The CFTR trafficking mutation F508del inhibits the constitutive activity of SLC26A9

American Journal of Physiology - Lung Cellular and Molecular Physiology

Volumn 312, Issue 6, 2017, Pages L12-L925

  Bertrand, Carol A ^a   Mitra, Shalini ^a   Mishra, Sanjay K ^a   Wang, Xiaohui ^a   Zhao, Yu ^b   Pilewski, Joseph M ^a   Madden, Dean R ^b   Frizzell, Raymond A ^a  

^a UNIVERSITY OF PITTSBURGH SCHOOL OF MEDICINE   (United States)

^b DARTMOUTH MEDICAL SCHOOL   (United States)

Author keywords

CAL; Chloride channel; Intracellular trafficking; NHERF 1; PDZ domain

Indexed keywords

ANION; BINDING PROTEIN; CAL PROTEIN; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; LUMACAFTOR; MEMBRANE PROTEIN; NHERF1 PROTEIN; PDZ PROTEIN; PHENYLALANINE; SLC26A9 PROTEIN; UNCLASSIFIED DRUG; ANTIPORTER; CARRIER PROTEIN; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR DELTA F508; GOPC PROTEIN, HUMAN; PEPTIDE; PHOSPHOPROTEIN; SLC26A9 PROTEIN, HUMAN; SODIUM PROTON EXCHANGE PROTEIN; SODIUM-HYDROGEN EXCHANGER REGULATORY FACTOR;

ARTICLE; BRONCHUS EPITHELIUM; CELL MEMBRANE; CONTROLLED STUDY; GENE DELETION; GENE LOSS; GENE MUTATION; HEK293 CELL LINE; HUMAN; HUMAN CELL; ION TRANSPORT; PDZ DOMAIN; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN EXPRESSION; PROTEIN GLYCOSYLATION; PROTEIN PROTEIN INTERACTION; PROTEIN SECRETION; PROTEIN TRANSPORT; BIOLOGICAL MODEL; CHEMISTRY; CYSTIC FIBROSIS; EPITHELIUM CELL; FLUORESCENT ANTIBODY TECHNIQUE; GENETICS; IMMUNOPRECIPITATION; METABOLISM; MUTATION; PATHOLOGY; PROTEIN MOTIF;

AMINO ACID MOTIFS; ANTIPORTERS; CARRIER PROTEINS; CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; EPITHELIAL CELLS; FLUORESCENT ANTIBODY TECHNIQUE; HEK293 CELLS; HUMANS; IMMUNOPRECIPITATION; MEMBRANE PROTEINS; MODELS, BIOLOGICAL; MUTATION; PDZ DOMAINS; PEPTIDES; PHOSPHOPROTEINS; SODIUM-HYDROGEN ANTIPORTER;

EID: 85020293306     PISSN: 10400605     EISSN: 15221504     Source Type: Journal    
DOI: 10.1152/ajplung.00178.2016     Document Type: Article

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