SMN, profilin IIa and plastin 3: A link between the deregulation of actin dynamics and SMA pathogenesis

Molecular and Cellular Neuroscience

Volumn 42, Issue 1, 2009, Pages 66-74

  Bowerman, Mélissa ^a,b   Anderson, Carrie L ^a,b   Beauvais, Ariane ^a,b   Boyl, Pietro Pilo ^c   Witke, Walter ^d   Kothary, Rashmi ^a,b  

^a OTTAWA HOSPITAL RESEARCH INSTITUTE   (Canada)

^b UNIVERSITY OF OTTAWA   (Canada)

^c UNIVERSITY OF LEUVEN   (Belgium)

^d UNIVERSITY OF BONN   (Germany)

Author keywords

Actin dynamics; Plastin 3; Profilin; Spinal muscular atrophy

Indexed keywords

ACTIN BINDING PROTEIN; PLASTIN 3; PROFILIN; PROFILIN IIA; REGULATOR PROTEIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; EMBRYO; KNOCKOUT MOUSE; MOLECULAR DYNAMICS; MOUSE; NONHUMAN; PATHOGENESIS; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEPLETION; PROTEIN EXPRESSION; SPINAL MUSCULAR ATROPHY; UPREGULATION;

ACTINS; ANIMALS; BRAIN; DISEASE MODELS, ANIMAL; GENE EXPRESSION REGULATION; MEMBRANE GLYCOPROTEINS; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MICROFILAMENT PROTEINS; MUSCULAR ATROPHY, SPINAL; PROFILINS; RATS; SPINAL CORD; SURVIVAL OF MOTOR NEURON 1 PROTEIN; TRANSFECTION;

EID: 67651004474     PISSN: 10447431     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.mcn.2009.05.009     Document Type: Article

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