding and hydrolysis
-
Gunderson, K. L., and Kopito, R. R. (1995). Conformational states of CFTR associated with channel gating: The role of ATP binding and hydrolysis. Cell 82, 231-239.
-
(1995)
Cell
, vol.82
, pp. 231-239
-
-
Gunderson, K.L.1
Kopito, R.R.2
-
68
-
-
0028076031
-
Folding of VSV G protein: Sequential interaction with BiP and calnexin
-
Hammond, C., and Helenius, A. (1994). Folding of VSV G protein: Sequential interaction with BiP and calnexin. Science 266, 456-458.
-
(1994)
Science
, vol.266
, pp. 456-458
-
-
Hammond, C.1
Helenius, A.2
-
69
-
-
0026702994
-
Recombinant synthesis, purification, and nucleotide binding characteristics of the first nucleotide binding domain of the cystic fibrosis gene product
-
Hartman, J., Huang, Z., Rado, T. A., Peng, S., Jilling, T., Muccio, D. D., and Sorscher, E. J. (1992). Recombinant synthesis, purification, and nucleotide binding characteristics of the first nucleotide binding domain of the cystic fibrosis gene product. J. Bial. Chem. 267, 6455-6458.
-
(1992)
J. Bial. Chem.
, vol.267
, pp. 6455-6458
-
-
Hartman, J.1
Huang, Z.2
Rado, T.A.3
Peng, S.4
Jilling, T.5
Muccio, D.D.6
Sorscher, E.J.7
-
70
-
-
0030054178
-
Ubiquitination of a yeast plasma membrane receptor signals its ligand-stimulated endocytosis
-
Hicke, L., and Riezman, H. (1996). Ubiquitination of a yeast plasma membrane receptor signals its ligand-stimulated endocytosis. Cell 84, 277-287.
-
(1996)
Cell
, vol.84
, pp. 277-287
-
-
Hicke, L.1
Riezman, H.2
-
71
-
-
0023644827
-
Molecular characterization of the oligopeptide permease of Salmonella typhimurium
-
Hiles, I. D., Gallagher, M. P., Jamieson, D. J., and Higgins, C. F. (1987). Molecular characterization of the oligopeptide permease of Salmonella typhimurium. J. Mol. Biol. 195, 125-142.
-
(1987)
J. Mol. Biol.
, vol.195
, pp. 125-142
-
-
Hiles, I.D.1
Gallagher, M.P.2
Jamieson, D.J.3
Higgins, C.F.4
-
73
-
-
0029994529
-
Aminoglycoside antibiotics restore CFTR function by overcoming premature stop mutations
-
Howard, M., Frizzell, R. A., and Bedwell, D. M. (1996). Aminoglycoside antibiotics restore CFTR function by overcoming premature stop mutations. Nature Med. 2, 467-469.
-
(1996)
Nature Med.
, vol.2
, pp. 467-469
-
-
Howard, M.1
Frizzell, R.A.2
Bedwell, D.M.3
-
74
-
-
0025374695
-
Structural model of ATP-binding proteins associated with cystic fibrosis, multidrug resistance and bacterial transport
-
Hyde, S. C., Emsley, P., Hartshorn, M. J., Mimmack, M. M., Gileadi, U., Pearce, S. R., Gallagher, M. P., Gill, D. R., Hubbard, R. E., and Higgins, C. F. (1990). Structural model of ATP-binding proteins associated with cystic fibrosis, multidrug resistance and bacterial transport. Nature (London) 346, 362-365.
-
(1990)
Nature (London)
, vol.346
, pp. 362-365
-
-
Hyde, S.C.1
Emsley, P.2
Hartshorn, M.J.3
Mimmack, M.M.4
Gileadi, U.5
Pearce, S.R.6
Gallagher, M.P.7
Gill, D.R.8
Hubbard, R.E.9
Higgins, C.F.10
-
75
-
-
0028972501
-
KATP: An inward rectifier subunit plus the sulfonylurea receptor
-
KATP: An inward rectifier subunit plus the sulfonylurea receptor. Science 270, 1166-1170.
-
(1995)
Science
, vol.270
, pp. 1166-1170
-
-
Inagaki, N.1
Gonoi, T.2
Clement, J.P.3
Namba, N.4
Inazawa, J.5
Gonzalez, G.6
Aguilar-Bryan, L.7
Seino, S.8
Bryan, J.9
-
76
-
-
0028858161
-
Multiple proteolytic systems, including the proteasome, contribute to CFTR processing
-
Jensen, T. J., Loo, M. A., Pind, S., Williams, D. B., Goldberg, A. L., and Riordan, J. R. (1995). Multiple proteolytic systems, including the proteasome, contribute to CFTR processing. Cell 83, 129-135.
-
(1995)
Cell
, vol.83
, pp. 129-135
-
-
Jensen, T.J.1
Loo, M.A.2
Pind, S.3
Williams, D.B.4
Goldberg, A.L.5
Riordan, J.R.6
-
77
-
-
0030029836
-
Cyclic AMP and chloride-dependent regulation of the apical constitutive secretory pathway in colonie epithelial cells
-
Jilling, T., and Kirk, K. L. (1996). Cyclic AMP and chloride-dependent regulation of the apical constitutive secretory pathway in colonie epithelial cells. J. Biol. Chem. 271, 4381-4387.
-
(1996)
J. Biol. Chem.
, vol.271
, pp. 4381-4387
-
-
Jilling, T.1
Kirk, K.L.2
-
78
-
-
0025668545
-
Genetic complementation in cystic fibrosis pancreatic cells by somatic cell fusion
-
Jilling, T., Cunningham, S., Barker, P. E., Green, M. W., Frizzell, R. A., and Kirk, K. L. (1990). Genetic complementation in cystic fibrosis pancreatic cells by somatic cell fusion. Am. J. Physiol. 259, C1010-C1015.
-
(1990)
Am. J. Physiol.
, vol.259
-
-
Jilling, T.1
Cunningham, S.2
Barker, P.E.3
Green, M.W.4
Frizzell, R.A.5
Kirk, K.L.6
-
79
-
-
0028902964
-
Rat kidney papilla contains abundant synaptobrevin protein that participates in the fusion of antidiuretic hormone-regulated water channel-containing endosomes in vitro
-
Jo, I., Harris, H. W., Amendt-Raduege, A., Majewski, R. R., and Hammond, T. G. (1995). Rat kidney papilla contains abundant synaptobrevin protein that participates in the fusion of antidiuretic hormone-regulated water channel-containing endosomes in vitro. Proc. Natl. Acad. Sci. USA 92, 1876-1880.
-
(1995)
Proc. Natl. Acad. Sci. USA
, vol.92
, pp. 1876-1880
-
-
Jo, I.1
Harris, H.W.2
Amendt-Raduege, A.3
Majewski, R.R.4
Hammond, T.G.5
-
80
-
-
0026019534
-
Severity of cystic fibrosis in patients homozygous and heterozygous for ΔF508 mutation
-
Johansen, H. K., Nir, M., Hoiby, N., Koch, C., and Schwartz, M. (1991). Severity of cystic fibrosis in patients homozygous and heterozygous for ΔF508 mutation. Lancet 337,631-634.
