The Actin Cytoskeleton in SMA and ALS: How Does It Contribute to Motoneuron Degeneration?

Neuroscientist

Volumn 24, Issue 1, 2018, Pages 54-72

  Hensel, Niko ^a,b   Claus, Peter ^a,b,c  

^a HANNOVER MEDICAL SCHOOL   (Germany)

^b Niedersachsen Research Network on Neuroinfectiology (N RENNT)   (Germany)

^c CENTER FOR SYSTEMS NEUROSCIENCE   (Germany)

Author keywords

actin; ALS; amyotrophic lateral sclerosis; motoneuron disease; profilin; Rho kinase; ROCK; SMA; SMN; spinal muscular atrophy; Survival of Motoneuron

Indexed keywords

ACTIN; CELL PROTEIN; PLASTIN 3; PROFILIN; UNCLASSIFIED DRUG;

ACTIN FILAMENT; AMYOTROPHIC LATERAL SCLEROSIS; AXON; BRANCHING MORPHOGENESIS; CELL MOTILITY; HUMAN; MODIFIER GENE; MOLECULAR DYNAMICS; MOLECULAR PATHOLOGY; MOTONEURON; NERVE CELL DIFFERENTIATION; NERVE SPROUTING; NEURITE OUTGROWTH; NEUROPATHOLOGY; NONHUMAN; POSTSYNAPTIC POTENTIAL; PRIORITY JOURNAL; REVIEW; SPINAL MUSCULAR ATROPHY; SYNAPSE VESICLE; ANIMAL; GENETICS; METABOLISM; NERVE DEGENERATION;

ACTIN CYTOSKELETON; AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; HUMANS; MOTOR NEURONS; MUSCULAR ATROPHY, SPINAL; NERVE DEGENERATION;

EID: 85040129119     PISSN: 10738584     EISSN: 10894098     Source Type: Journal    
DOI: 10.1177/1073858417705059     Document Type: Review

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