Effect of cystic fibrosis-associated mutations in the fourth intracellular loop of cystic fibrosis transmembrane conductance regulator

Journal of Biological Chemistry

Volumn 271, Issue 35, 1996, Pages 21279-21284

  Cotten, Joseph F ^a   Ostedgaard, Lynda S ^a   Carson, Mark R ^a   Welsh, Michael J ^a  

^a UNIVERSITY OF IOWA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

8 (4 CHLOROPHENYLTHIO) CYCLIC AMP; ABC TRANSPORTER; ADENOSINE TRIPHOSPHATE; CHLORIDE CHANNEL; CYCLIC AMP DEPENDENT PROTEIN KINASE; FORSKOLIN; ISOBUTYLMETHYLXANTHINE; MUTANT PROTEIN; PYROPHOSPHATE; TRANSMEMBRANE CONDUCTANCE REGULATOR;

ARTICLE; CELL MEMBRANE; CHANNEL GATING; CONTROLLED STUDY; CYSTIC FIBROSIS; GENE MUTATION; HUMAN; HUMAN CELL; HYDROPHOBICITY; MISSENSE MUTATION; PATCH CLAMP; PRIORITY JOURNAL; PROTEIN GLYCOSYLATION; PROTEIN PROCESSING; PROTEIN SYNTHESIS; SITE DIRECTED MUTAGENESIS;

AMINO ACID SEQUENCE; CHLORIDE CHANNELS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; HELA CELLS; HUMANS; ION CHANNEL GATING; MOLECULAR SEQUENCE DATA; MUTAGENESIS, SITE-DIRECTED; STRUCTURE-ACTIVITY RELATIONSHIP;

EID: 0029835571     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.271.35.21279     Document Type: Article

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