-
(1991)
Lancet
, vol.337
, pp. 631-634
-
-
Johansen, H.K.1
Nir, M.2
Hoiby, N.3
Koch, C.4
Schwartz, M.5
-
81
-
-
0024597862
-
Dye-coupling compartments in the human exocrine sweat gland
-
Jones, C. J., and Quinten, P. M. (1989). Dye-coupling compartments in the human exocrine sweat gland. Am. J. Physiol. 256, C478-C485.
-
(1989)
Am. J. Physiol.
, vol.256
-
-
Jones, C.J.1
Quinten, P.M.2
-
82
-
-
0027240379
-
A cytosolic complex of p62 and rab6 associates with TGN 38/41 and is involved in budding of exocytic vesicles from the trans-Golgi network
-
Jones, S. M., Crosby, J. R., Salamero, J., and Howell, K. E. (1993). A cytosolic complex of p62 and rab6 associates with TGN 38/41 and is involved in budding of exocytic vesicles from the trans-Golgi network. J. Cell Dial. 122, 775-788.
-
(1993)
J. Cell Dial.
, vol.122
, pp. 775-788
-
-
Jones, S.M.1
Crosby, J.R.2
Salamero, J.3
Howell, K.E.4
-
83
-
-
0028899752
-
Cystic fibrosis transmembrane conductance regulator is required for protein kinase A activation of an outwardly rectified anion channel purified from bovine tracheal epithelia
-
Jovov, B., Ismailov, I.I., and Benos, D. J. (1995a). Cystic fibrosis transmembrane conductance regulator is required for protein kinase A activation of an outwardly rectified anion channel purified from bovine tracheal epithelia. J. Biol. Chem. 270, 1521-1528.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 1521-1528
-
-
Jovov, B.1
Ismailov, I.I.2
Benos, D.J.3
-
84
-
-
0028810639
-
Interaction between cystic fibrosis transmembrane conductance regulator and outwardly rectified chloride channels
-
Jovov, B., Ismailov, I. I., Berdiev, B. K., Fuller, C. M., Sorscher, E. J., Dedman, J. R., Kaetzel, M. A., and Benos, D. J. (1995b). Interaction between cystic fibrosis transmembrane conductance regulator and outwardly rectified chloride channels. J. Biol. Cliein. 270, 29194-29200.
-
(1995)
J. Biol. Cliein.
, vol.270
, pp. 29194-29200
-
-
Jovov, B.1
Ismailov, I.I.2
Berdiev, B.K.3
Fuller, C.M.4
Sorscher, E.J.5
Dedman, J.R.6
Kaetzel, M.A.7
Benos, D.J.8
-
85
-
-
0026907529
-
Mislocalization of ΔF508 CFTR in cystic fibrosis sweat gland
-
Kartner, N., Augustinas, O., Jensen, T. J., Naismith, A. L., and Riordan, J. R. (1992). Mislocalization of ΔF508 CFTR in cystic fibrosis sweat gland. Nature Genet. 1, 321-327.
-
(1992)
Nature Genet.
, vol.1
, pp. 321-327
-
-
Kartner, N.1
Augustinas, O.2
Jensen, T.J.3
Naismith, A.L.4
Riordan, J.R.5
-
86
-
-
0024423668
-
Identification of the cystic fibrosis gene: Genetic analysis
-
Kerem, B., Rommens, J. M., Buchanan, J. A., Markiewicz, T., Cox, K., Chakravarti, A., Buchwald, M., and Tsui, T. C. (1989). Identification of the cystic fibrosis gene: Genetic analysis. Science 245, 1073-1080.
-
(1989)
Science
, vol.245
, pp. 1073-1080
-
-
Kerem, B.1
Rommens, J.M.2
Buchanan, J.A.3
Markiewicz, T.4
Cox, K.5
Chakravarti, A.6
Buchwald, M.7
Tsui, T.C.8
-
87
-
-
0025133518
-
Identification of mutations in regions corresponding to the two putative nucleotide (ATP)-binding folds of the cystic fibrosis gene
-
Kerem, B. S., Zielenski, J., Markiewicz, D., Bozen, D., Gazit, E., Yahar, J., Kennedy, D., Riordan, J. R., Collins, F. S., Rommens, J. M., et al. (1990). Identification of mutations in regions corresponding to the two putative nucleotide (ATP)-binding folds of the cystic fibrosis gene. Proc. Natl. Acad. Sci. USA 87, 8447-8451.
-
(1990)
Proc. Natl. Acad. Sci. USA
, vol.87
, pp. 8447-8451
-
-
Kerem, B.S.1
Zielenski, J.2
Markiewicz, D.3
Bozen, D.4
Gazit, E.5
Yahar, J.6
Kennedy, D.7
Riordan, J.R.8
Collins, F.S.9
Rommens, J.M.10
-
88
-
-
0028914085
-
Early pulmonary inflammation in infants with cystic fibrosis
-
Khan, T. Z., Wagener, J. S., Bost, T., Martinez, J., Accurso, F. J., and Riches, D. W. (1995). Early pulmonary inflammation in infants with cystic fibrosis. Am. J. Respir. Crit. Care Med. 151, 1075-1082.
-
(1995)
Am. J. Respir. Crit. Care Med.
, vol.151
, pp. 1075-1082
-
-
Khan, T.Z.1
Wagener, J.S.2
Bost, T.3
Martinez, J.4
Accurso, F.J.5
Riches, D.W.6
-
89
-
-
0029113976
-
The first nucleotide binding fold of the cystic fibrosis transmembrane conductance regulator can function as an active ATPase
-
Ko, Y. H., and Pedersen, P. L. (1995). The first nucleotide binding fold of the cystic fibrosis transmembrane conductance regulator can function as an active ATPase. J. Biol. Chem. 270, 22093-22096.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 22093-22096
-
-
Ko, Y.H.1
Pedersen, P.L.2
-
90
-
-
0028914667
-
Effect of high-doseibuprofen in patients with cystic fibrosis
-
Konstan, M. W., Byard, P. J., Hoppel, C. L., and Davis, P. B. (1995). Effect of high-doseibuprofen in patients with cystic fibrosis. N. Engl. J. Med. 332, 848-854.
-
(1995)
N. Engl. J. Med.
, vol.332
, pp. 848-854
-
-
Konstan, M.W.1
Byard, P.J.2
Hoppel, C.L.3
Davis, P.B.4
-
91
-
-
0029065704
-
Phospholipase D is present on Golgi-enriched membranes and its activation by ADP ribosylation factor is sensitive to brefeldin A
-
Ktistakis, N. T., Brown, H. A., Sternweis, P. C., and Roth, M. G. (1995). Phospholipase D is present on Golgi-enriched membranes and its activation by ADP ribosylation factor is sensitive to brefeldin A. Proc. Natl. Acad. Sci. USA 92, 4952-4956.
-
(1995)
Proc. Natl. Acad. Sci. USA
, vol.92
, pp. 4952-4956
-
-
Ktistakis, N.T.1
Brown, H.A.2
Sternweis, P.C.3
Roth, M.G.4
-
92
-
-
0028061411
-
Constitutive mucin secretion linked to CFTR expression
-
Kuver, R., Ramesh, N., Lau, S., Savard, C, Lee, S. P., and Osborne, W. R. (1994). Constitutive mucin secretion linked to CFTR expression. Biochein. Biophys. Res. Commun. 203,1457-1462.
