Vector-specific complementation profiles of two independent primary defects in cystic fibrosis airways

Human Gene Therapy

Volumn 9, Issue 5, 1998, Pages 635-648

  Zhang, Yulong ^a   Jiang, Qinshi ^a   Dudus, Lorita ^a   Yankaskas, James R ^b   Engelhardt, John F ^a  

^a UNIVERSITY OF IOWA   (United States)

^b UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CHLORIDE ION; CYCLIC AMP; GLYCOPROTEIN; LIPOSOME; SODIUM ION; TRANSMEMBRANE CONDUCTANCE REGULATOR;

ADENOVIRUS; AIRWAY; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BRONCHUS; CONTROLLED STUDY; CYSTIC FIBROSIS; EPITHELIUM; EPITHELIUM CELL; EXPRESSION VECTOR; GENE EXPRESSION; GENE THERAPY; GENE TRANSFER; GOBLET CELL; HUMAN; HUMAN CELL; HUMAN TISSUE; ION PERMEABILITY; MOUSE; MUCUS; NONHUMAN; PLASMID; PROTEIN EXPRESSION; PROTEIN PROCESSING; RAT; SULFATION; TARGET CELL; TRANSGENE; XENOGRAFT;

ADENOVIRIDAE; ANIMALIA; BRONCHUS;

EID: 0032549553     PISSN: 10430342     EISSN: None     Source Type: Journal    
DOI: 10.1089/hum.1998.9.5-635     Document Type: Article

References (5)

1. AL-AWQATI, Q., BARASCH, J., and LANDRY, D. (1992). Chloride channels of intracellular organelles and their potential role in cystic fibrosis. J. Exp. Biol. 172, 245-266.
2. BARASCH, J., KISS, B., PRINCE, A., SAIMAN, L., GRUENERT, D., and AL-AWQATI, Q. (1991). Defective acidification of intracellular organelles in cystic fibrosis. Nature 352, 70-73.
3. BELLON, G., CALMARD, L., THOUVENOT, D., LEVREY, H., JAGNEAUX, V., POITEVIN, F., MALCUS, C., ACCART, N., SENE, C., LAYANI, M.P., AYMARD, M., BIENVENU, J., COURTNEY, M., DURING, G., GILLY, B., GILLY, R., LAMY, D., MOREL, Y., PAULIN, C., PERRAUD, F., RODILLON, L., SO, S., TOURAINE, F., SCHATZ, C., PAVIRANI, A. (1996). Aerosol administration of a replication defective recombinant adenovirus expressing normal human cDNA-CFTR in the respiratory tractus in patients with cystic fibrosis. C R Seances Soc. Biol. Fil. 190, 109-142 [article in French].
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5. BOAT, T.F., WELSH, M.J., and BEAUDET, A.L. (1989). Cystic fibrosis. In The Metabolic Basis of Inherited Disease II, 6th ed. C.R. Scriver, A.L. Beaudet, W.S. Sly, and D. Valle. (McGraw-Hill, New York) pp. 2649-2680.