-
(1994)
Biochein. Biophys. Res. Commun.
, vol.203
, pp. 1457-1462
-
-
Kuver, R.1
Ramesh, N.2
Lau, S.3
Savard, C.4
Lee, S.P.5
Osborne, W.R.6
-
93
-
-
0028136433
-
HVEM tomography of the trans Golgi network: Structural insights and identification of a lace-like vesicle coat
-
Ladinsky, M. S., Kramer, J. R., Furcinitti, P. S., Mclntosh, J. R., and Howell, K. E. (1994). HVEM tomography of the trans Golgi network: Structural insights and identification of a lace-like vesicle coat. J. Cell Biol. 127, 29-38.
-
(1994)
J. Cell Biol.
, vol.127
, pp. 29-38
-
-
Ladinsky, M.S.1
Kramer, J.R.2
Furcinitti, P.S.3
Mclntosh, J.R.4
Howell, K.E.5
-
94
-
-
0028595709
-
Involvement of microtubule motors in basolateral and apical transport in kidney cells
-
Lafont, F., Burkhardt, J. K., and Simons, K. (1994). Involvement of microtubule motors in basolateral and apical transport in kidney cells. Nature 372, 801-803.
-
(1994)
Nature
, vol.372
, pp. 801-803
-
-
Lafont, F.1
Burkhardt, J.K.2
Simons, K.3
-
95
-
-
0028871658
-
Biosynthetic transport of the asialoglycoprotein receptor H1 to the cell surface occurs via endosomes
-
Leitinger, B., Hille-Rehfeld, A., and Spiess, M. (1995). Biosynthetic transport of the asialoglycoprotein receptor H1 to the cell surface occurs via endosomes. Proc. Natl. Acad. Sci. USA 92, 10109-10113.
-
(1995)
Proc. Natl. Acad. Sci. USA
, vol.92
, pp. 10109-10113
-
-
Leitinger, B.1
Hille-Rehfeld, A.2
Spiess, M.3
-
96
-
-
0023931773
-
Cyclic AMP-dependent protein kinase opens chloride channels in normal but not cystic fibrosis airway epithelium
-
Li, M., McCann, J. D., Liedtke, C. M., Nairn, A. C, Greengard, P., and Welsh, M. J. (1988). Cyclic AMP-dependent protein kinase opens chloride channels in normal but not cystic fibrosis airway epithelium. Nature (London) 331, 358-360.
-
(1988)
Nature (London)
, vol.331
, pp. 358-360
-
-
Li, M.1
McCann, J.D.2
Liedtke, C.M.3
Nairn, A.C.4
Greengard, P.5
Welsh, M.J.6
-
97
-
-
0026777811
-
The cystic fibrosis transmembrane regulator is present and functional in endosomes
-
Lukacs, G. L., Chang, X.-B., Kartner, N., Rotstein, O. D., Riordan, J. R., and Grinstein, S. (1992). The cystic fibrosis transmembrane regulator is present and functional in endosomes. J. Biol. Chem. 267, 14568-14572.
-
(1992)
J. Biol. Chem.
, vol.267
, pp. 14568-14572
-
-
Lukacs, G.L.1
Chang, X.-B.2
Kartner, N.3
Rotstein, O.D.4
Riordan, J.R.5
Grinstein, S.6
-
98
-
-
0028559511
-
Conformational maturation of CFTR but not its mutant counterpart (ΔF508) occurs in the endoplasmic reticulum and requires ATP
-
Lukacs, G. L., Mohamed, A., Kartner, N., Chang, X.-B., Riordan, J. R., and Grinstein, S. (1994). Conformational maturation of CFTR but not its mutant counterpart (ΔF508) occurs in the endoplasmic reticulum and requires ATP. EMBO J. 13, 6076-6086.
-
(1994)
EMBO J.
, vol.13
, pp. 6076-6086
-
-
Lukacs, G.L.1
Mohamed, A.2
Kartner, N.3
Chang, X.-B.4
Riordan, J.R.5
Grinstein, S.6
-
99
-
-
0025834174
-
Localization of the cystic fibrosis transmembrane conductance regulator in pancreas
-
Marino, C. R., Matovcik, L. M., Gorelick, F. S., and Cohn, J. A. (1991). Localization of the cystic fibrosis transmembrane conductance regulator in pancreas. J. Clin. Invest. 88,712-716.
-
(1991)
J. Clin. Invest.
, vol.88
, pp. 712-716
-
-
Marino, C.R.1
Matovcik, L.M.2
Gorelick, F.S.3
Cohn, J.A.4
-
100
-
-
0024379177
-
Aminoglycoside suppression of UAG, UAA and UGA condons in Escherichia coli and human tissue culture cells
-
Martin, R., Mogg, A. E., Heywood, L. A., Nitschke, L., and Burke, J. F. (1989). Aminoglycoside suppression of UAG, UAA and UGA condons in Escherichia coli and human tissue culture cells. Mol. Gen. Generic 217, 411-418.
-
(1989)
Mol. Gen. Generic
, vol.217
, pp. 411-418
-
-
Martin, R.1
Mogg, A.E.2
Heywood, L.A.3
Nitschke, L.4
Burke, J.F.5
-
101
-
-
0025057003
-
Sorting of endogenous plasma membrane proteins occurs from two sites in cultured human intestinal epithelial cells (Caco-2)
-
Matter, K., Brauchbar, M., Bucher, K., and Hauri, H. P. (1990a). Sorting of endogenous plasma membrane proteins occurs from two sites in cultured human intestinal epithelial cells (Caco-2). Cell 60, 429-437.
-
(1990)
Cell
, vol.60
, pp. 429-437
-
-
Matter, K.1
Brauchbar, M.2
Bucher, K.3
Hauri, H.P.4
-
102
-
-
0025184423
-
Microtubule perturbation retards both the direct and indirect apical pathway but does not affect sorting of plasma membrane proteins in intestinal epithelial cells (Caco-2)
-
Matter, K., Bucher, K., and Hauri, H. P. (1990b). Microtubule perturbation retards both the direct and indirect apical pathway but does not affect sorting of plasma membrane proteins in intestinal epithelial cells (Caco-2). EMBO J. 9, 3163-3170.
-
(1990)
EMBO J.
, vol.9
, pp. 3163-3170
-
-
Matter, K.1
Bucher, K.2
Hauri, H.P.3
-
103
-
-
0027444967
-
Common signals control low density lipoprotein receptor sorting in endosomes and the Golgi complex of MDCK cells
-
Matter, K., Whitney, J. A., Yamamoto, E. M., and Mellman, I. (1993). Common signals control low density lipoprotein receptor sorting in endosomes and the Golgi complex of MDCK cells. Cell 74, 1053-1064.
-
(1993)
Cell
, vol.74
, pp. 1053-1064
-
-
Matter, K.1
Whitney, J.A.2
Yamamoto, E.M.3
Mellman, I.4
-
104
-
-
0029621143
-
CFTR gene transfer corrects defective glycoconjugate secretion in human CF epithelial tracheal cells
-
Mergey, M., Lemnaouar, M., Veissiere, D., Perricaudet, M., Gruenert, D. C., Picard, J., Capeau, J., Brahimi, H. M., and Paul, A. (1995). CFTR gene transfer corrects defective glycoconjugate secretion in human CF epithelial tracheal cells. Am. J. Physiol. 269, 1855-1864.
-
(1995)
Am. J. Physiol.
, vol.269
, pp. 1855-1864
-
-
Mergey, M.1
Lemnaouar, M.2
Veissiere, D.3
Perricaudet, M.4
Gruenert, D.C.5
Picard, J.6
Capeau, J.7
Brahimi, H.M.8
Paul, A.9
-
105
-
-
0026687360
-
- secretion in colonic epithelial cells expressing high levels of cystic fibrosis transmembrane conductance regulator
-
- secretion in colonic epithelial cells expressing high levels of cystic fibrosis transmembrane conductance regulator. J. Biol. Chem. 267, 5575-5583.
-
(1992)
J. Biol. Chem.
, vol.267
, pp. 5575-5583
-
-
Morris, A.P.1
Cunningham, S.A.2
Benos, D.J.3
Frizzell, R.A.4
-
106
-
-
0029015710
-
Structure and function of ARF proteins: Activators of cholera toxin and critical components of intracellular vesicular transport processes
-
Moss, J., and Vaughan, M. (1995). Structure and function of ARF proteins: Activators of cholera toxin and critical components of intracellular vesicular transport processes. J. Biol. Chem. 270, 12327-12330.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 12327-12330
-
-
Moss, J.1
Vaughan, M.2
-
107
-
-
0026271370
-
The polymeric immunoglobulin receptor
-
Mostov, K. (1991). The polymeric immunoglobulin receptor. Semin. Cell Biol. 2, 411-418.
-
(1991)
Semin. Cell Biol.
, vol.2
, pp. 411-418
-
-
Mostov, K.1
-
108
-
-
0029240448
-
Regulation of protein traffic in polarized epithelial cells
-
Mostov, K. E., and Cardone, M. H. (1995). Regulation of protein traffic in polarized epithelial cells. BioEssays 17, 129-138.
-
(1995)
BioEssays
, vol.17
, pp. 129-138
-
-
Mostov, K.E.1
Cardone, M.H.2
-
109
-
-
33645850213
-
Syntaxin-CFTR interactions in colonie epithelial cells
-
Naren, A., Jovov, B., Tousson, A., Bradbury, N. A., Bennett, M. K., Benos, D. J., and Kirk, K. L. (1996). Syntaxin-CFTR interactions in colonie epithelial cells. Ped. Pulmonol. (Suppl. 13) pp. 222.
-
(1996)
Ped. Pulmonol. Suppl.
, vol.13
, pp. 222
-
-
Naren, A.1
Jovov, B.2
Tousson, A.3
Bradbury, N.A.4
Bennett, M.K.5
Benos, D.J.6
Kirk, K.L.7
-
111
-
-
0028883409
-
Calnexin fails to associate with substrate proteins in glucosidase-deficient cell lines
-
Ora, A., and Helenius, A. (1995). Calnexin fails to associate with substrate proteins in glucosidase-deficient cell lines. J. Biol. Chem. 270, 26060-26062.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 26060-26062
-
-
Ora, A.1
Helenius, A.2
-
112
-
-
0028977988
-
- channel is functional when retained in endoplasmic reticulum of mammalian cells
-
- channel is functional when retained in endoplasmic reticulum of mammalian cells. J. Biol. Chem. 270, 12347-12350.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 12347-12350
-
-
Pasyk, E.A.1
Foskett, J.K.2
-
113
-
-
0028232830
-
Bicarbonate conductance and pH regulatory capability of cystic fibrosis transmembrane conductance regulator
-
Paulsen, J. H., Fischer, H., Illek, B., and Machen, T. E. (1994). Bicarbonate conductance and pH regulatory capability of cystic fibrosis transmembrane conductance regulator. Proc. Natl. Acad. Sci. USA 91, 5340-5344.
-
(1994)
Proc. Natl. Acad. Sci. USA
, vol.91
, pp. 5340-5344
-
-
Paulsen, J.H.1
Fischer, H.2
Illek, B.3
Machen, T.E.4
-
114
-
-
0030021470
-
Role of mutant CFTR in hypersusceptibility of cystic fibrosis patients to lung infections
-
Pier, G. B., Grout, M., Zaid, T. S., Olsen, J. C, Johnson, L. G., Yankaskas, J. R., and Goldberg, J. B. (1996). Role of mutant CFTR in hypersusceptibility of cystic fibrosis patients to lung infections. Science 271, 64-67.
-
(1996)
Science
, vol.271
, pp. 64-67
-
-
Pier, G.B.1
Grout, M.2
Zaid, T.S.3
Olsen, J.C.4
Johnson, L.G.5
Yankaskas, J.R.6
Goldberg, J.B.7
-
115
-
-
0028232167
-
Participation of the endoplasmic reticulum chaperone calnexin (p88, 1P90) in the biogenesis of the cystic fibrosis transmembrane conductance regulator
-
Pind, S., Riordan, J. R., and Williams, D. B. (1994). Participation of the endoplasmic reticulum chaperone calnexin (p88, 1P90) in the biogenesis of the cystic fibrosis transmembrane conductance regulator. J. Biol. Chem. 269, 12784-12788.
-
(1994)
J. Biol. Chem.
, vol.269
, pp. 12784-12788
-
-
Pind, S.1
Riordan, J.R.2
Williams, D.B.3
-
116
-
-
0025168707
-
ATP and cytosol requirements for transferrin recycling in intact and disrupted MDCK cells
-
Podbliewicz, B., and Mellman, I. (1990). ATP and cytosol requirements for transferrin recycling in intact and disrupted MDCK cells. EMBO J. 9, 3477-3487.
-
(1990)
EMBO J.
, vol.9
, pp. 3477-3487
-
-
Podbliewicz, B.1
Mellman, I.2
-
117
-
-
0028801698
-
AMP-independent regulation of CFTR by the actin cytoskeleton
-
Prat, A. G., Xiao, Y.-F., Ausiello, D. A., and Cantiello, H. F. (1995). cAMP-independent regulation of CFTR by the actin cytoskeleton. Am. J. Physiol. 268, C1552-C1561.
-
(1995)
Am. J. Physiol.
, vol.268
-
-
Prat, A.G.1
Xiao, Y.-F.2
Ausiello, D.A.3
Cantiello, H.F.4
-
119
-
-
0028236014
-
Rapid endocytosis of the cystic fibrosis transmembrane conductance regulator chloride channel
-
Prince, L. S., Workman, R. B., and Marchase, R. B. (1994). Rapid endocytosis of the cystic fibrosis transmembrane conductance regulator chloride channel. Proc. Natl. Acad. Sci. USA 91, 5192-5196.
-
(1994)
Proc. Natl. Acad. Sci. USA
, vol.91
, pp. 5192-5196
-
-
Prince, L.S.1
Workman, R.B.2
Marchase, R.B.3
-
120
-
-
0026954365
-
Differential localization of the cystic fibrosis transmembrane conductance regulator in normal and cystic fibrosis airway epithelium
-
Puchelle, E., Gaillard, D., Ploton, D., Hinnrasky, J., Fuchey, C., Boutterin, M.-C., Jacquot, J., Dreyer, D., Pavirani, A., and Dalemans, W. (1992). Differential localization of the cystic fibrosis transmembrane conductance regulator in normal and cystic fibrosis airway epithelium. Am. J. Respir. Cell Mol. Biol. 7, 485-491.
-
(1992)
Am. J. Respir. Cell Mol. Biol.
, vol.7
, pp. 485-491
-
-
Puchelle, E.1
Gaillard, D.2
Ploton, D.3
Hinnrasky, J.4
Fuchey, C.5
Boutterin, M.-C.6
Jacquot, J.7
Dreyer, D.8
Pavirani, A.9
Dalemans, W.10
-
121
-
-
0020700816
-
Chloride impermeability in cystic fibrosis
-
Quinton, P. M. (1983). Chloride impermeability in cystic fibrosis. Nature {London) 301, 421-422.
-
(1983)
Nature London
, vol.301
, pp. 421-422
-
-
Quinton, P.M.1
-
122
-
-
0028484566
-
What is good about cystic fibrosis?
-
Quinton, P. M. (1994). What is good about cystic fibrosis? Curr. Biol. 4, 742-743.
-
(1994)
Curr. Biol.
, vol.4
, pp. 742-743
-
-
Quinton, P.M.1
-
123
-
-
0021030324
-
Effect of serum from normal and cystic fibrosis subjects on mucin secretion from dispersed rat submandibular cells
-
Quissell, D. O., McDonald, R. J., Barzen, K. A., and Deisher, L. M. (1983). Effect of serum from normal and cystic fibrosis subjects on mucin secretion from dispersed rat submandibular cells. Pediatr. Res. 17, 899-902.
-
(1983)
Pediatr. Res.
, vol.17
, pp. 899-902
-
-
Quissell, D.O.1
McDonald, R.J.2
Barzen, K.A.3
Deisher, L.M.4
-
125
-
-
0028923471
-
Expression and functional properties of the second predicted nucleotide binding fold of the cystic fibrosis transmembrane conductance regulator fused to glutathione-S-transferase
-
Randak, C, Roscher, A. A., Hadorn, H.-B., AssFalg-Machleidt, I., Auerswald, E. A., and Machleidt, W. (1995). Expression and functional properties of the second predicted nucleotide binding fold of the cystic fibrosis transmembrane conductance regulator fused to glutathione-S-transferase. FEBS Lett. 363, 189-194.
-
(1995)
FEBS Lett.
, vol.363
, pp. 189-194
-
-
Randak, C.1
Roscher, A.A.2
Hadorn, H.-B.3
Assfalg-Machleidt, I.4
Auerswald, E.A.5
Machleidt, W.6
-
126
-
-
0024436699
-
Altered electrical potential profile of human reabsorptive sweat duct cells in cystic fibrosis
-
Reddy, M. M., and Quinton, P. M. (1989). Altered electrical potential profile of human reabsorptive sweat duct cells in cystic fibrosis. Am. J. Physiol. 257, C722-C726.
-
(1989)
Am. J. Physiol.
, vol.257
-
-
Reddy, M.M.1
Quinton, P.M.2
-
127
-
-
0029998981
-
Failure of the cystic fibrosis transmembrane conductance regulator to conduct ATP
-
Reddy, M. M., Quinton, P. M., Haws, C., Wine, J. J., Grygorczyk, R., Tabcharani, J. A., Hanrahan, J. W., Gunderson, K. L., and Kopito, R. R. (1996). Failure of the cystic fibrosis transmembrane conductance regulator to conduct ATP. Science 271, 1876-1879.
-
(1996)
Science
, vol.271
, pp. 1876-1879
-
-
Reddy, M.M.1
Quinton, P.M.2
Haws, C.3
Wine, J.J.4
Grygorczyk, R.5
Tabcharani, J.A.6
Hanrahan, J.W.7
Gunderson, K.L.8
Kopito, R.R.9
-
128
-
-
0027937589
-
The cystic fibrosis transmembrane conductance regulator is a dual ATP and chloride channel
-
Reisin, I. L., Prat, A. G., Abraham, E. H., Amara, J. F., Gregory, R. J., Ausiello, D. A., and Cantiello, H. F. (1994). The cystic fibrosis transmembrane conductance regulator is a dual ATP and chloride channel. J. Biol. Client. 269, 20584-20591.
-
(1994)
J. Biol. Client.
, vol.269
, pp. 20584-20591
-
-
Reisin, I.L.1
Prat, A.G.2
Abraham, E.H.3
Amara, J.F.4
Gregory, R.J.5
Ausiello, D.A.6
Cantiello, H.F.7
-
129
-
-
0025155528
-
Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells
-
Rich, D. P., Anderson, M. P., Gregory, R. J., Cheng, S. H., Paul, S., Jefferson, D. M., McCann, J. D., Klinger, K. W., Smith, A. E., and Welsh, M. J. (1990). Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells. Nature (London) 347, 358-363.
-
(1990)
Nature (London)
, vol.347
, pp. 358-363
-
-
Rich, D.P.1
Anderson, M.P.2
Gregory, R.J.3
Cheng, S.H.4
Paul, S.5
Jefferson, D.M.6
McCann, J.D.7
Klinger, K.W.8
Smith, A.E.9
Welsh, M.J.10
-
130
-
-
0025744023
-
Effect of deleting the R domain on CFTR-generated chloride channels
-
Rich, D. P., Gregory, R. J., Anderson, M. P., Manavalan, P., Smith, A. E., and Welsh, M. J. (1991). Effect of deleting the R domain on CFTR-generated chloride channels. Science 253, 205-207.
-
(1991)
Science
, vol.253
, pp. 205-207
-
-
Rich, D.P.1
Gregory, R.J.2
Anderson, M.P.3
Manavalan, P.4
Smith, A.E.5
Welsh, M.J.6
-
131
-
-
0024424270
-
Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA
-
Riordan, J. R., Rommens, J. M., Kerem, B., Alon, N., Rozmahel, R., Grzelczak, Z., Zielenski, J., Lok, S., Plavsic, N., Chou, J., Drumm, M. L., lannuzzi, M. C., Collins, F. S., and Tsui, L. C. (1989). Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA. Science 245, 1066-1072.
-
(1989)
Science
, vol.245
, pp. 1066-1072
-
-
Riordan, J.R.1
Rommens, J.M.2
Kerem, B.3
Alon, N.4
Rozmahel, R.5
Grzelczak, Z.6
Zielenski, J.7
Lok, S.8
Plavsic, N.9
Chou, J.10
Drumm, M.L.11
Lannuzzi, M.C.12
Collins, F.S.13
Tsui, L.C.14
-
132
-
-
0024453308
-
Identification of the cystic fibrosis gene: Chromosome walking and jumping
-
Rommens, J. M., lannuzzi, M. C., Kerem, B., Drumm, M. L., Melmer, G., Dean, M., Rozmahel, R., Cole, J. L., Kennedy, D., Hidaka, N., Zsiga, M., Buchwald, M., Riordan, J. R., Tsui, L. C., and Collins, F. S. (1989). Identification of the cystic fibrosis gene: Chromosome walking and jumping. Science 245, 1059-1065.
-
(1989)
Science
, vol.245
, pp. 1059-1065
-
-
Rommens, J.M.1
Lannuzzi, M.C.2
Kerem, B.3
Drumm, M.L.4
Melmer, G.5
Dean, M.6
Rozmahel, R.7
Cole, J.L.8
Kennedy, D.9
Hidaka, N.10
Zsiga, M.11
Buchwald, M.12
Riordan, J.R.13
Tsui, L.C.14
Collins, F.S.15
-
133
-
-
0028143698
-
Mechanisms of intracellular protein transport
-
Rothman, J. E. (1994). Mechanisms of intracellular protein transport. Nature 372, 55-63.
-
(1994)
Nature
, vol.372
, pp. 55-63
-
-
Rothman, J.E.1
-
134
-
-
0022466383
-
Infection in patients with cystic fibrosis
-
Rubio, T. T. (1986). Infection in patients with cystic fibrosis. Am. J. Med. 81, 73-77.
-
(1986)
Am. J. Med.
, vol.81
, pp. 73-77
-
-
Rubio, T.T.1
-
135
-
-
0021366018
-
Secretory activity of hamster tracheal explants and isolated tracheal epithelial cells and the effects of cystic fibrosis serum
-
Rudick, V. L., Woolen, M. W., and Rudick, M. J. (1984). Secretory activity of hamster tracheal explants and isolated tracheal epithelial cells and the effects of cystic fibrosis serum. J. Cell. Physiol. 118, 67-78.
-
(1984)
J. Cell. Physiol.
, vol.118
, pp. 67-78
-
-
Rudick, V.L.1
Woolen, M.W.2
Rudick, M.J.3
-
136
-
-
0028063215
-
Activation of the cystic fibrosis transmembrane regulator by cyclic AMP is not correlated with inhibition of endocytosis
-
Santos, G. F., and Reenstra, W. W. (1994). Activation of the cystic fibrosis transmembrane regulator by cyclic AMP is not correlated with inhibition of endocytosis. Biocltem. Biophys. Acta 1195, 96-102.
-
(1994)
Biocltem. Biophys. Acta
, vol.1195
, pp. 96-102
-
-
Santos, G.F.1
Reenstra, W.W.2
-
137
-
-
0030042386
-
Glycerol reverses the misfolding phenotype of the most common cystic fibrosis mutation
-
Sato, S., Ward, C. L., Krause, M. E., Wine, J. J., and Kopito, R. R. (1996). Glycerol reverses the misfolding phenotype of the most common cystic fibrosis mutation. J. Biol. Chem. 271, 635-638.
-
(1996)
J. Biol. Chem.
, vol.271
, pp. 635-638
-
-
Sato, S.1
Ward, C.L.2
Krause, M.E.3
Wine, J.J.4
Kopito, R.R.5
-
138
-
-
0023546389
-
Phosphorylation fails to activate chloride channels from cystic fibrosis airway cells
-
Schoumacher, R. A., Shoemaker, R. L., Halm, D. R., Tallant, E. A., Wallace, R. W., and Frizzell, R. A. (1987). Phosphorylation fails to activate chloride channels from cystic fibrosis airway cells. Nature (London) 330, 752-754.
-
(1987)
Nature (London)
, vol.330
, pp. 752-754
-
-
Schoumacher, R.A.1
Shoemaker, R.L.2
Halm, D.R.3
Tallant, E.A.4
Wallace, R.W.5
Frizzell, R.A.6
-
139
-
-
0025337617
-
A cystic fibrosis pancreatic adenocarcinoma cell line
-
Schoumacher, R. A., Ram, J., lanuzzi, M. C, Bradbury, N. A., Wallace, R. W., Hon, C. T., Kelly, D. R., Schmid, S. M., Gelder, F. B., Rado, T. A., et al. (1990). A cystic fibrosis pancreatic adenocarcinoma cell line. Proc. Natl. Acad. Sci. USA 87, 4012-4016.
-
(1990)
Proc. Natl. Acad. Sci. USA
, vol.87
, pp. 4012-4016
-
-
Schoumacher, R.A.1
Ram, J.2
Lanuzzi, M.C.3
Bradbury, N.A.4
Wallace, R.W.5
Hon, C.T.6
Kelly, D.R.7
Schmid, S.M.8
Gelder, F.B.9
Rado, T.A.10
-
140
-
-
0029837055
-
Glibenclamide blockade of CFTR chloride channels
-
Schultz, B. D., DeRoos, A. D. G., Venglarik, C. J., Singh, A. K., Frizzell, R. A., and Bridges, R. J. (1996). Glibenclamide blockade of CFTR chloride channels. Am. J. Physiol. 271 (Lung Cell Mol. Physiol. 15), L192-L200.
-
(1996)
Am. J. Physiol.
, vol.271
-
-
Schultz, B.D.1
DeRoos, A.D.G.2
Venglarik, C.J.3
Singh, A.K.4
Frizzell, R.A.5
Bridges, R.J.6
-
141
-
-
0027966771
-
Both CFTR and outwardly rectifying chloride channels contribute to cAMP-stimulated whole cell chloride currents
-
Schwiebert, E. M., Flotte, T., Cutting, G. R., and Guggino, W. B. (1994a). Both CFTR and outwardly rectifying chloride channels contribute to cAMP-stimulated whole cell chloride currents. Am. J. Physiol. 266, C1464-C1477.
-
(1994)
Am. J. Physiol.
, vol.266
-
-
Schwiebert, E.M.1
Flotte, T.2
Cutting, G.R.3
Guggino, W.B.4
-
143
-
-
0028906638
-
AMP-dependent protein kinase-mediated phosphorylation of cystic fibrosis transmembrane conductance regulator residue ser-753 and its role in channel activation
-
Seibert, F. S., Tabcharani, J. A., Chang, X.-B., Dulhanty, A. M., Mathews, C, Hanrahan, J. W., and Riordan, J. R. (1995). cAMP-dependent protein kinase-mediated phosphorylation of cystic fibrosis transmembrane conductance regulator residue ser-753 and its role in channel activation. J. Biol. Chem. 270, 2158-2162.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 2158-2162
-
-
Seibert, F.S.1
Tabcharani, J.A.2
Chang, X.-B.3
Dulhanty, A.M.4
Mathews, C.5
Hanrahan, J.W.6
Riordan, J.R.7
-
146
-
-
0028929909
-
Mechanism of dysfunction of two nucleotide binding domain mutations in cystic fibrosis transmembrane conductance regulator that are associated with pancreatic sufficiency
-
Sheppard, D. N., Ostedgaard, L. S., Winter, M. C, and Welsh, M. J. (1995). Mechanism of dysfunction of two nucleotide binding domain mutations in cystic fibrosis transmembrane conductance regulator that are associated with pancreatic sufficiency. EMBO J. 14, 876-883.
-
(1995)
EMBO J.
, vol.14
, pp. 876-883
-
-
Sheppard, D.N.1
Ostedgaard, L.S.2
Winter, M.C.3
Welsh, M.J.4
-
147
-
-
0029046143
-
Dissection of GLUT4 recycling pathway into exocytosis and endocytosis in rat adipocytes
-
Shibata, H., Suzuki, Y., Omata, W., Tanaka, S., and Kojima, I. (1995). Dissection of GLUT4 recycling pathway into exocytosis and endocytosis in rat adipocytes. J. Biol. Chem. 270, 11489-11496.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 11489-11496
-
-
Shibata, H.1
Suzuki, Y.2
Omata, W.3
Tanaka, S.4
Kojima, I.5
-
148
-
-
0025341760
-
Polarized sorting in epithelia
-
Simons, K., and Wandinger-Ness, A. (1990). Polarized sorting in epithelia. Cell 62, 207-210.
-
(1990)
Cell
, vol.62
, pp. 207-210
-
-
Simons, K.1
Wandinger-Ness, A.2
-
149
-
-
0029591506
-
+ channel
-
+ channel. Cell 83, 969-978.
-
(1995)
Cell
, vol.83
, pp. 969-978
-
-
Snyder, P.M.1
Price, M.P.2
McDonald, F.J.3
Adams, C.M.4
Volk, K.A.5
Zeiher, B.G.6
Stokes, J.B.7
Welsh, M.J.8
-
150
-
-
33645847634
-
Immunocytochemical localization of an antibody to a disulfonic stilbene-binding peptide in T84 cells
-
Sorscher, E. J., Tousson, A., Bridges, R. J., Brinkley, B. R., Benos, D. J., and Frizzell, R. A. (1988). Immunocytochemical localization of an antibody to a disulfonic stilbene-binding peptide in T84 cells. Pediatr. Pulmonol. (Suppl. 4). [Abstract]
-
(1988)
Pediatr. Pulmonol. Suppl.
, vol.4
-
-
Sorscher, E.J.1
Tousson, A.2
Bridges, R.J.3
Brinkley, B.R.4
Benos, D.J.5
Frizzell, R.A.6
-
151
-
-
0028261425
-
Inhibition of rab5 GTPase activity stimulates membrane fusion in endocytosis
-
Stenmark, H., Parton, R. G., Steele-Mortimer, O., Llitcke, A., Gruenberg, J., and Zerial, M. (1994). Inhibition of rab5 GTPase activity stimulates membrane fusion in endocytosis. EMBO J. 13, 1287-1296.
-
(1994)
EMBO J.
, vol.13
, pp. 1287-1296
-
-
Stenmark, H.1
Parton, R.G.2
Steele-Mortimer, O.3
Llitcke, A.4
Gruenberg, J.5
Zerial, M.6
-
152
-
-
0025938893
-
Cystic fibrosis gene mutation in two sisters with mild disease and normal sweat electrolyte levels
-
Strong, T. V., Smit, L. S., Turpin, S. V., Cole, J. L., Hon, C. T., Markiewicz, D., Petty, T. L., Craig, M. W., Rosenow, E. C, Tsui, L.-C, et al. (1991). Cystic fibrosis gene mutation in two sisters with mild disease and normal sweat electrolyte levels. N. Engl. J. Med. 325, 1630-1634.
-
(1991)
N. Engl. J. Med.
, vol.325
, pp. 1630-1634
-
-
Strong, T.V.1
Smit, L.S.2
Turpin, S.V.3
Cole, J.L.4
Hon, C.T.5
Markiewicz, D.6
Petty, T.L.7
Craig, M.W.8
Rosenow, E.C.9
Tsui, L.-C.10
-
153
-
-
0027310434
-
Expression of an abundant alternatively spliced form of the cystic fibrosis conductance regulator (CFTR) gene is not associated with a cAMP-activated chloride conductance
-
Strong, T. V., Wilkinson, D. J., Mansoura, M. K., Devor, D. C, Henze, K., Yang, Y., Wilson, J. M., Cohn, J. A., Dawson, D. C, Frizzell, R. A., and Collins, F. S. (1993). Expression of an abundant alternatively spliced form of the cystic fibrosis conductance regulator (CFTR) gene is not associated with a cAMP-activated chloride conductance. Hum. Mol. Genet. 2, 225-230.
-
(1993)
Hum. Mol. Genet.
, vol.2
, pp. 225-230
-
-
Strong, T.V.1
Wilkinson, D.J.2
Mansoura, M.K.3
Devor, D.C.4
Henze, K.5
Yang, Y.6
Wilson, J.M.7
Cohn, J.A.8
Dawson, D.C.9
Frizzell, R.A.10
Collins, F.S.11
-
154
-
-
0028982894
-
CFTR as a cAMP-dependent regulator of sodium channels
-
Stutts, M. J., Canessa, C. M., Olsen, J. C, Hamrick, M., Cohn, J. A., Rossier, B. C., and Boucher, R. C. (1995). CFTR as a cAMP-dependent regulator of sodium channels. Science 269, 847-850.
-
(1995)
Science
, vol.269
, pp. 847-850
-
-
Stutts, M.J.1
Canessa, C.M.2
Olsen, J.C.3
Hamrick, M.4
Cohn, J.A.5
Rossier, B.C.6
Boucher, R.C.7
-
155
-
-
0029026392
-
The synaptic vesicle cycle: A cascade of protein-protein interactions
-
Südhof, T. C. (1995). The synaptic vesicle cycle: A cascade of protein-protein interactions. Nature 375, 645-653.
-
(1995)
Nature
, vol.375
, pp. 645-653
-
-
Südhof, T.C.1
-
156
-
-
0025885376
-
Phosphorylation-regulated CP channel in CHO cells stably expressing the cystic fibrosis gene
-
Tabcharini, J. A., Chang, X.-B., Riordan, J. R., and Hanrahan, J. W. (1991). Phosphorylation-regulated CP channel in CHO cells stably expressing the cystic fibrosis gene. Nature 352, 628-631.
-
(1991)
Nature
, vol.352
, pp. 628-631
-
-
Tabcharini, J.A.1
Chang, X.-B.2
Riordan, J.R.3
Hanrahan, J.W.4
-
157
-
-
0027153083
-
Identification of revenants for the cystic fibrosis delta F508 mutation using STE6-CFTR chimeras in yeast
-
Teem, J. L., Berger, H. A., Ostedgaard, L. S., Rich, D. P., Tsui, L.-C, and Welsh, M. J. (1993). Identification of revenants for the cystic fibrosis delta F508 mutation using STE6-CFTR chimeras in yeast. Cell 73, 335-346.
-
(1993)
Cell
, vol.73
, pp. 335-346
-
-
Teem, J.L.1
Berger, H.A.2
Ostedgaard, L.S.3
Rich, D.P.4
Tsui, L.-C.5
Welsh, M.J.6
-
158
-
-
0025306539
-
Mechanism of adenylate kinase. Are the essential lysines essential?
-
Tian, G., Yan, H., Jiang, R.-T., Kishi, R, Nakazawa, A., and Tsai, M.-D. (1990). Mechanism of adenylate kinase. Are the essential lysines essential? Biochemistry 29, 4296-4304.
-
(1990)
Biochemistry
, vol.29
, pp. 4296-4304
-
-
Tian, G.1
Yan, H.2
Jiang, R.-T.3
Kishi, R.4
Nakazawa, A.5
Tsai, M.-D.6
-
159
-
-
0029060392
-
Chloride channels: A state of flux
-
Valverde, M. A., Hardy, S. P., and Sepulveda, F. V. (1995). Chloride channels: A state of flux. FASEB J. 9, 509-515.
-
(1995)
FASEB J.
, vol.9
, pp. 509-515
-
-
Valverde, M.A.1
Hardy, S.P.2
Sepulveda, F.V.3
-
160
-
-
0024110256
-
Exocytosis of vacuolar apical compartment (VAC): A cell-cell contact controlled mechanism for the establishment of the apical plasma membrane domain in epithelial cells
-
Vega-Salas, D. E., Salas, P. J. I., and Rodriguez-Boulan, E. (1988). Exocytosis of vacuolar apical compartment (VAC): A cell-cell contact controlled mechanism for the establishment of the apical plasma membrane domain in epithelial cells. J. Cell Biol. 107, 1717-1728.
-
(1988)
J. Cell Biol.
, vol.107
, pp. 1717-1728
-
-
Vega-Salas, D.E.1
Salas, P.J.I.2
Rodriguez-Boulan, E.3
-
161
-
-
0028276430
-
ATP alters current fluctuations of cystic fibrosis transmembrane conductance regulator: Evidence for a three state activation mechanism
-
Venglarik, C. J., Schultz, B. D., Frizzell, R. A., and Bridges, R. J. (1994). ATP alters current fluctuations of cystic fibrosis transmembrane conductance regulator: Evidence for a three state activation mechanism. J. Gen. Physiol. 104, 123-146.
-
(1994)
J. Gen. Physiol.
, vol.104
, pp. 123-146
-
-
Venglarik, C.J.1
Schultz, B.D.2
Frizzell, R.A.3
Bridges, R.J.4
-
163
-
-
0028840915
-
Degradation of CFTR by the ubiquitin-proteasome pathway
-
Ward, C. L., Omura, S., and Kopito, R. R. (1995). Degradation of CFTR by the ubiquitin-proteasome pathway. Cell 83, 121-127.
-
(1995)
Cell
, vol.83
, pp. 121-127
-
-
Ward, C.L.1
Omura, S.2
Kopito, R.R.3
-
164
-
-
0028932360
-
The molecular chaperone calnexin binds Glc1Man9GlcNAc2 oligosaccharide as an initial step in recognizing unfolded glycoproteins
-
Ware, F. E., Vassilakos, A., Peterson, P. A., Jackson, M. R., Lehrman, M. A., and Williams, D. B. (1995). The molecular chaperone calnexin binds Glc1Man9GlcNAc2 oligosaccharide as an initial step in recognizing unfolded glycoproteins. J. Biol. Chem. 270, 4697-4704.
-
(1995)
J. Biol. Chem.
, vol.270
, pp. 4697-4704
-
-
Ware, F.E.1
Vassilakos, A.2
Peterson, P.A.3
Jackson, M.R.4
Lehrman, M.A.5
Williams, D.B.6
-
165
-
-
0027998367
-
Subcellular localization of CFTR to endosomes in a ductal epithelium
-
Webster, P., Vanacore, L., Nairn, A. C., and Marino, C. R. (1994). Subcellular localization of CFTR to endosomes in a ductal epithelium. Am. J. Physiol. 267, C340-C348.
-
(1994)
Am. J. Physiol.
, vol.267
-
-
Webster, P.1
Vanacore, L.2
Nairn, A.C.3
Marino, C.R.4
-
166
-
-
0029182966
-
The development of gene transfer for cystic fibrosis
-
Welsh, M. J. (1995). The development of gene transfer for cystic fibrosis. Adv. Intern. Med. 40, 429-444.
-
(1995)
Adv. Intern. Med.
, vol.40
, pp. 429-444
-
-
Welsh, M.J.1
-
167
-
-
0027162649
-
Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis
-
Welsh, M. J., and Smith, A. E. (1993). Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis. Cell 73, 1251-1254.
-
(1993)
Cell
, vol.73
, pp. 1251-1254
-
-
Welsh, M.J.1
Smith, A.E.2
-
168
-
-
0030045751
-
CFTR: The nucleotide binding folds regulate the accessibility and stability of the activated state
-
Wilkinson, D. J., Mansoura, M. K., Watson, P. Y., Smith, L. S., Collins, F. S., and Dawson, D. C. (1996). CFTR: The nucleotide binding folds regulate the accessibility and stability of the activated state. J. Gen. Physiol. 107, 103-119.
-
(1996)
J. Gen. Physiol.
, vol.107
, pp. 103-119
-
-
Wilkinson, D.J.1
Mansoura, M.K.2
Watson, P.Y.3
Smith, L.S.4
Collins, F.S.5
Dawson, D.C.6
-
169
-
-
0027488993
-
The common variant of cystic fibrosis transmembrane conductance regulator is recognized by hsp70 and degraded in a pre-Golgi nonlysosomal compartment
-
Yang, Y., Janich, S., Cohn, J. A., and Wilson, J. M. (1993). The common variant of cystic fibrosis transmembrane conductance regulator is recognized by hsp70 and degraded in a pre-Golgi nonlysosomal compartment. Proc. Natl. Acad. Sci. USA 90, 9480-9484.
-
(1993)
Proc. Natl. Acad. Sci. USA
, vol.90
, pp. 9480-9484
-
-
Yang, Y.1
Janich, S.2
Cohn, J.A.3
Wilson, J.M.4
-
171
-
-
0025245612
-
Restoration of inactivation in mutants of Shaker potassium channels by a peptide derived from ShB
-
Zagotta, W. N., Hoshi, T., and Aldrich, R. W. (1990). Restoration of inactivation in mutants of Shaker potassium channels by a peptide derived from ShB. Science 250, 568-571.
-
(1990)
Science
, vol.250
, pp. 568-571
-
-
Zagotta, W.N.1
Hoshi, T.2
Aldrich, R.W.3
-
172
-
-
0026643103
-
Intravesicular acidification correlates with binding of ADP-ribosylation factor to microsomal membranes
-
Zeuzem, S., Feick, P., Zimmermann, P., Haase, W., Kahn, R. A., and Schulz, I. (1992). Intravesicular acidification correlates with binding of ADP-ribosylation factor to microsomal membranes. Proc. Natl. Acad. Sci. USA 89, 6619-6623.
-
(1992)
Proc. Natl. Acad. Sci. USA
, vol.89
, pp. 6619-6623
-
-
Zeuzem, S.1
Feick, P.2
Zimmermann, P.3
Haase, W.4
Kahn, R.A.5
Schulz, I.6
-
173
-
-
0029616734
-
Cystic fibrosis: Genotypic and phenotypic variations
-
Zielenski, J., and Tsui, L.-C. (1995). Cystic fibrosis: Genotypic and phenotypic variations. Annu. Rev. Genet. 29, 777-807.
-
(1995)
Annu. Rev. Genet.
, vol.29
, pp. 777-807
-
-
Zielenski, J.1
Tsui, L.-C.2
|